Works about CYSTIC fibrosis transmembrane conductance regulator
Results: 1410
Eligibility of Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) modulator therapies: cohort of cystic fibrosis registry of Türkiye.
- Published in:
- Turkish Journal of Pediatrics, 2025, v. 67, n. 1, p. 22, doi. 10.24953/turkjpediatr.2025.4680
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- Publication type:
- Article
Reply to Martin and Grasemann: Is There a Role for Lumacaftor/Ivacaftor in Young Children with Cystic Fibrosis?
- Published in:
- Annals of the American Thoracic Society, 2025, v. 22, n. 3, p. 469, doi. 10.1513/AnnalsATS.202411-1237LE
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- Publication type:
- Article
The RNA-Binding Protein Tristetraprolin Contributes to CFTR mRNA Stability in Cystic Fibrosis.
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- American Journal of Respiratory Cell & Molecular Biology, 2025, v. 72, n. 3, p. 320, doi. 10.1165/rcmb.2023-0209OC
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- Publication type:
- Article
Perspectives in MicroRNA Therapeutics for Cystic Fibrosis.
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- Non-Coding RNA, 2025, v. 11, n. 1, p. 3, doi. 10.3390/ncrna11010003
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- Publication type:
- Article
The 12-Year Experience of the Hungarian Pancreatic Study Group.
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- Journal of Clinical Medicine, 2025, v. 14, n. 4, p. 1362, doi. 10.3390/jcm14041362
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- Publication type:
- Article
OTX2 regulates CFTR expression during endoderm differentiation and occupies 3′ cis‐regulatory elements.
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- Developmental Dynamics, 2021, v. 250, n. 5, p. 684, doi. 10.1002/dvdy.293
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- Publication type:
- Article
A chalcone derivative retards renal cyst enlargement by inhibiting fluid secretion and cell proliferation in an in vitro model of polycystic kidney disease.
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- Clinical & Experimental Nephrology, 2021, v. 25, n. 9, p. 944, doi. 10.1007/s10157-021-02080-1
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- Article
ADPKD and metformin: from bench to bedside.
- Published in:
- 2019
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- Publication type:
- Letter
Correction: Role of Hydrophobic Amino-Acid Side-Chains in the Narrow Selectivity Filter of the CFTR Chloride Channel Pore in Conductance and Selectivity.
- Published in:
- 2024
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- Publication type:
- Correction Notice
Role of Hydrophobic Amino-Acid Side-Chains in the Narrow Selectivity Filter of the CFTR Chloride Channel Pore in Conductance and Selectivity.
- Published in:
- Journal of Membrane Biology, 2023, v. 256, n. 4-6, p. 433, doi. 10.1007/s00232-023-00294-w
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- Publication type:
- Article
The Effect of Dynasore Upon the Negative Interaction Between ENaC and CFTR Channels in Xenopus laevis Oocytes.
- Published in:
- Journal of Membrane Biology, 2022, v. 255, n. 1, p. 61, doi. 10.1007/s00232-021-00212-y
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- Publication type:
- Article
Ouabain Regulates CFTR-Mediated Anion Secretion and Na,K-ATPase Transport in ADPKD Cells.
- Published in:
- 2015
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- Publication type:
- journal article
Analysis of a hybrid numerical method - decomposing leaf hydraulic conductance.
- Published in:
- Letters in Biomathematics, 2018, v. 5, n. 1, p. 98, doi. 10.1080/23737867.2018.1463183
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- Publication type:
- Article
CFTR may influence sperm apoptosis and vitality via the AMPK signaling pathway.
- Published in:
- Chinese Journal of Andrology, 2024, v. 38, n. 4, p. 33, doi. 10.3969/j.issn.1008-0848.2024.04.005
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- Publication type:
- Article
Analysis of AlphaMissense data in different protein groups and structural context.
- Published in:
- Scientific Data, 2024, v. 11, n. 1, p. 1, doi. 10.1038/s41597-024-03327-8
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- Publication type:
- Article
Social aspect as a part of HRQoL in patients with cystic fibrosis in Republic of North Macedonia.
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- Macedonian Pharmaceutical Bulletin / Makedonsko Farmacevtski Bilten, 2020, v. 66, p. 167, doi. 10.33320/maced.pharm.bull.2020.66.03.083
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- Publication type:
- Article
Abstracts of the Annual Conference of Doctoral School of Biology, University of Szeged - 2020.
- Published in:
- Acta Biologica Szegediensis, 2020, v. 64, n. 1, p. 73, doi. 10.14232/abs.2020.1.73-90
- Publication type:
- Article
The molecular mechanism of CFTR‐ and secretin‐dependent renal bicarbonate excretion.
- Published in:
- Journal of Physiology, 2021, v. 599, n. 12, p. 3003, doi. 10.1113/JP281285
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- Publication type:
- Article
Paracellular bicarbonate flux across human cystic fibrosis airway epithelia tempers changes in airway surface liquid pH.
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- Journal of Physiology, 2020, v. 598, n. 19, p. 4307, doi. 10.1113/JP280120
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- Publication type:
- Article
Suppressing 'nonsense' in cystic fibrosis.
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- Journal of Physiology, 2020, v. 598, n. 3, p. 429, doi. 10.1113/JP279267
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- Publication type:
- Article
Positional effects of premature termination codons on the biochemical and biophysical properties of CFTR.
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- Journal of Physiology, 2020, v. 598, n. 3, p. 517, doi. 10.1113/JP278418
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- Publication type:
- Article
Structural mechanisms for defective CFTR gating caused by the Q1412X mutation, a severe Class VI pathogenic mutation in cystic fibrosis.
- Published in:
- Journal of Physiology, 2019, v. 597, n. 2, p. 543, doi. 10.1113/JP277042
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- Publication type:
- Article
CrossTalk proposal: mucosal acidification drives early progressive lung disease in cystic fibrosis.
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- Journal of Physiology, 2018, v. 596, n. 16, p. 3433, doi. 10.1113/JP275425
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- Publication type:
- Article
Bicarbonate-rich fluid secretion predicted by a computational model of guinea-pig pancreatic duct epithelium.
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- Journal of Physiology, 2017, v. 595, n. 6, p. 1947, doi. 10.1113/JP273306
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- Publication type:
- Article
Altering intracellular pH reveals the kinetic basis of intraburst gating in the CFTR Cl<sup>−</sup> channel.
- Published in:
- Journal of Physiology, 2017, v. 595, n. 4, p. 1059, doi. 10.1113/JP273205
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- Publication type:
- Article
Beyond cystic fibrosis transmembrane conductance regulator (CFTR) single channel kinetics: implications for therapeutic intervention.
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- Journal of Physiology, 2017, v. 595, n. 4, p. 1015, doi. 10.1113/JP273675
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- Publication type:
- Article
Pore dilatation increases the bicarbonate permeability of CFTR, ANO1 and glycine receptor anion channels.
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- Journal of Physiology, 2016, v. 594, n. 11, p. 2929, doi. 10.1113/JP271311
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- Publication type:
- Article
Hypercapnia modulates cAMP signalling and cystic fibrosis transmembrane conductance regulator-dependent anion and fluid secretion in airway epithelia.
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- Journal of Physiology, 2016, v. 594, n. 6, p. 1643, doi. 10.1113/JP271309
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- Publication type:
- Article
Impact of the F508del mutation on ovine CFTR, a Cl<sup>−</sup> channel with enhanced conductance and ATP-dependent gating.
- Published in:
- Journal of Physiology, 2015, v. 593, n. 11, p. 2427, doi. 10.1113/JP270227
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- Publication type:
- Article
Revertant mutants modify, but do not rescue, the gating defect of the cystic fibrosis mutant G551D-CFTR.
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- Journal of Physiology, 2014, v. 592, n. 9, p. 1931, doi. 10.1113/jphysiol.2014.271817
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- Publication type:
- Article
The G551D CFTR chloride channel spurs the development of personalized medicine.
- Published in:
- Journal of Physiology, 2014, v. 592, n. 9, p. 1907, doi. 10.1113/jphysiol.2014.274464
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- Publication type:
- Article
The secret life of CFTR as a calcium-activated chloride channel.
- Published in:
- Journal of Physiology, 2013, v. 591, n. 21, p. 5273, doi. 10.1113/jphysiol.2013.261909
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- Publication type:
- Article
Study of a panel of genetic mutations in fibrocalcific pancreatic diabetes (FCPD): SPINK1 (N34S) mutation unlikely to be relevant.
- Published in:
- Scientific Reports, 2024, v. 14, n. 1, p. 1, doi. 10.1038/s41598-024-83113-z
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- Publication type:
- Article
Inhibiting CFTR through inh-172 in primary neutrophils reveals CFTR-specific functional defects.
- Published in:
- Scientific Reports, 2024, v. 14, n. 1, p. 1, doi. 10.1038/s41598-024-82535-z
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- Publication type:
- Article
Assessment of respiratory mechanics and X-ray velocimetry functional imaging in two cystic fibrosis rat models.
- Published in:
- Scientific Reports, 2024, v. 14, n. 1, p. 1, doi. 10.1038/s41598-024-71632-8
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- Publication type:
- Article
Liver biochemical indexes and cholesterol metabolism in cystic fibrosis patients with F508del/CFTR variant genotype after elexacaftor/tezacaftor/ivacaftor treatment.
- Published in:
- Scientific Reports, 2024, v. 14, n. 1, p. 1, doi. 10.1038/s41598-024-68511-7
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- Publication type:
- Article
Inflammation in the COVID-19 airway is due to inhibition of CFTR signaling by the SARS-CoV-2 spike protein.
- Published in:
- Scientific Reports, 2024, v. 14, n. 1, p. 1, doi. 10.1038/s41598-024-66473-4
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- Publication type:
- Article
The Expression of Affective Temperaments in Cystic Fibrosis Patients: Psychopathological Associations and Possible Neurobiological Mechanisms.
- Published in:
- Brain Sciences (2076-3425), 2023, v. 13, n. 4, p. 619, doi. 10.3390/brainsci13040619
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- Publication type:
- Article
The Functional Impact of VX-770 on the Cystic Fibrosis Transmembrane Conductance Regulator Is Enduring and Increases the Constitutive Activity of This Channel in Primary Airway Epithelia Generated from Healthy Donors.
- Published in:
- Biomolecules (2218-273X), 2024, v. 14, n. 11, p. 1378, doi. 10.3390/biom14111378
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- Publication type:
- Article
Matrix Metalloproteinases in Health and Disease 3.0.
- Published in:
- Biomolecules (2218-273X), 2024, v. 14, n. 9, p. 1059, doi. 10.3390/biom14091059
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- Publication type:
- Article
Cystic Fibrosis Bone Disease: The Interplay between CFTR Dysfunction and Chronic Inflammation.
- Published in:
- Biomolecules (2218-273X), 2023, v. 13, n. 3, p. 425, doi. 10.3390/biom13030425
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- Publication type:
- Article
The Role of MMPs in the Era of CFTR Modulators: An Additional Target for Cystic Fibrosis Patients?
- Published in:
- Biomolecules (2218-273X), 2023, v. 13, n. 2, p. 350, doi. 10.3390/biom13020350
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- Publication type:
- Article
An Update on CFTR Drug Discovery: Opportunities and Challenges.
- Published in:
- Biomolecules (2218-273X), 2022, v. 12, n. 6, p. 792, doi. 10.3390/biom12060792
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- Publication type:
- Article
Structural Comparative Modeling of Multi-Domain F508del CFTR.
- Published in:
- Biomolecules (2218-273X), 2022, v. 12, n. 3, p. 471, doi. 10.3390/biom12030471
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- Publication type:
- Article
NBD2 Is Required for the Rescue of Mutant F508del CFTR by a Thiazole-Based Molecule: A Class II Corrector for the Multi-Drug Therapy of Cystic Fibrosis.
- Published in:
- Biomolecules (2218-273X), 2021, v. 11, n. 10, p. 1417, doi. 10.3390/biom11101417
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- Publication type:
- Article
Lumacaftor and Matrine: Possible Therapeutic Combination to Counteract the Inflammatory Process in Cystic Fibrosis.
- Published in:
- Biomolecules (2218-273X), 2021, v. 11, n. 3, p. 422, doi. 10.3390/biom11030422
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- Publication type:
- Article
Chitosan Nanocomplexes for the Delivery of ENaC Antisense Oligonucleotides to Airway Epithelial Cells.
- Published in:
- Biomolecules (2218-273X), 2020, v. 10, n. 4, p. 553, doi. 10.3390/biom10040553
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- Publication type:
- Article
Abstracts.
- Published in:
- Haemophilia, 2019, v. 25, p. 3, doi. 10.1111/hae.13856
- Publication type:
- Article
Identification of GLPG/ABBV-2737, a Novel Class of Corrector, Which Exerts Functional Synergy With Other CFTR Modulators.
- Published in:
- Frontiers in Pharmacology, 2019, p. N.PAG, doi. 10.3389/fphar.2019.00514
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- Publication type:
- Article
Emerging Therapeutic Approaches for Cystic Fibrosis. From Gene Editing to Personalized Medicine.
- Published in:
- Frontiers in Pharmacology, 2019, p. N.PAG, doi. 10.3389/fphar.2019.00121
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- Publication type:
- Article