Works about CYSTIC fibrosis

Results: 5000

Pharmacodynamic assessment of apramycin against Mycobacterium abscessus in a hollow fibre infection model.

Published in:

Journal of Antimicrobial Chemotherapy (JAC), 2025, v. 80, n. 5, p. 1309, doi. 10.1093/jac/dkaf073

By:

Singh, Nidhi;
Dangi, Bikash;
Johnson, Jeremy J;
Louie, Arnold;
Karunanidhi, Arunkumar;
Curry, Brooke N;
Mitarai, Satoshi;
Daley, Charles L;
Hobbie, Sven N;
Bulman, Zackery P

Publication type:

Article

Three‐Dimensional Free‐Breathing Ultrashort Echo Time (UTE) <sup>1</sup>H MRI Regional Ventilation: Comparison With Hyperpolarized <sup>129</sup>Xe MRI and Pulmonary Function Testing in Healthy Volunteers and People With Cystic Fibrosis.

Published in:

NMR in Biomedicine, 2025, v. 38, n. 6, p. 1, doi. 10.1002/nbm.70033

By:

Tan, Fei;
Eddy, Rachel L.;
Diamond, Vanessa M.;
Rayment, Jonathan H.;
Larson, Peder E. Z.

Publication type:

Article

Cystic Fibrosis and Abnormal Lung Function.

Published in:

RT: The Journal for Respiratory Care Practitioners, 2025, v. 38, n. 2, p. 6

By:

PRUITT, BILL

Publication type:

Article

Clinical and laboratory findings of patients with cystic fibrosis: a single center experience from Türkiye.

Published in:

Journal of Pediatric Disease / Türkiye Çocuk Hastalıkları Dergisi, 2025, v. 19, n. 3, p. 92, doi. 10.12956/tchd.1562280

By:

Çetinkaya, Aslıhan Köse;
Doğru, Deniz;
Cinel, Güzin;
Yalçın, Ebru;
Özçelik, Uğur;
Kiper, Nural;
Özen, Hasan;
Alikaşifoğlu, Ayfer;
Şener, Burçin;
Erden, Didem Dayangaç

Publication type:

Article

Predictive Value of 1-Hour Glucose Elevations during Oral Glucose Tolerance Testing for Cystic Fibrosis-Related Diabetes.

Published in:

Pediatric Diabetes, 2023, v. 2023, p. 1, doi. 10.1155/2023/4395556

By:

Lorenz, Andrea N.;
Pyle, Laura;
Joon Ha;
Sherman, Arthur;
Cree-Green, Melanie;
Sagel, Scott D.;
Nadeau, Kristen J.;
Chan, Christine L.

Publication type:

Article

Exploring the utilisation and effectiveness of implementation science strategies by cystic fibrosis registries for healthcare improvement: a systematic review.

Published in:

European Respiratory Review, 2025, v. 34, n. 176, p. 1, doi. 10.1183/16000617.0227-2024

By:

Stirling, Rob G.;
Sood, Bhumika;
Stirling, Macken J. L.;
Kotsimbos, Tom;
Keating, Dominic T.;
Rang, Catherine E.;
Trauer, James M.;
Young, Alan C.;
Yu, Christiaan;
Bailey, Julianna;
Wark, Peter;
Melder, Angela;
Dawkins, Paul

Publication type:

Article

A Liquid Chromatography-Tandem Mass Spectrometry Method for the Quantification of Cystic Fibrosis Drugs (Caftors) in Plasma and Its Application for Therapeutic Monitoring.

Published in:

Molecules, 2025, v. 30, n. 9, p. 1866, doi. 10.3390/molecules30091866

By:

D'Atri, Valentina;
Corrado, Fabrizio;
Versace, François;
Saldanha, Susana Alves;
Mercier, Thomas;
Guidi, Monia;
Thoueille, Paul;
Blanchon, Sylvain;
Koutsokera, Angela;
Vogeser, Michael;
Marzolini, Catia;
Girardin, François;
Mitropoulou, Georgia;
Balmpouzis, Zisis;
Rochat, Isabelle;
Sauty, Alain;
Decosterd, Laurent Arthur;
Choong, Eva

Publication type:

Article

Clinical Disorders in Cystic Fibrosis That Affect Emergency Procedures—A Case Report and Review.

Published in:

Journal of Clinical Medicine, 2025, v. 14, n. 9, p. 3187, doi. 10.3390/jcm14093187

By:

Jarzynka, Sylwia;
Dobrosz, Mateusz;
Jaworski, Sebastian;
Jóźwicki, Kamil;
Wierzba, Sebastian;
Barbarska, Olga;
Minkiewicz-Zochniak, Anna

Publication type:

Article

Advances in Therapeutics for Chronic Lung Diseases: From Standard Therapies to Emerging Breakthroughs.

Published in:

Journal of Clinical Medicine, 2025, v. 14, n. 9, p. 3118, doi. 10.3390/jcm14093118

By:

Brewer, Kyle D.;
Santo, Niki V.;
Samanta, Ankur;
Nag, Ronjon;
Trotsyuk, Artem A.;
Rajadas, Jayakumar

Publication type:

Article

Paranasal Sinus Hypoplasia and Sinonasal Anatomical Variants in Cystic Fibrosis Adult Patients: A Computed- Tomography-Based Volumetric Comparison with Healthy Controls.

Published in:

Journal of Clinical Medicine, 2025, v. 14, n. 9, p. 2977, doi. 10.3390/jcm14092977

By:

Russo, Camilla;
Di Lullo, Antonella Miriam;
Ugga, Lorenzo;
Cavaliere, Michele;
Tortora, Mario;
Cuocolo, Renato;
Nele, Gisella;
Caranci, Ferdinando;
Briganti, Francesco;
Castaldo, Giuseppe;
Elefante, Andrea

Publication type:

Article

The apical mucus layer alters the pharmacological properties of the airway epithelium.

Published in:

Journal of Physiology, 2025, v. 603, n. 9, p. 2619, doi. 10.1113/JP287891

By:

Guidone, Daniela;
de Santis, Martina;
Pesce, Emanuela;
Capurro, Valeria;
Pedemonte, Nicoletta;
Galietta, Luis J. V.

Publication type:

Article

Respiratory viruses were frequently detected in young children with cystic fibrosis but had limited clinical significance.

Published in:

Acta Paediatrica, 2025, v. 114, n. 6, p. 1202, doi. 10.1111/apa.17544

By:

Cömert, Hatice N.;
Sandvik, Rikke M.;
Ma, Chih M. G.;
Buchvald, Frederik;
Schønning, Kristian;
Skov, Marianne;
Schmidt, Marika N.;
Pressler, Tacjana;
Johansen, Helle K.;
Nielsen, Kim G.

Publication type:

Article

Wound repair and immune function in the Pseudomonas infected CF lung: before and after highly effective modulator therapy.

Published in:

Frontiers in Cellular & Infection Microbiology, 2025, p. 1, doi. 10.3389/fcimb.2025.1566495

By:

Matthews, Emma Lea;
Hirsch, Meghan June;
Prokopczuk, Federico;
Jones, Luke I.;
Martínez, Eriel;
Barnes, Jarrod W.;
Krick, Stefanie

Publication type:

Article

Anti-infectives in Pediatric Patients with Cystic Fibrosis: A Comprehensive Review of Population Pharmacokinetic Analyses.

Published in:

Clinical Pharmacokinetics, 2025, v. 64, n. 5, p. 631, doi. 10.1007/s40262-025-01505-4

By:

Yaliniz, Aysenur;
El Hassani, Mehdi;
Blanchard, Ana C.;
Marsot, Amélie

Publication type:

Article

Neural network based prediction of site-specific stable mutants in wild type CFTR protein.

Published in:

Indian Journal of Biochemistry & Biophysics, 2025, v. 62, n. 5, p. 511, doi. 10.56042/ijbb.v62i5.14275

By:

Dachani, Sudharshan Reddy;
Shukla, Rishikesh;
Kakkireni, Bharath Kumar;
Sadineni, Shreyas;
Mrudula, Balla Sai;
Malothu, Ramesh;
Yata, Vinod Kumar

Publication type:

Article

Lancereaux, diabète maigre, and diabète gras revisited.

Published in:

2025

By:

Wright Jr., James R.;
McIntyre, Lynn

Publication type:

Letter

Recent developments in cystic fibrosis drug discovery: where are we today?

Published in:

Expert Opinion on Drug Discovery, 2025, v. 20, n. 5, p. 659, doi. 10.1080/17460441.2025.2490250

By:

Lopes-Pacheco, Miquéias;
Winters, Ashlyn G.;
Jackson, JaNise J.;
Olson 3rd, John A.;
Kim, Minsoo;
Ledwitch, Kaitlyn V.;
Tedman, Austin;
Jhangiani, Ashish R.;
Schlebach, Jonathan P.;
Meiler, Jens;
Plate, Lars;
Oliver, Kathryn E.

Publication type:

Article

The Prognostic Significance of MELD-XI in Patients Admitted to the Intensive Care Unit for Respiratory Failure.

Published in:

Thoracic Research & Practice, 2025, v. 26, n. 3, p. 115, doi. 10.4274/ThoracResPract.2024.24047

By:

Arslan, Fatma;
Timurhan, Yağmur Gizem;
Mülazımoğlu, Deniz Doğan;
Öz, Miraç;
Kaya, Aslıhan Gürün;
Erol, Serhat;
Çiledağ, Aydın;
Kaya, Akın

Publication type:

Article

Improved quality of life in cystic fibrosis patients observed up to 36 months after starting Elexacaftor/Tezacaftor/Ivacaftor treatment.

Published in:

Journal of Patient-Reported Outcomes, 2025, v. 9, n. 1, p. 1, doi. 10.1186/s41687-025-00879-0

By:

Francesca, Buniotto;
Gloria, Tridello;
Antonella, De Scolari;
Ilaria, Meneghelli;
Emily, Pintani;
Sandra, Perobelli;
Marco, Cipolli

Publication type:

Article

Sodium aescinate promotes apoptosis of pancreatic stellate cells and alleviates pancreatic fibrosis by inhibiting the PI3K/Akt/FOXO1 signaling pathways.

Published in:

Frontiers in Pharmacology, 2025, p. 1, doi. 10.3389/fphar.2025.1554260

By:

Wang, Qing-Yun;
Xu, Bai-Yan;
Wang, Yi;
Lin, Yan-Mei;
Zheng, Lin-Fu;
Liu, Gang;
Li, Da-Zhou;
Jiang, Chuan-Shen;
Wang, Wen;
Zeng, Xiang-Peng

Publication type:

Article

Advances in gut-lung axis research: clinical perspectives on pneumonia prevention and treatment.

Published in:

Frontiers in Immunology, 2025, p. 1, doi. 10.3389/fimmu.2025.1576141

By:

Ye, Fang;
Li, Linnan;
Wang, Jiao;
Yang, Hongfeng

Publication type:

Article

Roscovitine enhances the bactericidal activity of the airway surface liquid of the cystic fibrosis bronchial epithelium but does not protect against Pseudomonas aeruginosa infection.

Published in:

PLoS ONE, 2025, v. 20, n. 5, p. 1, doi. 10.1371/journal.pone.0321996

By:

Maupas, Adrien;
Muggeo, Anaëlle;
Vermeulen, Pierre;
Moussalih, Sophie;
Sage, Edouard;
Luczka-Majérus, Emilie;
Coraux, Christelle;
Guillard, Thomas

Publication type:

Article

Living with cystic fibrosis during the COVID-19 pandemic: An interpretive description of healthcare access from patients with cystic fibrosis and their providers in Alberta, Canada.

Published in:

PLoS ONE, 2025, v. 20, n. 5, p. 1, doi. 10.1371/journal.pone.0322911

By:

Brehon, Katelyn;
Hung, Pam;
Miciak, Maxi;
Leung, Winnie M.;
Perreault, Kadija;
Gross, Douglas P.;
Weatherald, Jason;
Ronksley, Paul E.;
Stickland, Michael K.;
Lam, Grace Y.

Publication type:

Article

Sex disparities in cystic fibrosis in the era of highly effective modulator treatment.

Published in:

BMC Pulmonary Medicine, 2025, v. 25, n. 1, p. 1, doi. 10.1186/s12890-025-03621-0

By:

McNally, Emma;
Casey, Michelle

Publication type:

Article

Toxicology and TDM.

Published in:: Clinical Chemistry & Laboratory Medicine, 2025, v. 63, n. 1, p. s2643, doi. 10.1515/cclm-2025-8071
Publication type:: Article

Genetic diseases.

Published in:: Clinical Chemistry & Laboratory Medicine, 2025, v. 63, n. 1, p. s1285, doi. 10.1515/cclm-2025-8047
Publication type:: Article

Sleep Disturbances and Depression in Adults with Steady- State Bronchiectasis.

Published in:

JPMI: Journal of Postgraduate Medical Institute, 2024, v. 38, n. 4, p. 295, doi. 10.54079/jpmi.38.4.3410

By:

Rehman, Iqra;
Zaman, Syed Arif Saeed;
Ashraf, Junaid;
Fayyaz, Maria;
Naseem, Sidra;
Akram, Fazeelat

Publication type:

Article

CFTR Modulators Redefining Cystic Fibrosis Care in the Youngest Patients.

Published in:

RT: The Journal for Respiratory Care Practitioners, 2023, v. 36, n. 5, p. 10

By:

ARNETT, ALYX

Publication type:

Article

The PFT Infection Control Practices That Saw New Popularity During the Pandemic.

Published in:

RT: The Journal for Respiratory Care Practitioners, 2021, v. 34, n. 7, p. 10

By:

SPEAR, LISA

Publication type:

Article

The Latest Respiratory Care News.

Published in:: RT: The Journal for Respiratory Care Practitioners, 2019, p. 6
Publication type:: Article

Cystic Fibrosis: Ivacaftor/Kalydeco May Reduce Common Lung Infections.

Published in:: RT: The Journal for Respiratory Care Practitioners, 2019, p. 4
Publication type:: Article

Airway Clearance Adherence: Self-reporting and Self-subsistence Ineffective.

Published in:: RT: The Journal for Respiratory Care Practitioners, 2019, v. 32, n. 2, p. 26
Publication type:: Article

Preventing Cystic Fibrosis Infections Part II: Medications & Airway Clearance.

Published in:

RT: The Journal for Respiratory Care Practitioners, 2018, v. 31, n. 7, p. 7

By:

Hanlon, Phyllis

Publication type:

Article

Origins of Cystic Fibrosis Discovered in Bronze Age Europeans.

Published in:: RT: The Journal for Respiratory Care Practitioners, 2018, v. 31, n. 7, p. 5
Publication type:: Article

CYSTIC FIBROSIS AFFECTS GROWTH IN THE WOMB.

Published in:: RT: The Journal for Respiratory Care Practitioners, 2018, v. 31, n. 6, p. 20
Publication type:: Article

Preventing Cystic Fibrosis Infections with Airway Clearance, Part I: Medical Devices.

Published in:

RT: The Journal for Respiratory Care Practitioners, 2018, v. 31, n. 6, p. 18

By:

Hanlon, Phyllis

Publication type:

Article

The Latest Respiratory Care News.

Published in:: RT: The Journal for Respiratory Care Practitioners, 2018, v. 31, n. 6, p. 6
Publication type:: Article

For CF Patients, No One Right Device for Airway Clearance Therapy.

Published in:

RT: The Journal for Respiratory Care Practitioners, 2017, v. 30, n. 5, p. 16

By:

Rimler, Rose

Publication type:

Article

Pediatric Patient Monitoring.

Published in:

RT: The Journal for Respiratory Care Practitioners, 2016, v. 29, n. 11, p. 10

By:

Hanlon, Phyllis

Publication type:

Article

Spirometry and Plethysmography: Combining Diagnostic Power.

Published in:

RT: The Journal for Respiratory Care Practitioners, 2015, v. 28, n. 5, p. 11

By:

HANLON, PHYLLIS

Publication type:

Article

Cystic Fibrosis: Advances in Research and Treatment.

Published in:

RT: The Journal for Respiratory Care Practitioners, 2014, v. 27, n. 9, p. 6

By:

FRATANTORO, MIKE

Publication type:

Article

Lymphocytic Mastitis and Diabetic Mastopathy: A Molecular, Immunophenotypic, and Clinicopathologic Evaluation of 11 Cases.

Published in:

Modern Pathology, 2003, v. 16, n. 3, p. 223, doi. 10.1097/01.MP.0000056627.21128.74

By:

Valdez, Riccardo;
Thorson, John;
Finn, William G.;
Schnitzer, Bertram;
Kleer, Celina G.

Publication type:

Article

Histopathologic Features of Burkholderia Cepacia Pneumonia in Patients Without Cystic Fibrosis.

Published in:

Modern Pathology, 2000, v. 13, n. 4, p. 369, doi. 10.1038/modpathol.3880060

By:

Belchis, Deborah A.;
Simpson, Elizabeth;
Colby, Thomas

Publication type:

Article

Evolution and Medicine.

Published in:

2015

By:

Trevathan, Wenda

Publication type:

Book Review

Ribosomal Stalk Protein Silencing Partially Corrects the ΔF508-CFTR Functional Expression Defect.

Published in:

PLoS Biology, 2016, v. 14, n. 5, p. 1, doi. 10.1371/journal.pbio.1002462

By:

Veit, Guido;
Oliver, Kathryn;
Apaja, Pirjo M.;
Perdomo, Doranda;
Bidaud-Meynard, Aurélien;
Lin, Sheng-Ting;
Guo, Jingyu;
Icyuz, Mert;
Sorscher, Eric J.;
Hartman IV, John L.;
Lukacs, Gergely L.

Publication type:

Article

Living in Constant Crisis—When Stress Management Becomes the Problem.

Published in:

PLoS Biology, 2014, v. 12, n. 11, p. 1, doi. 10.1371/journal.pbio.1001999

By:

Roberts, Roland G.

Publication type:

Article

A Lack of Premature Termination Codon Read-Through Efficacy of PTC124 (Ataluren) in a Diverse Array of Reporter Assays.

Published in:

PLoS Biology, 2013, v. 11, n. 6, p. 1, doi. 10.1371/journal.pbio.1001593

By:

McElroy, Stuart P.;
Nomura, Toshifumi;
Torrie, Leah S.;
Warbrick, Emma;
Gartner, Ulrike;
Wood, Gavin;
McLean, W. H. Irwin

Publication type:

Article

Engineered Common Cold Virus Helps Cultured Cystic Fibrosis Tissues Clear Mucus.

Published in:

PLoS Biology, 2009, v. 7, n. 7, p. 1, doi. 10.1371/journal.pbio.1000160

By:

Meadows, Robin

Publication type:

Article

CFTR Delivery to 25% of Surface Epithelial Cells Restores Normal Rates of Mucus Transport to Human Cystic Fibrosis Airway Epithelium.

Published in:

PLoS Biology, 2009, v. 7, n. 7, p. 1, doi. 10.1371/journal.pbio.1000155

By:

Liqun Zhang;
Button, Brian;
Gabriel, Sherif E.;
Burkett, Susan;
Yu Yan;
Skiadopoulos, Mario H.;
Yan Li Dang;
Vogel, Leatrice N.;
McKay, Tristan;
Mengos, April;
Boucher, Richard C.;
Collins, Peter L.;
Pickles, Raymond J.

Publication type:

Article

Indexes reviewed.

Published in:

2008

By:

Shuttleworth, Christine

Publication type:

Excerpt