Works about PRION diseases

Results: 1993

Advancing Parkinson's diagnosis: seed amplification assay for α-synuclein detection in minimally invasive samples.

Published in:

Molecular & Cellular Biochemistry, 2025, v. 480, n. 6, p. 3297, doi. 10.1007/s11010-024-05190-y

By:

Carrazana, Elizabeth;
Montalbán-Gutiérrez, Leonardo;
Chana-Cuevas, Pedro;
Salvadores, Natalia

Publication type:

Article

TREM2 supports neuronal protection and microglial reactivity without an effect on misfolded protein deposition in chronic neurodegenerative prion disease.

Published in:

Frontiers in Neuroscience, 2025, p. 1, doi. 10.3389/fnins.2025.1525017

By:

Carpanini, Sarah M.;
Bradford, Barry M.;
Alfieri, Alessio;
Piccardo, Pedro;
Monzón-Sandoval, Jimena;
Brown, Deborah;
Boyle, Aileen;
Pokrovskaya, Aleksandra;
Mabbott, Neil A.;
Manson, Jean;
McColl, Barry W.

Publication type:

Article

Downregulation of STAT3 transcription factor reverses synaptotoxic phenotype of reactive astrocytes associated with prion diseases.

Published in:

Acta Neuropathologica Communications, 2025, v. 13, n. 1, p. 1, doi. 10.1186/s40478-025-02028-6

By:

Kushwaha, Rajesh;
Molesworth, Kara;
Makarava, Natallia;
Baskakov, Ilia V.

Publication type:

Article

Cognitive and behavioral manifestations in neurological and psychiatric diseases as models to understand the complexity of human biology.

Published in:

Revista Mexicana de Neurociencia, 2025, v. 26, n. 2, p. 41, doi. 10.24875/RMN.M25000106

By:

Ruiz-Garcia, Ramiro

Publication type:

Article

Internal consistency, construct validity, and responsiveness of the MRC Prion Disease Rating Scale.

Published in:

Journal of Patient-Reported Outcomes, 2025, v. 9, n. 1, p. 1, doi. 10.1186/s41687-025-00884-3

By:

Leidy, Leah;
Yarlas, Aaron;
Pulido, Robert S.;
Ludwig, Jessica;
Glisic, Kathleen;
Appleby, Brian S.

Publication type:

Article

Correction: Fishing for Prion Protein Function.

Published in:: 2014
Publication type:: Correction Notice

The Mechanism of Toxicity in HET-S/HET-s Prion Incompatibility

Published in:

PLoS Biology, 2012, v. 10, n. 12, p. 1, doi. 10.1371/journal.pbio.1001451

By:

Seuring, Carolin;
Greenwald, Jason;
Wasmer, Christian;
Wepf, Roger;
Saupe, Sven J.;
Meier, Beat H.;
Riek, Roland

Publication type:

Article

Conformational biosensor for diagnosis of prion diseases.

Published in:

Biotechnology Letters, 2005, v. 27, n. 9, p. 671, doi. 10.1007/s10529-005-4478-7

By:

Tcherkasskaya, Olga;
Davidson, Eugene A.;
Schmerr, Mary Jo;
Orser, Cindy S.

Publication type:

Article

Short TE quantitative proton magnetic resonance spectroscopy in variant Creutzfeldt-Jakob disease.

Published in:

2006

By:

Cordery, R. J.;
MacManus, D.;
Godbolt, A.;
Rossor, M. N.;
Waldman, A. D.

Publication type:

journal article

Molecular analysis of prion strain variation and the aetiology of `new variant' CJD.

Published in:

Nature, 1996, v. 383, n. 6602, p. 685, doi. 10.1038/383685a0

By:

Collinge, John;
Sidle, Katie C.L.

Publication type:

Article

A suspicious signature.

Published in:

Nature, 1996, v. 383, n. 6602, p. 666, doi. 10.1038/383666a0

By:

Aguzzi, Adriano;
Weissmann, Charles

Publication type:

Article

Unaltered susceptibility to BSE in transgenic mice...

Published in:

Nature, 1995, v. 378, n. 6559, p. 779, doi. 10.1038/378779a0

By:

Collinge, John;
Palmer, Mark S.

Publication type:

Article

Non-genetic propagation of strain-specific properties of scrapie prion protein.

Published in:

Nature, 1995, v. 375, n. 6533, p. 698, doi. 10.1038/375698a0

By:

Bessen, Richard A.;
Kocisko, David A.

Publication type:

Article

Yielding under strain.

Published in:

Nature, 1995, v. 375, n. 6533, p. 628, doi. 10.1038/375628a0

By:

Weissmann, C.

Publication type:

Article

Prion protein is necessary for normal synaptic function.

Published in:

Nature, 1994, v. 370, n. 6487, p. 295, doi. 10.1038/370295a0

By:

Collinge, John;
Whittington, Miles A.

Publication type:

Article

A question of conformation.

Published in:

Nature, 1993, v. 365, n. 6445, p. 386, doi. 10.1038/365386a0

By:

Carr, Kimberly

Publication type:

Article

Prion disease scare.

Published in:

Nature, 1993, v. 365, n. 6442, p. 98, doi. 10.1038/365098a0

By:

Maddox, John D.

Publication type:

Article

Pharmacokinetics and distribution of clioquinol in golden hamsters.

Published in:

Journal of Pharmacy & Pharmacology, 2007, v. 59, n. 3, p. 387

By:

Gianpietro Bondiolotti;
Mariaelvina Sala;
Claudia Pollera;
Marco Gervasoni;
Maria Puricelli;
Wilma Ponti;
Silvio R. Bareggi

Publication type:

Article

Prions: a threat to health security and the need for effective medical countermeasures.

Published in:

Global Health Journal, 2023, v. 7, n. 1, p. 43, doi. 10.1016/j.glohj.2023.02.004

By:

Lee, Ying-Chiang J.

Publication type:

Article

Chronic wasting disease: a jurisdictional scan of advice for hunters and cervid meat-processors in CWD affected areas.

Published in:

Environmental Health Review (Online), 2025, v. 68, n. 1, p. 9, doi. 10.5864/d2025-003

By:

O'Keeffe, Juliette;
Lee, Michael J.;
Tong, Esther

Publication type:

Article

Validation of the Medical Research Council prion disease rating scale in France.

Published in:

Brain Communications, 2023, v. 5, n. 6, p. 1, doi. 10.1093/braincomms/fcad267

By:

Brandel, Jean-Philippe;
Welaratne, Arlette;
Denouel, Angeline;
Haïk, Stéphane

Publication type:

Article

Prion protein degradation by lichens of the genus Cladonia.

Published in:

Lichenologist, 2012, v. 44, n. 4, p. 523, doi. 10.1017/S0024282912000102

By:

BENNETT, James P.;
RODRIGUEZ, Cynthia M.;
JOHNSON, Christopher J.

Publication type:

Article

MicroRNAs in Neuroinflammation: Implications in Disease Pathogenesis, Biomarker Discovery and Therapeutic Applications.

Published in:

Non-Coding RNA, 2019, v. 5, n. 2, p. 1, doi. 10.3390/ncrna5020035

By:

Slota, Jessy A.;
Booth, Stephanie A.

Publication type:

Article

Evaluation of the genetic resistance status to classical and atypical scrapie in Karacabey merino rams.

Published in:

Turkish Journal of Veterinary & Animal Sciences, 2015, v. 39, n. 6, p. 736, doi. 10.3906/vet-1507-36

By:

YAMAN, Yalçın;
SOYSAL, Mehmet İhsan;
ÜN, Cemal

Publication type:

Article

Nanotechnology-Driven Approaches in Overcoming Drug Delivery Challenges for Neurodegenerative Diseases.

Published in:

Indian Journal of Pharmaceutical Education & Research, 2024, v. 58, p. S1185, doi. 10.5530/ijper.58.4s.116

By:

Palaniyappan, Rajamanickam;
Arthanari, Saravanakumar;
Subramanian, Mohanraj;
Periyasamy, Parthiban;
Pethappachetty, Palanisamy;
Ganesan, Ragupathi;
Prakash, Manivasakam;
Govindaraj, Anandharaj

Publication type:

Article

Alkaline hydrolysis of mouse-adapted scrapie for inactivation and disposal of prion-positive material.

Published in:

Journal of Animal Science, 2009, v. 87, n. 5, p. 1787, doi. 10.2527/jas.2008-1492

By:

Murphy, R. G. L.;
Scanga, J. A.;
Powers, B. E.;
Pilon, J. L.;
VerCauteren, K. C.;
Nash, P. B.;
Smith, G. C.;
Belk, K. E.

Publication type:

Article

Using the Synchrotron (SRFTIRM) to Reveal Molecular Structural-Chemical Differences between Two Types of Forages Seeds -Winterfat (Krascheninnikovia lanata).

Published in:

Journal of Animal Science, 2006, v. 84, p. 21

By:

Yu, P.;
Wang, R.;
Bai, Y.

Publication type:

Article

Chronic antioxidant therapy reduces oxidative stress in a mouse model of Alzheimer's disease.

Published in:

Free Radical Research, 2009, v. 43, n. 2, p. 156, doi. 10.1080/10715760802644694

By:

Siedlak, Sandra L.;
Casadesus, Gemma;
Webber, Kate M.;
Pappolla, Miguel A.;
Atwood, Craig S.;
Smith, Mark A.;
Perry, George

Publication type:

Article

Facing up to Complexity: Implications for Our Social Experiments.

Published in:

Science & Engineering Ethics, 2016, v. 22, n. 3, p. 775, doi. 10.1007/s11948-015-9657-x

By:

Hawkins, Ronnie

Publication type:

Article

Prion infectivity is encoded exclusively within the structure of proteinase K-resistant fragments of synthetically generated recombinant PrPSc.

Published in:

Acta Neuropathologica Communications, 2018, v. 6, n. 1, p. N.PAG, doi. 10.1186/s40478-018-0534-0

By:

Wang, Fei;
Wang, Xinhe;
Abskharon, Romany;
Ma, Jiyan

Publication type:

Article

Familial human prion diseases associated with prion protein mutations Y226X and G131V are transmissible to transgenic mice expressing human prion protein.

Published in:

Acta Neuropathologica Communications, 2018, v. 6, p. 1, doi. 10.1186/s40478-018-0516-2

By:

Race, Brent;
Williams, Katie;
Hughson, Andrew G.;
Jansen, Casper;
Parchi, Piero;
Rozemuller, Annemieke J. M.;
Chesebro, Bruce

Publication type:

Article

Enhanced neuroinvasion by smaller, soluble prions.

Published in:

Acta Neuropathologica Communications, 2017, v. 5, p. 1, doi. 10.1186/s40478-017-0430-z

By:

Bett, Cyrus;
Lawrence, Jessica;
Kurt, Timothy D.;
Orru, Christina;
Aguilar-Calvo, Patricia;
Kincaid, Anthony E.;
Surewicz, Witold K.;
Caughey, Byron;
Chengbiao Wu;
Sigurdson, Christina J.

Publication type:

Article

Two alternative pathways for generating transmissible prion disease de novo.

Published in:

Acta Neuropathologica Communications, 2015, v. 3, p. 1, doi. 10.1186/s40478-015-0248-5

By:

Makarava, Natallia;
Savtchenko, Regina;
Baskakov, Ilia V.

Publication type:

Article

Interaction of prion protein with acetylcholinesterase: potential pathobiological implications in prion diseases.

Published in:

Acta Neuropathologica Communications, 2015, v. 3, n. 1, p. 1, doi. 10.1186/s40478-015-0188-0

By:

Torrent, Joan;
Vilchez-Acosta, Alba;
Muñoz-Torrero, Diego;
Trovaslet, Marie;
Nachon, Florian;
Chatonnet, Arnaud;
Grznarova, Katarina;
Van Ba, Isabelle Acquatella-Tran;
Le Goffic, Ronan;
Herzog, Laetitia;
Béringue, Vincent;
Rezaei, Human

Publication type:

Article

Featured Abstracts.

Published in:: 2016
Publication type:: Abstract

Chronic wasting disease — A prion disease through a One Health lens.

Published in:

Canadian Veterinary Journal / Revue Vétérinaire Canadienne, 2022, v. 63, n. 4, p. 431

By:

Gilch, Sabine

Publication type:

Article

Syntaxin-6 delays prion protein fibril formation and prolongs the presence of toxic aggregation intermediates.

Published in:

eLife, 2024, p. 1, doi. 10.7554/eLife.83320

By:

Sangar, Daljit;
Hill, Elizabeth;
Jack, Kezia;
Batchelor, Mark;
Mistry, Beenaben;
Ribes, Juan M.;
Jackson, Graham S.;
Mead, Simon;
Bieschke, Jan

Publication type:

Article

A case report of genetic prion disease with two different PRNP variants.

Published in:

Molecular Genetics & Genomic Medicine, 2020, v. 8, n. 3, p. 1, doi. 10.1002/mgg3.1134

By:

Piazza, Megan;
Prior, Thomas W.;
Khalsa, Prabhjot S.;
Appleby, Brian

Publication type:

Article

Amino acid sequence of the Pekingese dog prion protein gene.

Published in:

Xenotransplantation, 2006, v. 13, n. 5, p. 471, doi. 10.1111/j.1399-3089.2006.00325.x

By:

Changde Wu;
Wanyong Pang;
Jianmin Yang;
Xiangmei Zhou;
Deming Zhao

Publication type:

Article

The Novel Sorting Nexin SNX33 Interferes with Cellular PrPSc Formation by Modulation of PrPc Shedding.

Published in:

Traffic, 2008, v. 9, n. 7, p. 1116, doi. 10.1111/j.1600-0854.2008.00750.x

By:

Heiseke, Andreas;
Schöbel, Susanne;
Lichtenthaler, Stefan F.;
Vorberg, Ina;
Groschup, Martin H.;
Kretzschmar, Hans;
Schätzl, Hermann M.;
Nunziante, Max

Publication type:

Article

Detection of prions in matching post-mortem skin and cerebrospinal fluid samples using second-generation real-time quaking-induced conversion assay.

Published in:

Scientific Reports, 2024, v. 14, n. 1, p. 1, doi. 10.1038/s41598-024-56789-6

By:

Baranová, Soňa;
Moško, Tibor;
Brůžová, Magdalena;
Haldiman, Tracy;
Kim, Chae;
Safar, Jiri G.;
Matěj, Radoslav;
Holada, Karel

Publication type:

Article

Quantitative analysis of prion disease using an AI-powered digital pathology framework.

Published in:

Scientific Reports, 2023, v. 13, n. 1, p. 1, doi. 10.1038/s41598-023-44782-4

By:

Salvi, Massimo;
Molinari, Filippo;
Ciccarelli, Mario;
Testi, Roberto;
Taraglio, Stefano;
Imperiale, Daniele

Publication type:

Article

Protocol for further laboratory investigations into the distribution of infectivity of Atypical BSE.

Published in:: EFSA Journal, 2014, v. 12, n. 7, p. 1, doi. 10.2903/j.efsa.2014.3798
Publication type:: Article

A Remarkable Journey of Porcine to Human Xenotransplantation.

Published in:

Indian Journal of Transplantation, 2024, v. 18, n. 2, p. 109, doi. 10.4103/ijot.ijot_49_22

By:

Sharma, Dhruva;
Subramaniam, Krishnan Ganapathy

Publication type:

Article

In Response to the Letter to the Editors.

Published in:

Journal of Intensive Care Medicine, 2005, v. 20, n. 3, p. 182, doi. 10.1177/0885066605275318

By:

Shapiro, Janet M.

Publication type:

Article

Creutzfeldt-Jakob Disease Presenting as Refractory Nonconvulsive Status Epilepticus.

Published in:

Journal of Intensive Care Medicine, 2004, v. 19, n. 6, p. 345, doi. 10.1177/0885066604269771

By:

Shapiro, Janet M.;
Shujaat, Adil;
Wang, Jill;
Chen, Xiaowei

Publication type:

Article

Prion diseases and dental treatment: principles and practice of patients with/suspected or at-risk of CJD: Case reports.

Published in:

British Dental Journal, 2003, v. 195, n. 6, p. 319, doi. 10.1038/sj.bdj.4810542

By:

Smith, A.J.;
Sweeney, M.P.;
Bagg, J.

Publication type:

Article

The Role of Unfolded Protein Response and Mitogen-Activated Protein Kinase Signaling in Neurodegenerative Diseases with Special Focus on Prion Diseases.

Published in:

Frontiers in Aging Neuroscience, 2017, v. 9, p. 1, doi. 10.3389/fnagi.2017.00120

By:

Ali Shah, Syed Zahid;
Deming Zhao;
Hussain, Tariq;
Lifeng Yang

Publication type:

Article

Hijacking PrPc-dependent signal transduction: when prions impair Aβ clearance.

Published in:

Frontiers in Aging Neuroscience, 2014, v. 6, p. 1, doi. 10.3389/fnagi.2014.00025

By:

Hernandez-Rapp, Julia;
Martin-Lannerée, Séverine;
Hirsch, Théo Z.;
Launay, Jean-Marie;
Mouillet-Richard, Sophie

Publication type:

Article

Preface—Prion research in perspective IV.

Published in:

Journal of Toxicology & Environmental Health: Part A, 2016, v. 79, n. 16/17, p. 675, doi. 10.1080/15287394.2016.1173985

By:

Cashman, Neil;
Darshan, Shalu;
Tyshenko, Michael G.

Publication type:

Article