Works matching DE "PROPIONYL-CoA carboxylase"

Results: 24

Possible mechanisms for sensorineural hearing loss and deafness in patients with propionic acidemia.

Published in:

2017

By:

Grünert, S. C.;
Bodi, I.;
Odening, K. E.

Publication type:

Letter

Methylmalonic Acidemia Diagnosis by Laboratory Methods.

Published in:

Reports of Biochemistry & Molecular Biology, 2016, v. 5, n. 1, p. 1

By:

Keyfi, Fatemeh;
Talebi, Saeed;
Varasteh, Abdol-Reza

Publication type:

Article

Two Frequent Mutations Associated with the Classic Form of Propionic Acidemia in Taiwan.

Published in:

Biochemical Genetics, 2014, v. 52, n. 9/10, p. 415, doi. 10.1007/s10528-014-9657-6

By:

Chiu, Yen-Hui;
Liu, Yu-Ning;
Liao, Wei-Ling;
Chang, Ying-Chen;
Lin, Shuan-Pei;
Hsu, Chia-Chi;
Chiu, Pao-Chin;
Niu, Dau-Ming;
Wang, Chung-Hsing;
Ke, Yu-Yuan;
Chien, Yin-Hsiu;
Hsiao, Kwang-Jen;
Liu, Tze-Tze

Publication type:

Article

C-assisted metabolomics analysis reveals the positive correlation between specific erythromycin production rate and intracellular propionyl-CoA pool size in Saccharopolyspora erythraea.

Published in:

Bioprocess & Biosystems Engineering, 2017, v. 40, n. 9, p. 1337, doi. 10.1007/s00449-017-1792-0

By:

Hong, Ming;
Mou, Han;
Liu, Xiaoyun;
Huang, Mingzhi;
Chu, Ju

Publication type:

Article

Biosynthesis of poly(3-hydroxybutyrate- co-3-hydroxyvalerate) from glucose with elevated 3-hydroxyvalerate fraction via combined citramalate and threonine pathway in Escherichia coli.

Published in:

Applied Microbiology & Biotechnology, 2014, v. 98, n. 9, p. 3923, doi. 10.1007/s00253-013-5494-5

By:

Wang, Qian;
Liu, Xiaolong;
Qi, Qingsheng

Publication type:

Article

A dodecylamine derivative of cyanocobalamin potently inhibits the activities of cobalamin-dependent methylmalonyl-CoA mutase and methionine synthase of Caenorhabditis elegans.

Published in:

FEBS Open Bio, 2014, v. 4, p. 722, doi. 10.1016/j.fob.2014.07.008

By:

Bito, Tomohiro;
Yabuta, Yukinori;
Ichiyanagi, Tsuyoshi;
Kawano, Tsuyoshi;
Watanabe, Fumio

Publication type:

Article

Determining the Biochemical Properties of the Oxalate Biosynthetic Component (Obc)1 from Burkholderia mallei.

Published in:

PLoS ONE, 2016, v. 11, n. 9, p. 1, doi. 10.1371/journal.pone.0163294

By:

Lambert, Peter M.;
Nakata, Paul A.

Publication type:

Article

Assay for methylmalonyl coenzyme A mutase activity based on determination of succinyl coenzyme A by ultrahigh-performance liquid chromatography tandem mass spectrometry.

Published in:

Analytical & Bioanalytical Chemistry, 2015, v. 407, n. 18, p. 5281, doi. 10.1007/s00216-015-8753-8

By:

Gotoh, Kana;
Nakajima, Yoko;
Tajima, Go;
Hotta, Yuji;
Kataoka, Tomoya;
Kawade, Yoshihiro;
Sugiyama, Naruji;
Ito, Tetsuya;
Kimura, Kazunori;
Maeda, Yasuhiro

Publication type:

Article

Construction of a novel anaerobic pathway in Escherichia coli for propionate production.

Published in:

BMC Biotechnology, 2017, v. 17, p. 1, doi. 10.1186/s12896-017-0354-5

By:

Jing Li;
Xinna Zhu;
Jing Chen;
Dongdong Zhao;
Xueli Zhang;
Changhao Bi

Publication type:

Article

Severe renal failure and hyperammonemia in a newborn with propionic acidemia: effects of treatment on the clinical course.

Published in:

Renal Failure, 2014, v. 36, n. 3, p. 451, doi. 10.3109/0886022X.2013.865484

By:

Kasapkara, Çiğdem Seher;
Akar, Melek;
Yürük Yıldırım, Zeynep Nagehan;
Tüzün, Heybet;
Kanar, Berat;
Özbek, Mehmet Nuri

Publication type:

Article

Systematic literature review and meta-analysis on the epidemiology of methylmalonic acidemia (MMA) with a focus on MMA caused by methylmalonyl-CoA mutase (mut) deficiency.

Published in:

2019

By:

Almási, Tímea;
Guey, Lin T.;
Lukacs, Christine;
Csetneki, Kata;
Vokó, Zoltán;
Zelei, Tamás

Publication type:

journal article

Methylmalonic acidemia/propionic acidemia - the biochemical presentation and comparing the outcome between liver transplantation versus non-liver transplantation groups.

Published in:

2019

By:

Yang, Chia-Feng;
Niu, Dau-Ming;
Chu, Tzu-Hung;
Hu, Rey-Heng;
Ho, Ming-Chih;
Chien, Yin-Hsiu;
Hwu, Wuh-Liang;
Lee, Ni-Chung;
Lin, Shuan-Pei;
Lin, Hsiang-Yu;
Liao, Hsuan-Chieh;
Chiang, Chuan-Chi;
Ho, Huey-Jane;
Lai, Chih-Jou;
Lin, Niang-Cheng;
Liu, Chin-Su

Publication type:

journal article

Methylmalonyl-CoA Epimerase Deficiency Mimicking Propionic Aciduria.

Published in:

2017

By:

Abily-Donval, Lenaig;
Torre, Stéphanie;
Samson, Aurélie;
Sudrié-Arnaud, Bénédicte;
Acquaviva, Cécile;
Guerrot, Anne-Marie;
Benoist, Jean-François;
Marret, Stéphane;
Bekri, Soumeya;
Tebani, Abdellah

Publication type:

Case Study

Anaesthetic considerations in a patient with methylmalonyl-coenzyme A mutase deficiency.

Published in:

Indian Journal of Anaesthesia, 2017, v. 61, n. 12, p. 1018, doi. 10.4103/ija.IJA_463_17

By:

Shaikh, Nabila;
Gulam Hashmi, Mukhtadir;
Shah, Chandrakant;
Dhansura, Tasneem

Publication type:

Article

Nitrogen deprivation in Fusarium oxysporum promotes mycotoxin production via intermediates in the Krebs cycle and unreported methylmalonyl-CoA mutase activity.

Published in:

Metabolomics, 2018, v. 14, n. 12, p. 1, doi. 10.1007/s11306-018-1459-0

By:

Karpe, A. V.;
Dunn, M. S.;
Taylor, M. C.;
Nguyen, T.;
Ong, C.;
Karla, T.;
Rockman, S.;
Beale, D. J.

Publication type:

Article

Effects of the Methylmalonyl-CoA Metabolic Pathway on Ansamitocin Production in Actinosynnema pretiosum.

Published in:

Applied Biochemistry & Biotechnology, 2017, v. 181, n. 3, p. 1167, doi. 10.1007/s12010-016-2276-4

By:

Zhao, Mengjiang;
Fan, Yuxiang;
Wei, Liujing;
Hu, Fengxian;
Hua, Qiang

Publication type:

Article

Cloning, expression, purification, crystallization and X-ray crystallographic analysis of β-ketothiolase B from Ralstonia eutropha H16.

Published in:

Acta Crystallographica: Section F, Structural Biology Communications, 2014, v. 70, n. 3, p. 316, doi. 10.1107/S2053230X14001228

By:

Kim, Eun-Jung;
Son, Hyeoncheol Francis;
Chang, Jeong Ho;
Kim, Kyung-Jin

Publication type:

Article

Poly(3-hydroxybutyrate-co-3-hydroxyvalerate) co-produced with l-isoleucine in <italic>Corynebacterium glutamicum</italic> WM001.

Published in:

Microbial Cell Factories, 2018, v. 17, n. 1, p. N.PAG, doi. 10.1186/s12934-018-0942-7

By:

Ma, Wenjian;
Wang, Jianli;
Li, Ye;
Yin, Lianghong;
Wang, Xiaoyuan

Publication type:

Article

Biosynthesis of angelyl-CoA in <italic>Saccharomyces cerevisiae</italic>.

Published in:

Microbial Cell Factories, 2018, v. 17, n. 1, p. N.PAG, doi. 10.1186/s12934-018-0925-8

By:

Callari, Roberta;
Fischer, David;
Heider, Harald;
Weber, Nora

Publication type:

Article

Awakening sleeping beauty: production of propionic acid in Escherichia coli through the sbm operon requires the activity of a methylmalonyl-CoA epimerase.

Published in:

Microbial Cell Factories, 2017, v. 16, p. 1, doi. 10.1186/s12934-017-0735-4

By:

Gonzalez-Garcia, Ricardo Axayacatl;
McCubbin, Tim;
Wille, Annalena;
Plan, Manuel;
Nielsen, Lars Keld;
Marcellin, Esteban

Publication type:

Article

Cloning and transcription analysis of the Candida rugosa propionyl-CoA dehydrogenase gene and its expression in Pichia pastoris.

Published in:

Journal of Basic Microbiology, 2012, v. 52, n. 3, p. 360, doi. 10.1002/jobm.201100050

By:

Zhou, Feng-Li;
Zhang, Ru-Bing;
Zhang, Yong-Guang;
Zhang, Fan;
Zhu, Jian-Hang

Publication type:

Article

Living-donor liver transplantation for propionic acidemia.

Published in:

Pediatric Transplantation, 2012, v. 16, n. 3, p. 230, doi. 10.1111/j.1399-3046.2011.01607.x

By:

Kasahara, Mureo;
Sakamoto, Seisuke;
Kanazawa, Hiroyuki;
Karaki, Chiaki;
Kakiuchi, Toshihiko;
Shigeta, Takanobu;
Fukuda, Akinari;
Kosaki, Rika;
Nakazawa, Atsuko;
Ishige, Mika;
Nagao, Masayoshi;
Shigematsu, Yosuke;
Yorifuji, Tohru;
Naiki, Yasuhiro;
Horikawa, Reiko

Publication type:

Article

Clinical Spectrum of Propionic Acidaemia.

Published in:

Journal of Nutrition & Metabolism, 2013, p. 1, doi. 10.1155/2013/975964

By:

Rafique, Muhammad

Publication type:

Article

Optimization and validation of a reversed-phase high performance liquid chromatography method for the measurement of bovine liver methylmalonyl-coenzyme a mutase activity.

Published in:

BMC Biochemistry, 2013, v. 14, n. 1, p. 2, doi. 10.1186/1471-2091-14-25

By:

Ouattara, Bazoumana;
Duplessis, Mélissa;
Girard, Christiane L

Publication type:

Article