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The transformation of trust in China's alternative food networks: disruption, reconstruction, and development.
- Published in:
- Ecology & Society, 2015, v. 20, n. 2, p. 435, doi. 10.5751/ES-07536-200219
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- Publication type:
- Article
Occupation of Cultivated Land for Urban–Rural Expansion in China: Evidence from National Land Survey 1996–2006.
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- Land (2012), 2021, v. 10, n. 12, p. 1378, doi. 10.3390/land10121378
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- Publication type:
- Article
Patterns and Distributions of Urban Expansion in Global Watersheds.
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- Earth's Future, 2021, v. 9, n. 8, p. 1, doi. 10.1029/2021EF002062
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- Publication type:
- Article
Guidelines on the diagnosis, clinical assessments, treatment and management for CLN2 disease patients.
- Published in:
- 2021
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- Publication type:
- journal article
Abnormally increased carotid intima media-thickness and elasticity in patients with Morquio A disease.
- Published in:
- 2020
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- Publication type:
- journal article
Multiple bumps can enhance robustness to noise in continuous attractor networks.
- Published in:
- PLoS Computational Biology, 2022, v. 18, n. 10, p. 1, doi. 10.1371/journal.pcbi.1010547
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- Publication type:
- Article
Studies of the reactivity of morpholine, 2-mercaptobenzothiazole and 2 of their derivatives with selected amino acids.
- Published in:
- Contact Dermatitis (01051873), 1988, v. 19, n. 1, p. 16, doi. 10.1111/j.1600-0536.1988.tb02862.x
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- Publication type:
- Article
Cardiac responses in paediatric Pompe disease in the ADVANCE patient cohort.
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- Cardiology in the Young, 2022, v. 32, n. 3, p. 364, doi. 10.1017/S1047951121002079
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- Publication type:
- Article
Institutional Bricolage in Irrigation Governance in Rural Northwest China: Diversity, Legitimacy, and Persistence.
- Published in:
- Water Alternatives, 2021, v. 14, n. 2, p. 350
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- Publication type:
- Article
Irrigation Management in East Asia: Institutions, Socio-Economic Transformation and Adaptations.
- Published in:
- Water Alternatives, 2021, v. 14, n. 2, p. 319
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- Publication type:
- Article
Intra-Articular AAV9 α-l-Iduronidase Gene Replacement in the Canine Model of Mucopolysaccharidosis Type I.
- Published in:
- Advances in Cell & Gene Therapy, 2023, p. 1, doi. 10.1155/2023/7419017
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- Publication type:
- Article
Can we take the pulse of environmental governance the way we take the pulse of nature? Applying the Freshwater Health Index in Latin America.
- Published in:
- AMBIO - A Journal of the Human Environment, 2021, v. 50, n. 4, p. 870, doi. 10.1007/s13280-020-01407-8
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- Publication type:
- Article
Aligning the Freshwater Health Index Indicator System against the Transboundary Water Governance Framework of Southeast Asia's Sesan, Srepok, and Sekong River Basin.
- Published in:
- Water (20734441), 2019, v. 11, n. 11, p. 2307, doi. 10.3390/w11112307
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- Publication type:
- Article
On the Inapplicability of the Cobb-Douglas Production Function for Estimating the Benefit of Water Use and the Value of Water Resources.
- Published in:
- Water Resources Management, 2016, v. 30, n. 10, p. 3645, doi. 10.1007/s11269-016-1349-z
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- Publication type:
- Article
Expanded access with intravenous hydroxypropyl-β-cyclodextrin to treat children and young adults with Niemann-Pick disease type C1: a case report analysis.
- Published in:
- 2019
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- Publication type:
- journal article
Bridging critical institutionalism and fragmented authoritarianism in China: An analysis of centralized water policies and their local implementation in semi‐arid irrigation districts.
- Published in:
- Regulation & Governance, 2018, v. 12, n. 4, p. 451, doi. 10.1111/rego.12198
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- Publication type:
- Article
CRISPR-mediated generation and characterization of a Gaa homozygous c.1935C>A (p.D645E) Pompe disease knock-in mouse model recapitulating human infantile onset-Pompe disease.
- Published in:
- Scientific Reports, 2022, v. 12, n. 1, p. 1, doi. 10.1038/s41598-022-25914-8
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- Publication type:
- Article
Distinct pathways of homologous recombination controlled by the SWS1--SWSAP1--SPIDR complex.
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- Nature Communications, 2021, v. 8, p. 1, doi. 10.1038/s41467-021-24205-6
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- Publication type:
- Article
Interlocking Spiral Confinement for Rectangular Columns.
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- Concrete International, 2011, v. 33, n. 12, p. 38
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- Publication type:
- Article
Cross-Strait Relations: Diplomatic Entanglement or Rapprochement?
- Published in:
- 2015
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- Publication type:
- Essay
Can Centralized Sanctioning Promote Trust in Social Dilemmas? A Two-Level Trust Game with Incomplete Information.
- Published in:
- PLoS ONE, 2015, v. 10, n. 4, p. 1, doi. 10.1371/journal.pone.0124513
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- Publication type:
- Article
Joint Effects of Asymmetric Payoff and Reciprocity Mechanisms on Collective Cooperation in Water Sharing Interactions: A Game Theoretic Perspective.
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- PLoS ONE, 2013, v. 8, n. 8, p. 1, doi. 10.1371/journal.pone.0073793
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- Publication type:
- Article
Algorithm for the Early Diagnosis and Treatment of Patients with Cross Reactive Immunologic Material-Negative Classic Infantile Pompe Disease: A Step towards Improving the Efficacy of ERT.
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- PLoS ONE, 2013, v. 8, n. 6, p. 1, doi. 10.1371/journal.pone.0067052
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- Publication type:
- Article
Individual heat map assessments demonstrate vestronidase alfa treatment response in a highly heterogeneous mucopolysaccharidosis VII study population.
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- Journal of Inherited Metabolic Disease Reports, 2019, v. 49, n. 1, p. 53, doi. 10.1002/jmd2.12043
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- Publication type:
- Article
Improving localization accuracy for non-invasive automated early left ventricular origin localization approach.
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- Frontiers in Physiology, 2023, p. 1, doi. 10.3389/fphys.2023.1183280
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- Publication type:
- Article
Elevated oxysterol and N‐palmitoyl‐O‐phosphocholineserine levels in congenital disorders of glycosylation.
- Published in:
- Journal of Inherited Metabolic Disease, 2023, v. 46, n. 2, p. 326, doi. 10.1002/jimd.12595
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- Publication type:
- Article
Effects of hematopoietic stem cell transplantation on acyl-CoA oxidase deficiency: a sibling comparison study.
- Published in:
- Journal of Inherited Metabolic Disease, 2014, v. 37, n. 5, p. 791, doi. 10.1007/s10545-014-9698-3
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- Publication type:
- Article
Mitochondrial Complex III Deficiency Caused by a Homozygous UQCRC2 Mutation Presenting with Neonatal-Onset Recurrent Metabolic Decompensation.
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- Human Mutation, 2013, v. 34, n. 3, p. 446, doi. 10.1002/humu.22257
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- Publication type:
- Article
D-glyceric aciduria is caused by genetic deficiency of D-glycerate kinase ( GLYCTK).
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- Human Mutation, 2010, v. 31, n. 12, p. 1280, doi. 10.1002/humu.21375
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- Publication type:
- Article
Water woes: the institutional challenges in achieving SDG 6.
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- Sustainable Earth Reviews, 2023, v. 6, n. 1, p. 1, doi. 10.1186/s42055-023-00067-2
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- Publication type:
- Article
Characterization of disease-specific chondroitin sulfate nonreducing end accumulation in mucopolysaccharidosis IVA.
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- Glycobiology, 2020, v. 30, n. 7, p. 433, doi. 10.1093/glycob/cwz109
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- Publication type:
- Article
Immunomodulatory contribution of mast cells to the regenerative biomaterial microenvironment.
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- NPJ Regenerative Medicine, 2023, v. 8, n. 1, p. 1, doi. 10.1038/s41536-023-00324-0
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- Publication type:
- Article
An updated management approach of Pompe disease patients with high-sustained anti-rhGAA IgG antibody titers: experience with bortezomib-based immunomodulation.
- Published in:
- Frontiers in Immunology, 2024, p. 1, doi. 10.3389/fimmu.2024.1360369
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- Publication type:
- Article
Homeostatic control of recombination is implemented progressively in mouse meiosis.
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- Nature Cell Biology, 2012, v. 14, n. 4, p. 424, doi. 10.1038/ncb2451
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- Publication type:
- Article
Cerliponase Alfa for the Treatment of Atypical Phenotypes of CLN2 Disease: A Retrospective Case Series.
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- Journal of Child Neurology, 2021, v. 36, n. 6, p. 468, doi. 10.1177/0883073820977997
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- Publication type:
- Article
Development of an Arbitrary Waveform Membrane Stretcher for Dynamic Cell Culture.
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- Annals of Biomedical Engineering, 2014, v. 42, n. 5, p. 1062, doi. 10.1007/s10439-014-0976-x
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- Publication type:
- Article
CRISPR-Cas9 generated Pompe knock-in murine model exhibits early-onset hypertrophic cardiomyopathy and skeletal muscle weakness.
- Published in:
- Scientific Reports, 2020, v. 10, n. 1, p. 1, doi. 10.1038/s41598-020-65259-8
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- Publication type:
- Article
Integrating Institutions with Local Contexts in Community-Based Irrigation Governance: A Qualitative Systematic Review of Variables, Combinations, and Effects.
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- International Journal of the Commons, 2021, v. 15, n. 1, p. 320, doi. 10.5334/ijc.1108
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- Publication type:
- Article
Thinking outside "The Box": Case‐based didactics for medical education and the instructional legacy of Dr John M. Graham, Jr.
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- American Journal of Medical Genetics. Part A, 2021, v. 185, n. 9, p. 2636, doi. 10.1002/ajmg.a.62202
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- Publication type:
- Article
Ehlers-Danlos type VIII, periodontitis-type: Further delineation of the syndrome in a four-generation pedigree.
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- American Journal of Medical Genetics. Part A, 2011, v. 155A, n. 4, p. 742, doi. 10.1002/ajmg.a.33914
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- Publication type:
- Article
Climate Change Affects National Security.
- Published in:
- Asia-Pacific Social Science Review, 2014, v. 14, n. 2, p. 127, doi. 10.59588/2350-8329.1035
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- Publication type:
- Article
The Carotid Intima-Media Thickness and Arterial Stiffness of Pediatric Mucopolysaccharidosis Patients Are Increased Compared to Both Pediatric and Adult Controls.
- Published in:
- International Journal of Molecular Sciences, 2017, v. 18, n. 3, p. 637, doi. 10.3390/ijms18030637
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- Publication type:
- Article
Jun Dimerization Protein 2 Activates Mc2r Transcriptional Activity: Role of Phosphorylation and SUMOylation.
- Published in:
- International Journal of Molecular Sciences, 2017, v. 18, n. 2, p. 304, doi. 10.3390/ijms18020304
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- Publication type:
- Article
Aortic Root Dilatation in Mucopolysaccharidosis I-VII.
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- International Journal of Molecular Sciences, 2016, v. 17, n. 12, p. 2004, doi. 10.3390/ijms17122004
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- Publication type:
- Article
Prevention of metabolic decompensation in an infant with mutase deficient methylmalonic aciduria undergoing cardiopulmonary bypass.
- Published in:
- World Journal of Pediatrics, 2014, v. 10, n. 1, p. 83, doi. 10.1007/s12519-014-0458-0
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- Publication type:
- Article
Pentosan Polysulfate: Oral Versus Subcutaneous Injection in Mucopolysaccharidosis Type I Dogs.
- Published in:
- PLoS ONE, 2016, v. 11, n. 4, p. 1, doi. 10.1371/journal.pone.0153136
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- Publication type:
- Article
Immune-Mediated Inflammation May Contribute to the Pathogenesis of Cardiovascular Disease in Mucopolysaccharidosis Type I.
- Published in:
- PLoS ONE, 2016, v. 11, n. 3, p. 1, doi. 10.1371/journal.pone.0150850
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- Publication type:
- Article