Works matching DE "PATHOPHYSIOLOGY of amyotrophic lateral sclerosis"

Results: 30

Theme 13 Respiratory and nutritional management.

Published in:: 2017
Publication type:: Abstract

Motor neuron disease mortality rates in U.S. states are associated with well water use.

Published in:

2016

By:

Schwartz, Gary G.;
Klug, Marilyn G.

Publication type:

Case Study

The selective anatomical vulnerability of ALS: ‘disease-defining’ and ‘disease-defying’ brain regions.

Published in:

Amyotrophic Lateral Sclerosis & Frontotemporal Degeneration, 2016, v. 17, n. 7/8/2016, p. 561, doi. 10.3109/21678421.2016.1173702

By:

Bede, Peter;
Iyer, Parameswaran M.;
Schuster, Christina;
Elamin, Marwa;
Mclaughlin, Russell L.;
Kenna, Kevin;
Hardiman, Orla

Publication type:

Article

ALSUntangled No. 35: Hyperbaric Oxygen Therapy*.

Published in:: Amyotrophic Lateral Sclerosis & Frontotemporal Degeneration, 2016, v. 17, n. 7/8/2016, p. 622, doi. 10.3109/21678421.2016.1172818
Publication type:: Article

Plasma metabolomic biomarker panel to distinguish patients with amyotrophic lateral sclerosis from disease mimics.

Published in:

Amyotrophic Lateral Sclerosis & Frontotemporal Degeneration, 2014, v. 15, n. 5/6, p. 362, doi. 10.3109/21678421.2014.908311

By:

Lawton, Kay A.;
Brown, Meredith V.;
Alexander, Danny;
Li, Zhen;
Wulff, Jacob E.;
Lawson, Robert;
Jaffa, Matt;
Milburn, Mike V.;
Ryals, John A.;
Bowser, Robert;
Cudkowicz, Merit E.;
Berry, James D.

Publication type:

Article

Opportunities for improving therapy development in ALS.

Published in:

Amyotrophic Lateral Sclerosis & Frontotemporal Degeneration, 2014, v. 15, n. 3/4, p. 169, doi. 10.3109/21678421.2013.872662

By:

Bruijn, Lucie;
Cudkowicz, Merit

Publication type:

Article

Assessment of disease progression and functional benefit in neurodegenerative disease: Can we tell the difference?

Published in:

Amyotrophic Lateral Sclerosis & Frontotemporal Degeneration, 2014, v. 15, n. 5/6, p. 337, doi. 10.3109/21678421.2014.918150

By:

Shefner, Jeremy M.;
Mihaila, Dragos

Publication type:

Article

Economic burden of amyotrophic lateral sclerosis: A Canadian study of out-of-pocket expenses.

Published in:

Amyotrophic Lateral Sclerosis & Frontotemporal Degeneration, 2014, v. 15, n. 5/6, p. 426, doi. 10.3109/21678421.2014.932382

By:

Gladman, Matthew;
Dharamshi, Celina;
Zinman, Lorne

Publication type:

Article

Atypical Alzheimer's disease in an elderly United States resident with amyotrophic lateral sclerosis and pathological tau in spinal motor neurons.

Published in:

Amyotrophic Lateral Sclerosis & Frontotemporal Degeneration, 2014, v. 15, n. 5/6, p. 466, doi. 10.3109/21678421.2014.903973

By:

McCluskey, Leo F.;
Geser, Felix;
Elman, Lauren B.;
Van Deerlin, Vivianna M.;
Robinson, John L.;
Lee, Virginia M.-Y.;
Trojanowski, John Q.

Publication type:

Article

Increased iron level in motor cortex of amyotrophic lateral sclerosis patients: An in vivo MR study.

Published in:

Amyotrophic Lateral Sclerosis & Frontotemporal Degeneration, 2014, v. 15, n. 5/6, p. 357, doi. 10.3109/21678421.2014.906618

By:

Yu, Jixu;
Qi, Faying;
Wang, Nian;
Gao, Peihong;
Dai, Shouping;
Lu, Yucheng;
Su, Quanping;
Du, Yifeng;
Che, Fengyuan

Publication type:

Article

Multicentre quality control evaluation of different biomarker candidates for amyotrophic lateral sclerosis.

Published in:

Amyotrophic Lateral Sclerosis & Frontotemporal Degeneration, 2014, v. 15, n. 5/6, p. 344, doi. 10.3109/21678421.2014.884592

By:

Lehnert, Stefan;
Costa, Julia;
de Carvalho, Mamede;
Kirby, Janine;
Kuzma-Kozakiewicz, Magdalena;
Morelli, Claudia;
Robberecht, Wim;
Shaw, Pamela;
Silani, Vincenzo;
Steinacker, Petra;
Tumani, Hayrettin;
Van Damme, Philip;
Ludolph, Albert;
Otto, Markus

Publication type:

Article

RNA metabolism in ALS: When normal processes become pathological.

Published in:

Amyotrophic Lateral Sclerosis & Frontotemporal Degeneration, 2014, v. 15, n. 5/6, p. 321, doi. 10.3109/21678421.2014.881377

By:

Droppelmann, Cristian A.;
Campos-Melo, Danae;
Ishtiaq, Muhammad;
Volkening, Kathryn;
Strong, Michael J.

Publication type:

Article

The impact of physical impairment on emotional well-being in ALS.

Published in:

Amyotrophic Lateral Sclerosis & Frontotemporal Degeneration, 2014, v. 15, n. 5/6, p. 392, doi. 10.3109/21678421.2014.932380

By:

Abdulla, Susanne;
Vielhaber, Stefan;
Kollewe, Katja;
Machts, Judith;
Heinze, Hans-Jochen;
Dengler, Reinhard;
Petri, Susanne

Publication type:

Article

Cortical hyperexcitability and the split-hand plus phenomenon: Pathophysiological insights in ALS.

Published in:

Amyotrophic Lateral Sclerosis & Frontotemporal Degeneration, 2014, v. 15, n. 3/4, p. 250, doi. 10.3109/21678421.2013.872150

By:

Bae, Jong Seok;
Menon, Parvathi;
Mioshi, Eneida;
Kiernan, Matthew C.;
Vucic, Steve

Publication type:

Article

Distinct patterns of cortical atrophy in ALS patients with or without dementia: An MRI VBM study.

Published in:

Amyotrophic Lateral Sclerosis & Frontotemporal Degeneration, 2014, v. 15, n. 3/4, p. 216, doi. 10.3109/21678421.2014.880179

By:

Rajagopalan, Venkateswaran;
Pioro, Erik P.

Publication type:

Article

Detection of a novel frameshift mutation and regions with homozygosis within ARHGEF28 gene in familial amyotrophic lateral sclerosis.

Published in:

Amyotrophic Lateral Sclerosis & Frontotemporal Degeneration, 2013, v. 14, n. 5/6, p. 444, doi. 10.3109/21678421.2012.758288

By:

Droppelmann, Cristian A.;
Wang, Jian;
Campos-Melo, Danae;
Keller, Brian;
Volkening, Kathryn;
Hegele, Robert A.;
Strong, Michael J.

Publication type:

Article

Amyotrophic lateral sclerosis: Mayhem-making microglia.

Published in:

Nature Medicine, 2014, v. 20, n. 4, p. 349, doi. 10.1038/nm.3536

By:

Chmielnicki, Eva

Publication type:

Article

Immunization with a Myelin-Derived Antigen Activates the Brain's Choroid Plexus for Recruitment of Immunoregulatory Cells to the CNS and Attenuates Disease Progression in a Mouse Model of ALS.

Published in:

Journal of Neuroscience, 2015, p. 6381, doi. 10.1523/JNEUROSCI.3644-14.2015

By:

Kunis, Gilad;
Baruch, Kuti;
Miller, Omer;
Schwartz, Michal

Publication type:

Article

Low-frequency magnetic fields do not aggravate disease in mouse models of Alzheimer's disease and amyotrophic lateral sclerosis.

Published in:

Scientific Reports, 2015, p. 8585, doi. 10.1038/srep08585

By:

Liebl, Martina P.;
Windschmitt, Johannes;
Besemer, Anna S.;
Schäfer, Anne-Kathrin;
Reber, Helmut;
Behl, Christian;
Clement, Albrecht M.

Publication type:

Article

Immunoablation and Stem Cell Transplantation in Amyotrophic Lateral Sclerosis: The Ultimate Test for the Autoimmune pathogenesis Hypothesis.

Published in:

Frontiers in Neurology, 2016, p. 1, doi. 10.3389/fneur.2016.00012

By:

Ross, Mark A.;
Leis, A. Arturo;
Verheijde, Joseph L.;
Leis, Jose F.

Publication type:

Article

Cerebrospinal fluid cytotoxicity in amyotrophic lateral sclerosis and sample size.

Published in:

Acta Neurologica Scandinavica, 2017, v. 136, n. 1, p. 79, doi. 10.1111/ane.12746

By:

Galán, L.;
Matias‐Guiu, J. A.;
Guerrero‐Sola, A.;
Matías‐Guiu, J.

Publication type:

Article

Cerebrospinal fluid cytotoxicity does not affect survival in amyotrophic lateral sclerosis; Methodological issues.

Published in:

Acta Neurologica Scandinavica, 2017, v. 136, n. 1, p. 78, doi. 10.1111/ane.12747

By:

Pakzad, R.;
Safiri, S.

Publication type:

Article

Brca1 is expressed in human microglia and is dysregulated in human and animal model of ALS.

Published in:

Molecular Neurodegeneration, 2015, v. 10, n. 1, p. 1, doi. 10.1186/s13024-015-0023-x

By:

Noristani, Harun Najib;
Sabourin, Jean Charles;
Gerber, Yannick Nicolas;
Teigell, Marisa;
Sommacal, Andreas;
Vivanco, Maria dM;
Weber, Markus;
Perrin, Florence Evelyne

Publication type:

Article

In vivo kinetic approach reveals slow SOD1 turnover in the CNS.

Published in:

Journal of Clinical Investigation, 2015, v. 125, n. 7, p. 2772, doi. 10.1172/JCI80705

By:

Crisp, Matthew J.;
Mawuenyega, Kwasi C.;
Patterson, Bruce W.;
Reddy, Naveen C.;
Chott, Robert;
Self, Wade K.;
Weihl, Conrad C.;
Jockel-Balsarotti, Jennifer;
Varadhachary, Arun S.;
Bucelli, Robert C.;
Yarasheski, Kevin E.;
Bateman, Randall;
Miller, Timothy M.

Publication type:

Article

Cell Death-Autophagy Loop and Glutamate-Glutamine Cycle in Amyotrophic Lateral Sclerosis.

Published in:

Frontiers in Molecular Neuroscience, 2017, p. 1, doi. 10.3389/fnmol.2017.00231

By:

Shu Yuan;
Zhong-Wei Zhang;
Zi-Lin Li

Publication type:

Article

Motor Neuron Susceptibility in ALS/FTD.

Published in:

Frontiers in Neuroscience, 2019, p. N.PAG, doi. 10.3389/fnins.2019.00532

By:

Ragagnin, Audrey M. G.;
Shadfar, Sina;
Vidal, Marta;
Jamali, Md Shafi;
Atkin, Julie D.

Publication type:

Article

Evidence for an early innate immune response in the motor cortex of ALS.

Published in:

2017

By:

Jara, Javier H.;
Genç, Barış;
Stanford, Macdonell J.;
Pytel, Peter;
Roos, Raymond P.;
Weintraub, Sandra;
Mesulam, M. Marsel;
Bigio, Eileen H.;
Miller, Richard J.;
Özdinler, P. Hande

Publication type:

journal article

Peripheral monocytes are functionally altered and invade the CNS in ALS patients.

Published in:

Acta Neuropathologica, 2016, v. 132, n. 3, p. 391, doi. 10.1007/s00401-016-1548-y

By:

Zondler, Lisa;
Müller, Kathrin;
Khalaji, Samira;
Bliederhäuser, Corinna;
Ruf, Wolfgang;
Grozdanov, Veselin;
Thiemann, Meinolf;
Fundel-Clemes, Katrin;
Freischmidt, Axel;
Holzmann, Karlheinz;
Strobel, Benjamin;
Weydt, Patrick;
Witting, Anke;
Thal, Dietmar;
Helferich, Anika;
Hengerer, Bastian;
Gottschalk, Kay-Eberhard;
Hill, Oliver;
Kluge, Michael;
Ludolph, Albert

Publication type:

Article

Prion-like propagation of mutant SOD1 misfolding and motor neuron disease spread along neuroanatomical pathways.

Published in:

Acta Neuropathologica, 2016, v. 131, n. 1, p. 103, doi. 10.1007/s00401-015-1514-0

By:

Ayers, Jacob;
Fromholt, Susan;
O'Neal, Veronica;
Diamond, Jeffrey;
Borchelt, David

Publication type:

Article

Antecedent Disease Is Less Prevalent in Amyotrophic Lateral Sclerosis.

Published in:

Neurodegenerative Diseases, 2015, v. 15, n. 2, p. 109, doi. 10.1159/000369812

By:

Mitchell, Cassie S.;
Hollinger, Sabrina K.;
Goswami, Shivani D.;
Polak, Meraida a.;
Lee, Robert H.;
Glass, Jonathan D.

Publication type:

Article