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Neuropeptide Y Enhances Progerin Clearance and Ameliorates the Senescent Phenotype of Human Hutchinson-Gilford Progeria Syndrome Cells.
- Published in:
- 2020
- By:
- Publication type:
- journal article
Re-establishing ataxin-2 downregulates translation of mutant ataxin-3 and alleviates Machado-Joseph disease.
- Published in:
- 2015
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- Publication type:
- journal article
Caffeine alleviates progressive motor deficits in a transgenic mouse model of spinocerebellar ataxia.
- Published in:
- 2017
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- Publication type:
- journal article
Cerebellar morphometric and spectroscopic biomarkers for Machado-Joseph Disease.
- Published in:
- Acta Neuropathologica Communications, 2022, v. 10, n. 1, p. 1, doi. 10.1186/s40478-022-01329-4
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- Publication type:
- Article
The blood-brain barrier is disrupted in Machado-Joseph disease/spinocerebellar ataxia type 3: evidence from transgenic mice and human post-mortem samples.
- Published in:
- Acta Neuropathologica Communications, 2020, v. 8, n. 1, p. N.PAG, doi. 10.1186/s40478-020-00955-0
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- Publication type:
- Article
Establishment and characterization of human pluripotent stem cells-derived brain organoids to model cerebellar diseases.
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- Scientific Reports, 2022, v. 12, n. 1, p. 1, doi. 10.1038/s41598-022-16369-y
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- Publication type:
- Article
Highly Specific Blood-Brain Barrier Transmigrating Single-Domain Antibodies Selected by an In Vivo Phage Display Screening.
- Published in:
- Pharmaceutics, 2021, v. 13, n. 10, p. 1598, doi. 10.3390/pharmaceutics13101598
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- Publication type:
- Article
Viral-based animal models in polyglutamine disorders.
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- Brain: A Journal of Neurology, 2024, v. 147, n. 4, p. 1166, doi. 10.1093/brain/awae012
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- Publication type:
- Article
stress granule protein G3BP1 alleviates spinocerebellar ataxia-associated deficits.
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- Brain: A Journal of Neurology, 2023, v. 146, n. 6, p. 2346, doi. 10.1093/brain/awac473
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- Publication type:
- Article
Transplantation of cerebellar neural stem cells improves motor coordination and neuropathology in Machado-Joseph disease mice.
- Published in:
- 2015
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- Publication type:
- Journal Article
Transplantation of cerebellar neural stem cells improves motor coordination and neuropathology in Machado-Joseph disease mice.
- Published in:
- Brain: A Journal of Neurology, 2015, v. 138, n. 2, p. 320
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- Publication type:
- Article
SIRT2 Deficiency Exacerbates Hepatic Steatosis via a Putative Role of the ER Stress Pathway.
- Published in:
- International Journal of Molecular Sciences, 2022, v. 23, n. 12, p. 6790, doi. 10.3390/ijms23126790
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- Publication type:
- Article
Extracellular Vesicles Physiological Role and the Particular Case of Disease-Spreading Mechanisms in Polyglutamine Diseases.
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- International Journal of Molecular Sciences, 2021, v. 22, n. 22, p. 12288, doi. 10.3390/ijms222212288
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- Publication type:
- Article
Living Proof of Activity of Extracellular Vesicles in the Central Nervous System.
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- International Journal of Molecular Sciences, 2021, v. 22, n. 14, p. 7294, doi. 10.3390/ijms22147294
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- Publication type:
- Article
Characterization of common and rare human papillomaviruses in Portuguese women by the polymerase chain reaction, restriction fragment length polymorphism and sequencing.
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- Journal of Medical Virology, 2010, v. 82, n. 6, p. 1024, doi. 10.1002/jmv.21756
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- Publication type:
- Article
RNA Interference Mitigates Motor and Neuropathological Deficits in a Cerebellar Mouse Model of Machado-Joseph Disease.
- Published in:
- PLoS ONE, 2014, v. 9, n. 8, p. 1, doi. 10.1371/journal.pone.0100086
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- Publication type:
- Article
Fluoxetine Induces Proliferation and Inhibits Differentiation of Hypothalamic Neuroprogenitor Cells <i>In Vitro</i>.
- Published in:
- PLoS ONE, 2014, v. 9, n. 3, p. 1, doi. 10.1371/journal.pone.0088917
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- Publication type:
- Article
Silencing Mutant Ataxin-3 Rescues Motor Deficits and Neuropathology in Machado-Joseph Disease Transgenic Mice.
- Published in:
- PLoS ONE, 2013, v. 8, n. 1, p. 1, doi. 10.1371/journal.pone.0052396
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- Publication type:
- Article
Moderate Long-Term Modulation of Neuropeptide Y in Hypothalamic Arcuate Nucleus Induces Energy Balance Alterations in Adult Rats.
- Published in:
- PLoS ONE, 2011, v. 6, n. 7, p. 1, doi. 10.1371/journal.pone.0022333
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- Publication type:
- Article
Proliferative Hypothalamic Neurospheres Express NPY, AGRP, POMC, CART and Orexin-A and Differentiate to Functional Neurons.
- Published in:
- PLoS ONE, 2011, v. 6, n. 5, p. 1, doi. 10.1371/journal.pone.0019745
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- Publication type:
- Article
Allele-Specific RNA Silencing of Mutant Ataxin-3 Mediates Neuroprotection in a Rat Model of Machado-Joseph Disease.
- Published in:
- PLoS ONE, 2008, v. 3, n. 10, p. 1, doi. 10.1371/journal.pone.0003341
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- Publication type:
- Article
Isolation of Extracellular Vesicles from Human Follicular Fluid: Size-Exclusion Chromatography versus Ultracentrifugation.
- Published in:
- Biomolecules (2218-273X), 2023, v. 13, n. 2, p. 278, doi. 10.3390/biom13020278
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- Publication type:
- Article
The autophagy‐enhancing drug carbamazepine improves neuropathology and motor impairment in mouse models of Machado–Joseph disease.
- Published in:
- Neuropathology & Applied Neurobiology, 2022, v. 48, n. 1, p. 1, doi. 10.1111/nan.12763
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- Publication type:
- Article
Identification of the calpain‐generated toxic fragment of ataxin‐3 protein provides new avenues for therapy of Machado–Joseph disease| Spinocerebellar ataxia type 3.
- Published in:
- Neuropathology & Applied Neurobiology, 2022, v. 48, n. 1, p. 1, doi. 10.1111/nan.12748
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- Publication type:
- Article
Motor Dysfunctions and Neuropathology in Mouse Models of Spinocerebellar Ataxia Type 2: A Comprehensive Review.
- Published in:
- Frontiers in Neuroscience, 2016, v. 10, p. 1, doi. 10.3389/fnins.2016.00572
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- Publication type:
- Article
Beclin 1 mitigates motor and neuropathological deficits in genetic mouse models of Machado-Joseph disease.
- Published in:
- 2013
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- Publication type:
- journal article
Beclin 1 mitigates motor and neuropathological deficits in genetic mouse models of Machado–Joseph disease.
- Published in:
- Brain: A Journal of Neurology, 2013, v. 136, n. 7, p. 2173, doi. 10.1093/brain/awt144
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- Publication type:
- Article
Calpastatin-mediated inhibition of calpains in the mouse brain prevents mutant ataxin 3 proteolysis, nuclear localization and aggregation, relieving Machado-Joseph disease.
- Published in:
- 2012
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- Publication type:
- journal article
Calpastatin-mediated inhibition of calpains in the mouse brain prevents mutant ataxin 3 proteolysis, nuclear localization and aggregation, relieving Machado–Joseph disease.
- Published in:
- Brain: A Journal of Neurology, 2012, v. 135, n. 8, p. 2428, doi. 10.1093/brain/aws177
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- Publication type:
- Article
Overexpression of the autophagic beclin-1 protein clears mutant ataxin-3 and alleviates Machado–Joseph disease.
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- Brain: A Journal of Neurology, 2011, v. 134, n. 5, p. 1400, doi. 10.1093/brain/awr047
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- Publication type:
- Article
Caloric restriction blocks neuropathology and motor deficits in Machado-Joseph disease mouse models through SIRT1 pathway.
- Published in:
- Nature Communications, 2016, v. 7, n. 5, p. 11445, doi. 10.1038/ncomms11445
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- Publication type:
- Article
Caffeine and adenosine A(2A) receptor inactivation decrease striatal neuropathology in a lentiviral-based model of Machado-Joseph disease.
- Published in:
- 2013
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- Publication type:
- journal article
Correction to: The frequency of non‑motor symptoms in SCA3 and their association with disease severity and lifestyle factors.
- Published in:
- 2024
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- Publication type:
- Correction Notice
The frequency of non-motor symptoms in SCA3 and their association with disease severity and lifestyle factors.
- Published in:
- Journal of Neurology, 2023, v. 270, n. 2, p. 944, doi. 10.1007/s00415-022-11441-z
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- Publication type:
- Article
Neuropeptide Y (NPY) intranasal delivery alleviates Machado–Joseph disease.
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- Scientific Reports, 2021, v. 11, n. 1, p. 1, doi. 10.1038/s41598-021-82339-5
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- Publication type:
- Article
Ibuprofen enhances synaptic function and neural progenitors proliferation markers and improves neuropathology and motor coordination in Machado–Joseph disease models.
- Published in:
- Human Molecular Genetics, 2019, v. 28, n. 22, p. 3691, doi. 10.1093/hmg/ddz097
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- Publication type:
- Article
Cordycepin activates autophagy through AMPK phosphorylation to reduce abnormalities in Machado–Joseph disease models.
- Published in:
- Human Molecular Genetics, 2019, v. 28, n. 1, p. 51, doi. 10.1093/hmg/ddy328
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- Publication type:
- Article
Loss of hierarchical imprinting regulation at the Prader–Willi/Angelman syndrome locus in human iPSCs.
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- Human Molecular Genetics, 2018, v. 27, n. 23, p. 3999, doi. 10.1093/hmg/ddy274
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- Publication type:
- Article
Neuropeptide Y mitigates neuropathology and motor deficits in mouse models of Machado-Joseph disease.
- Published in:
- Human Molecular Genetics, 2015, v. 24, n. 19, p. 5451, doi. 10.1093/hmg/ddv271
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- Publication type:
- Article
Calpain inhibition reduces ataxin-3 cleavage alleviating neuropathology and motor impairments in mouse models of Machado–Joseph disease.
- Published in:
- Human Molecular Genetics, 2014, v. 23, n. 18, p. 4932, doi. 10.1093/hmg/ddu209
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- Publication type:
- Article
MicroRNA-21 silencing enhances the cytotoxic effect of the antiangiogenic drug sunitinib in glioblastoma.
- Published in:
- Human Molecular Genetics, 2013, v. 22, n. 5, p. 904, doi. 10.1093/hmg/dds496
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- Publication type:
- Article
In Vitro Evaluation of Biphasic Calcium Phosphate Scaffolds Derived from Cuttlefish Bone Coated with Poly(ester urea) for Bone Tissue Regeneration.
- Published in:
- Polymers (20734360), 2023, v. 15, n. 10, p. 2256, doi. 10.3390/polym15102256
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- Publication type:
- Article
Mannose and Lactobionic Acid in Nasal Vaccination: Enhancing Antigen Delivery via C-Type Lectin Receptors.
- Published in:
- Pharmaceutics, 2024, v. 16, n. 10, p. 1308, doi. 10.3390/pharmaceutics16101308
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- Publication type:
- Article
Autophagy in Spinocerebellar ataxia type 2, a dysregulated pathway, and a target for therapy.
- Published in:
- Cell Death & Disease, 2021, v. 12, n. 12, p. 1, doi. 10.1038/s41419-021-04404-1
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- Publication type:
- Article
Stress granules, RNA-binding proteins and polyglutamine diseases: too much aggregation?
- Published in:
- Cell Death & Disease, 2021, v. 12, n. 6, p. 1, doi. 10.1038/s41419-021-03873-8
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- Publication type:
- Article
Stage‐Dependent Biomarker Changes in Spinocerebellar Ataxia Type 3.
- Published in:
- Annals of Neurology, 2024, v. 95, n. 2, p. 400, doi. 10.1002/ana.26824
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- Publication type:
- Article
Differential Temporal Dynamics of Axial and Appendicular Ataxia in SCA3.
- Published in:
- 2022
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- Publication type:
- journal article
Characterization of Lifestyle in Spinocerebellar Ataxia Type 3 and Association with Disease Severity.
- Published in:
- Movement Disorders, 2022, v. 37, n. 2, p. 405, doi. 10.1002/mds.28844
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- Publication type:
- Article
Successes and Hurdles in Stem Cells Application and Production for Brain Transplantation.
- Published in:
- Frontiers in Neuroscience, 2019, v. 13, p. 1, doi. 10.3389/fnins.2019.01194
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- Publication type:
- Article
miR-155 modulates microglia-mediated immune response by down-regulating SOCS-1 and promoting cytokine and nitric oxide production.
- Published in:
- Immunology, 2012, v. 135, n. 1, p. 73, doi. 10.1111/j.1365-2567.2011.03514.x
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- Publication type:
- Article