Works matching DE "PRION diseases"

Results: 2005

Transient receptor potential vanilloid channel 2 contributes to multi-modal endoplasmic reticulum and perinuclear space dilations that can also be observed in prion-infected mice.

Published in:

Acta Neuropathologica, 2025, v. 149, n. 1, p. 1, doi. 10.1007/s00401-025-02906-2

By:

Zhao, Wenda;
Eid, Shehab;
Sackmann, Chris;
Williams, Declan;
Wang, Xinzhu;
Ouyang, Yunqing;
Zerbes, Thomas;
Schmitt-Ulms, Gerold

Publication type:

Article

HeMiTo-dynamics: a characterization of mammalian prion toxicity using non-dimensionalization, linear stability and perturbation analyses.

Published in:

Mathematical Medicine & Biology: A Journal of the IMA, 2025, v. 42, n. 2, p. 159, doi. 10.1093/imammb/dqae024

By:

Borgqvist, Johannes G;
Alexandersen, Christoffer Gretarsson

Publication type:

Article

Microglia-specific NF-κB signaling is a critical regulator of prion-induced glial inflammation and neuronal loss.

Published in:

PLoS Pathogens, 2025, v. 21, n. 6, p. 1, doi. 10.1371/journal.ppat.1012582

By:

Hay, Arielle J. D.;
Popichak, Katriana A.;
Mumford, Genova;
Bian, Jifeng;
Shirley, Payton;
Wolfrath, Lauren;
Eggers, Michael;
Nicholson, Eric M.;
Tjalkens, Ronald B.;
Zabel, Mark D.;
Moreno, Julie A.

Publication type:

Article

White‐tailed deer behaviors at three forage settings: Implications for transmission of chronic wasting disease.

Published in:

Journal of Wildlife Management, 2025, v. 89, n. 5, p. 1, doi. 10.1002/jwmg.70036

By:

Courtney, Samantha E.;
Magee, Jack C.;
Nichols, Melissa;
Etter, Dwayne R.;
Gray, Steven M.;
Christensen, Sonja;
Williams, David;
Roloff, Gary J.

Publication type:

Article

Characterization of prion strains and peripheral prion infectivity patterns in E200K genetic CJD patients.

Published in:

Acta Neuropathologica, 2025, v. 149, n. 1, p. 1, doi. 10.1007/s00401-025-02903-5

By:

Barrio, Tomás;
Douet, Jean-Yves;
Žáková, Dana;
Eraña, Hasier;
Huor, Alvina;
Cassard, Hervé;
Alzuguren, Oihane;
Lugan, Séverine;
Aron, Naïma;
Péran, Patrice;
Castilla, Joaquín;
Andréoletti, Olivier

Publication type:

Article

Mesenchymal Stem Cell Secretome Attenuates PrP 106-126 -Induced Neurotoxicity by Suppressing Neuroinflammation and Apoptosis and Enhances Cell Migration.

Published in:

Cells (2073-4409), 2025, v. 14, n. 11, p. 851, doi. 10.3390/cells14110851

By:

Zayed, Mohammed;
Jeong, Byung-Hoon

Publication type:

Article

The potential role of biomarkers CD28 and PF4 in the pathogenesis of idiopathic pulmonary fibrosis and their impact on the prognosis: an immune microenvironment analysis.

Published in:

Hereditas, 2025, v. 162, n. 1, p. 1, doi. 10.1186/s41065-025-00464-x

By:

Yan, Li;
Li, Jiang-Han;
Zhang, Ai-Li;
Li, He;
Pang, Bo;
Meng, De-Yang;
Fu, Qian;
Du, Li-Juan;
Su, Yan

Publication type:

Article

Creutzfeldt-Jakob disease - a rarity that can become a tragedy. How to ensure the safety of medical staff and other patients in cases of prion disease?

Published in:

European Journal of Clinical & Experimental Medicine, 2025, v. 23, p. 39

By:

Marin, Gheorghe Eduard;
Iova, Olga Maria;
Labo, Matei;
Nistor, Cristina

Publication type:

Article

Correction to 'EXPRESSION OF CONCERN: Combined Pharmacological, Mutational and Cell Biology Approaches Indicate That p53‐Dependent Caspase 3 Activation Triggered by Cellular Prion Is Dependent on Its Endocytosis'.

Published in:: Journal of Neurochemistry, 2025, v. 169, n. 5, p. 1, doi. 10.1111/jnc.70096
Publication type:: Article

EXPRESSION OF CONCERN: Combined Pharmacological, Mutational and Cell Biology Approaches Indicate That p53‐Dependent Caspase 3 Activation Triggered by Cellular Prion Is Dependent on Its Endocytosis.

Published in:: Journal of Neurochemistry, 2025, v. 169, n. 5, p. 1, doi. 10.1111/jnc.70074
Publication type:: Article

Association of sporadic Creutzfeldt–Jakob disease with homozygous genotypes at PRNP codons 129 and 219 in the Korean population.

Published in:

Neurogenetics, 2005, v. 6, n. 4, p. 229, doi. 10.1007/s10048-005-0016-y

By:

Jeong, Byung-Hoon;
Lee, Kyung-Hee;
Kim, Nam-Ho;
Jin, Jae-Kwang;
Kim, Jae-Il;
Carp, Richard;
Kim, Yong-Sun

Publication type:

Article

Analysis of sequence variability of the bovine prion protein gene (PRNP) in German cattle breeds.

Published in:

Neurogenetics, 2004, v. 5, n. 1, p. 19, doi. 10.1007/s10048-003-0171-y

By:

Sander, Petra;
Hamann, Henning;
Pfeiffer, Ina;
Wemheuer, Wilhelm;
Brenig, Bertram;
Groschup, Martin H.;
Ziegler, Ute;
Distl, Ottmar;
Leeb, Tosso

Publication type:

Article

High-resolution structure of infectious prion protein: the final frontier.

Published in:

Nature Structural & Molecular Biology, 2012, v. 19, n. 4, p. 370, doi. 10.1038/nsmb.2266

By:

Diaz-Espinoza, Rodrigo;
Soto, Claudio

Publication type:

Article

Dominant prion mutants induce curing through pathways that promote chaperone-mediated disaggregation.

Published in:

Nature Structural & Molecular Biology, 2011, v. 18, n. 4, p. 486, doi. 10.1038/nsmb.2031

By:

DiSalvo, Susanne;
Derdowski, Aaron;
Pezza, John A.;
Serio, Tricia R.

Publication type:

Article

Prions and their lethal journey to the brain.

Published in:

Nature Reviews Microbiology, 2006, v. 4, n. 3, p. 201, doi. 10.1038/nrmicro1346

By:

Mabbott, Neil A.;
MacPherson, G. Gordon

Publication type:

Article

Diagnosing prion diseases: needs, challenges and hopes.

Published in:

Nature Reviews Microbiology, 2004, v. 2, n. 10, p. 809, doi. 10.1038/nrmicro1003

By:

Soto, Claudio

Publication type:

Article

Prions: Proteins go it alone.

Published in:

Nature Reviews Microbiology, 2004, v. 2, n. 5, p. 357, doi. 10.1038/nrmicro895

By:

Flintoft, Louisa

Publication type:

Article

Analysis of Prion Strains by PrP<sup>Sc</sup> Profiling in Sporadic Creutzfeldt--Jakob Disease.

Published in:

PLoS Medicine, 2006, v. 3, n. 2, p. 0236, doi. 10.1371/journal.pmed.0030014

By:

Schoch, Gaby;
Seeger, Harald;
Bogousslavsky, Julien;
Tolnay, Markus;
Janzer, Robert Charles;
Aguzzi, Adriano;
Glatzel, Markus

Publication type:

Article

Familial Prion Disease: First Indian Kindred with Gerstmann-Sträussler-Scheinker Syndrome.

Published in:

2020

By:

Bhatia, Sameer;
Bijarnia-Mahay, Sunita;
Dubey, Sudisha;
Gourie-Devi, Mandaville

Publication type:

journal article

Structural Effects of Multiple Pathogenic Mutations Suggest a Model for the Initiation of Misfolding of the Prion Protein.

Published in:

Angewandte Chemie, 2015, v. 127, n. 26, p. 7639, doi. 10.1002/ange.201501011

By:

Singh, Jogender;
Udgaonkar, Jayant B.

Publication type:

Article

Prion susceptibility and protective alleles exhibit marked geographic differences (Communicated by Mark H. Paalman) Online Citation: Human Mutation, Mutation in Brief #628 (2003) Online http://www.interscience.wiley.com/humanmutation/pdf/mutation/628.pdf)

Published in:

Human Mutation, 2003, v. 22, n. 1, p. 104, doi. 10.1002/humu.9157

By:

Marta Soldevila;
Francesc Calafell;
Aida M. Andrés;
Jordi Yagüe;
Agnar Helgason;
Kári Stefánsson;
Jaume Bertranpetit

Publication type:

Article

Prion susceptibility and protective alleles exhibit marked geographic differencesCommunicated by Mark H. PaalmanOnline Citation: Human Mutation, Mutation in Brief #628 (2003) Onlinehttp://www.interscience.wiley.com/humanmutation/pdf/mutation/628.pdf.

Published in:

Human Mutation, 2003, v. 22, n. 1, p. 104, doi. 10.1002/humu.9157

By:

Marta Soldevila;
Francesc Calafell;
Aida M. Andrés;
Jordi Yagüe;
Agnar Helgason;
Kári Stefánsson;
Jaume Bertranpetit

Publication type:

Article

Optimization of an amplification protocol for misfolded proteins by using relaxed control.

Published in:

Journal of Mathematical Biology, 2015, v. 70, n. 1/2, p. 289, doi. 10.1007/s00285-014-0768-9

By:

Coron, Jean-Michel;
Gabriel, Pierre;
Shang, Peipei

Publication type:

Article

c-Fos expression in the limbic thalamus following thermoregulatory and wake–sleep changes in the rat.

Published in:

Experimental Brain Research, 2019, v. 237, n. 6, p. 1397, doi. 10.1007/s00221-019-05521-2

By:

Luppi, Marco;
Cerri, Matteo;
Di Cristoforo, Alessia;
Hitrec, Timna;
Dentico, Daniela;
Del Vecchio, Flavia;
Martelli, Davide;
Perez, Emanuele;
Tupone, Domenico;
Zamboni, Giovanni;
Amici, Roberto

Publication type:

Article

A system-level approach for deciphering the transcriptional response to prion infection.

Published in:

Bioinformatics, 2011, v. 27, n. 24, p. 3407, doi. 10.1093/bioinformatics/btr580

By:

Zampieri, Mattia;
Legname, Giuseppe;
Segrè, Daniel;
Altafini, Claudio

Publication type:

Article

Principal network analysis: identification of subnetworks representing major dynamics using gene expression data.

Published in:

Bioinformatics, 2011, v. 27, n. 3, p. 391, doi. 10.1093/bioinformatics/btq670

By:

Kim, Yongsoo;
Kim, Taek-Kyun;
Kim, Yungu;
Yoo, Jiho;
You, Sungyong;
Lee, Inyoul;
Carlson, George;
Hood, Leroy;
Choi, Seungjin;
Hwang, Daehee

Publication type:

Article

Prions: a threat to health security and the need for effective medical countermeasures.

Published in:

Global Health Journal, 2023, v. 7, n. 1, p. 43, doi. 10.1016/j.glohj.2023.02.004

By:

Lee, Ying-Chiang J.

Publication type:

Article

The shifting spectrum of emerging infectious diseases.

Published in:

Medical Laboratory Observer (MLO), 2019, v. 51, n. 3, p. 14

By:

Ross, Linda L.;
Pifer, Linda L. Williford

Publication type:

Article

The proper handling of CJD-infected patient samples in the pathology laboratory.

Published in:

Medical Laboratory Observer (MLO), 2018, v. 50, n. 5, p. 40

By:

Pizzella, Nadine;
Kurec, Anthony

Publication type:

Article

Brain aging is faithfully modelled in organotypic brain slices and accelerated by prions.

Published in:

Communications Biology, 2022, v. 5, n. 1, p. 1, doi. 10.1038/s42003-022-03496-5

By:

Liu, Yingjun;
Senatore, Assunta;
Sorce, Silvia;
Nuvolone, Mario;
Guo, Jingjing;
Gümüş, Zeynep H.;
Aguzzi, Adriano

Publication type:

Article

Brain aging is faithfully modelled in organotypic brain slices and accelerated by prions.

Published in:

Communications Biology, 2022, v. 5, n. 1, p. 1, doi. 10.1038/s42003-022-03496-5

By:

Liu, Yingjun;
Senatore, Assunta;
Sorce, Silvia;
Nuvolone, Mario;
Guo, Jingjing;
Gümüş, Zeynep H.;
Aguzzi, Adriano

Publication type:

Article

Brain aging is faithfully modelled in organotypic brain slices and accelerated by prions.

Published in:

Communications Biology, 2022, v. 5, n. 1, p. 1, doi. 10.1038/s42003-022-03496-5

By:

Liu, Yingjun;
Senatore, Assunta;
Sorce, Silvia;
Nuvolone, Mario;
Guo, Jingjing;
Gümüş, Zeynep H.;
Aguzzi, Adriano

Publication type:

Article

Apparent stability masks underlying change in a mule deer herd with unmanaged chronic wasting disease.

Published in:

Communications Biology, 2022, v. 5, n. 1, p. 1, doi. 10.1038/s42003-021-02951-z

By:

Fisher, Mark C.;
Prioreschi, Ryan A.;
Wolfe, Lisa L.;
Runge, Jonathan P.;
Griffin, Karen A.;
Swanson, Heather M.;
Miller, Michael W.

Publication type:

Article

Spectrum and Pattern of Movement Disorders in Patients with Sporadic Creutzfeldt-Jakob Disease.

Published in:

Tremor & Other Hyperkinetic Movements, 2023, v. 13, p. 1, doi. 10.5334/tohm.753

By:

Gurram, Sandeep;
Holla, Vikram V.;
Sharma, Praveen;
Kamble, Nitish;
Saini, Jitender;
Netravathi, Manjunath;
Yadav, Ravi;
Pal, Pramod Kumar

Publication type:

Article

Antiprion immunotherapy: to suppress or to stimulate?

Published in:

Nature Reviews Immunology, 2004, v. 4, n. 9, p. 725, doi. 10.1038/nri1437

By:

Aguzzi, Adriano;
Sigurdson, Christina J.

Publication type:

Article

Infectious disease: Immunotherapy for prion disease.

Published in:

Nature Reviews Immunology, 2003, v. 3, n. 4, p. 267, doi. 10.1038/nri1076

By:

Buckland, Jenny

Publication type:

Article

IMMUNOTHERAPY: Friend or foe?

Published in:

Nature Reviews Immunology, 2001, v. 1, n. 1, p. 7, doi. 10.1038/35095537

By:

Bell, Jen

Publication type:

Article

A Preliminary Study for the Determination of Prion Disease for Farm Animals in Ethiopia.

Published in:

Journal of Animal Production / Hayvansal Üretim, 2020, v. 61, n. 1, p. 17, doi. 10.29185/hayuretim.583573

By:

TEFERDEGN, Eden Yitna;
ÜN, Cemal;
TAŞKIN, Turğay

Publication type:

Article

The novel T107I Inherited prion disease can present as a clinical and biomarker mimic of familial Alzheimer's disease.

Published in:

Journal of Neurogenetics, 2025, v. 39, n. 1, p. 16, doi. 10.1080/01677063.2024.2440395

By:

Holm-Mercer, Leah;
Coysh, Thomas;
Mok, Tze How;
Rudge, Peter;
Reisz, Zita;
Troakes, Claire;
Al-Sarraj, Safa;
Campbell, Tracy;
Hosszu, Laszlo L.P.;
Bieschke, Jan;
Zhang, Fuquan;
Wadsworth, Jonathan D.F.;
Smith, Colin;
Jenkinson, Jenna;
Rittman, Timothy;
Brandner, Sebastian;
Jaunmuktane, Zane;
Collinge, John;
Mead, Simon

Publication type:

Article

Approaches to therapy against prion diseases focused on the individual defence system.

Published in:

AIMS Molecular Science, 2017, v. 4, n. 3, p. 241, doi. 10.3934/molsci.2017.3.241

By:

Monzón, Marta

Publication type:

Article

Treatment of Prion Disease: Is it possible? A Review.

Published in:

Jordan Medical Journal, 2025, v. 59, n. 2, p. 312, doi. 10.35516/jmj.v59i2.2211

By:

Devaraj, Navin Kumar

Publication type:

Article

FDG‐PET patterns associate with survival in patients with prion disease.

Published in:

Annals of Clinical & Translational Neurology, 2024, v. 11, n. 12, p. 3227, doi. 10.1002/acn3.52230

By:

Corriveau‐Lecavalier, Nick;
Piura, Yoav D.;
Appleby, Brian S.;
Shir, Dror;
Barnard, Leland R.;
Gogineni, Venkatsampath;
Jones, David T.;
Day, Gregory S.

Publication type:

Article

Detection of prions in the urine of patients affected by sporadic Creutzfeldt–Jakob disease.

Published in:

Annals of Clinical & Translational Neurology, 2023, v. 10, n. 12, p. 2316, doi. 10.1002/acn3.51919

By:

Pritzkow, Sandra;
Ramirez, Frank;
Lyon, Adam;
Schulz, Paul E.;
Appleby, Brian;
Moda, Fabio;
Ramirez, Santiago;
Notari, Silvio;
Gambetti, Pierluigi;
Soto, Claudio

Publication type:

Article

Role of cellular prion protein in splenic CD4<sup>+</sup> T cell differentiation in cerebral ischaemic/reperfusion.

Published in:

Annals of Clinical & Translational Neurology, 2021, v. 8, n. 10, p. 2040, doi. 10.1002/acn3.51453

By:

Zhang, Baizhuo;
Yin, Xiang;
Lang, Yue;
Han, Xiaoou;
Shao, Jie;
Bai, Rongrong;
Cui, Li

Publication type:

Article

Baseline neuropsychological profiles in prion disease predict survival time.

Published in:

Annals of Clinical & Translational Neurology, 2020, v. 7, n. 9, p. 1535, doi. 10.1002/acn3.51115

By:

Sundaram, Saranya E.;
Staffaroni, Adam M.;
Walker, Nicole C.;
Casaletto, Kaitlin B.;
Casey, Megan;
Golubjatnikov, Aili;
Metcalf, Stacy;
O'Leary, Kelly;
Wong, Katherine;
Benisano, Kendra;
Forner, Sven;
Gonzalez Catalan, Marta;
Allen, Isabel E.;
Rosen, Howard J.;
Kramer, Joel H.;
Geschwind, Michael D.

Publication type:

Article

Transmission of CJD from nasal brushings but not spinal fluid or RT‐QuIC product.

Published in:

Annals of Clinical & Translational Neurology, 2020, v. 7, n. 6, p. 932, doi. 10.1002/acn3.51057

By:

Raymond, Gregory J.;
Race, Brent;
Orrú, Christina D.;
Raymond, Lynne D.;
Bongianni, Matilde;
Fiorini, Michele;
Groveman, Bradley R.;
Ferrari, Sergio;
Sacchetto, Luca;
Hughson, Andrew G.;
Monaco, Salvatore;
Pocchiari, Maurizio;
Zanusso, Gianluigi;
Caughey, Byron

Publication type:

Article

Variably protease‐sensitive prionopathy presenting within ALS/FTD spectrum.

Published in:

Annals of Clinical & Translational Neurology, 2018, v. 5, n. 10, p. 1297, doi. 10.1002/acn3.632

By:

Lladó, Albert;
Valls, Josep;
Sánchez‐Valle, Raquel;
Vicente‐Pascual, Mikel;
Nos, Carlos;
Grau‐Rivera, Oriol;
Gelpí, Ellen;
Rossi, Marcello;
Parchi, Piero;
Gámez, Josep;
Ávila Polo, Rainiero;
Zerr, Inga;
Llorens, Franc;
Ferrer, Isidre

Publication type:

Article

Aggregation of MBP in chronic demyelination.

Published in:

Annals of Clinical & Translational Neurology, 2015, v. 2, n. 7, p. 711, doi. 10.1002/acn3.207

By:

Frid, Kati;
Einstein, Ofira;
Friedman‐Levi, Yael;
Binyamin, Orli;
Ben‐Hur, Tamir;
Gabizon, Ruth

Publication type:

Article

The cognitive profile of prion disease: a prospective clinical and imaging study.

Published in:

Annals of Clinical & Translational Neurology, 2015, v. 2, n. 5, p. 548, doi. 10.1002/acn3.195

By:

Caine, Diana;
Tinelli, Renata J.;
Hyare, Harpreet;
De Vita, Enrico;
Lowe, Jessica;
Lukic, Ana;
Thompson, Andrew;
Porter, Marie‐Claire;
Cipolotti, Lisa;
Rudge, Peter;
Collinge, John;
Mead, Simon

Publication type:

Article

Thirty years of fatal familial insomnia and autonomic research: celebrating the past, embracing the future.

Published in:

2021

By:

Cortelli, Pietro

Publication type:

Editorial