Works matching DE "ORNITHINE"


Results: 385
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    Polyamine depletion limits progression of acute leukaemia.

    Published in:
    International Journal of Cancer, 2025, v. 156, n. 12, p. 2360, doi. 10.1002/ijc.35362
    By:
    • Gao, Weiman;
    • Karsa, Mawar;
    • Xiao, Lin;
    • Spurling, Dayna;
    • Karsa, Ayu;
    • Ronca, Emma;
    • Bongers, Angelika;
    • Guo, Xinyi;
    • Mayoh, Chelsea;
    • Azfar, Mujahid;
    • Verhelst, Steven H. L.;
    • Tanaka, Katsunori;
    • Cheung, Laurence C.;
    • Kotecha, Rishi S.;
    • Lock, Richard B.;
    • Burns, Mark R.;
    • Vangheluwe, Peter;
    • Norris, Murray D.;
    • Haber, Michelle;
    • Somers, Klaartje
    Publication type:
    Article
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    Predicting the disease severity in male individuals with ornithine transcarbamylase deficiency.

    Published in:
    Annals of Clinical & Translational Neurology, 2022, v. 9, n. 11, p. 1715, doi. 10.1002/acn3.51668
    By:
    • Scharre, Svenja;
    • Posset, Roland;
    • Garbade, Sven F.;
    • Gleich, Florian;
    • Seidl, Marie J.;
    • Druck, Ann‐Catrin;
    • Okun, Jürgen G.;
    • Gropman, Andrea L.;
    • Nagamani, Sandesh C. S.;
    • Hoffmann, Georg F.;
    • Kölker, Stefan;
    • Zielonka, Matthias;
    • Ah Mew, Nicholas;
    • Baumgartner, Matthias R.;
    • Berry, Gerard T.;
    • Berry, Susan A.;
    • Burrage, Lindsay;
    • Diaz, George A.;
    • Ficicioglu, Can;
    • Kisin, Genya
    Publication type:
    Article
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    Ageing Investigation Using Two-Time-Point Metabolomics Data from KORA and CARLA Studies.

    Published in:
    Metabolites (2218-1989), 2019, v. 9, n. 3, p. 44, doi. 10.3390/metabo9030044
    By:
    • Chak, Choiwai Maggie;
    • Lacruz, Maria Elena;
    • Adam, Jonathan;
    • Brandmaier, Stefan;
    • Covic, Marcela;
    • Huang, Jialing;
    • Meisinger, Christa;
    • Tiller, Daniel;
    • Prehn, Cornelia;
    • Adamski, Jerzy;
    • Berger, Ursula;
    • Gieger, Christian;
    • Peters, Annette;
    • Kluttig, Alexander;
    • Wang-Sattler, Rui
    Publication type:
    Article
    34

    Three-Country Snapshot of Ornithine Transcarbamylase Deficiency.

    Published in:
    2022
    By:
    • Seker Yilmaz, Berna;
    • Baruteau, Julien;
    • Arslan, Nur;
    • Aydin, Halil Ibrahim;
    • Barth, Magalie;
    • Bozaci, Ayse Ergul;
    • Brassier, Anais;
    • Canda, Ebru;
    • Cano, Aline;
    • Chronopoulou, Efstathia;
    • Connolly, Grainne M.;
    • Damaj, Lena;
    • Dawson, Charlotte;
    • Dobbelaere, Dries;
    • Douillard, Claire;
    • Eminoglu, Fatma Tuba;
    • Erdol, Sahin;
    • Ersoy, Melike;
    • Fang, Sherry;
    • Feillet, François
    Publication type:
    Case Study
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    Ornithine In Vivo Administration Disrupts Redox Homeostasis and Decreases Synaptic Na, K-ATPase Activity in Cerebellum of Adolescent Rats: Implications for the Pathogenesis of Hyperornithinemia-Hyperammonemia-Homocitrullinuria (HHH) Syndrome.

    Published in:
    Cellular & Molecular Neurobiology, 2015, v. 35, n. 6, p. 797, doi. 10.1007/s10571-015-0173-y
    By:
    • Zanatta, Ângela;
    • Viegas, Carolina;
    • Hickmann, Fernanda;
    • Oliveira Monteiro, Wagner;
    • Sitta, Angela;
    • Moura Coelho, Daniela;
    • Vargas, Carmen;
    • Leipnitz, Guilhian;
    • Wajner, Moacir
    Publication type:
    Article
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