Found: 37
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SARM1 deletion delays cerebellar but not spinal cord degeneration in an enhanced mouse model of SPG7 deficiency.
- Published in:
- Brain: A Journal of Neurology, 2023, v. 146, n. 10, p. 4117, doi. 10.1093/brain/awad136
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- Publication type:
- Article
Reprograming of proteasomal degradation by branched chain amino acid metabolism.
- Published in:
- Aging Cell, 2022, v. 21, n. 12, p. 1, doi. 10.1111/acel.13725
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- Publication type:
- Article
Mitochondrial matrix proteases: quality control and beyond.
- Published in:
- FEBS Journal, 2022, v. 289, n. 22, p. 7128, doi. 10.1111/febs.15964
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- Publication type:
- Article
CLUH controls astrin-1 expression to couple mitochondrial metabolism to cell cycle progression.
- Published in:
- eLife, 2022, p. 1, doi. 10.7554/eLife.74552
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- Publication type:
- Article
Spatial and temporal control of mitochondrial H<sub>2</sub>O<sub>2</sub> release in intact human cells.
- Published in:
- EMBO Journal, 2022, v. 41, n. 7, p. 1, doi. 10.15252/embj.2021109169
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- Publication type:
- Article
CLPP deficiency ameliorates neurodegeneration caused by impaired mitochondrial protein synthesis.
- Published in:
- 2022
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- Publication type:
- journal article
Correction to 'DNA polymerase gamma mutations that impair holoenzyme stability cause catalytic subunit depletion'.
- Published in:
- Nucleic Acids Research, 2021, v. 49, n. 18, p. 10803, doi. 10.1093/nar/gkab837
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- Publication type:
- Article
PERM1 interacts with the MICOS-MIB complex to connect the mitochondria and sarcolemma via ankyrin B.
- Published in:
- Nature Communications, 2021, v. 12, n. 1, p. 1, doi. 10.1038/s41467-021-25185-3
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- Publication type:
- Article
DNA polymerase gamma mutations that impair holoenzyme stability cause catalytic subunit depletion.
- Published in:
- Nucleic Acids Research, 2021, v. 49, n. 9, p. 5230, doi. 10.1093/nar/gkab282
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- Publication type:
- Article
A C. elegans model for neurodegeneration in Cockayne syndrome.
- Published in:
- Nucleic Acids Research, 2020, v. 48, n. 19, p. 10973, doi. 10.1093/nar/gkaa795
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- Publication type:
- Article
DARS2 is indispensable for Purkinje cell survival and protects against cerebellar ataxia.
- Published in:
- Human Molecular Genetics, 2020, v. 29, n. 17, p. 2845, doi. 10.1093/hmg/ddaa176
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- Publication type:
- Article
Alterations of redox and iron metabolism accompany the development of HIV latency.
- Published in:
- EMBO Journal, 2020, v. 39, n. 9, p. 1, doi. 10.15252/embj.2019102209
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- Publication type:
- Article
Mitochondrial Dysfunction Combined with High Calcium Load Leads to Impaired Antioxidant Defense Underlying the Selective Loss of Nigral Dopaminergic Neurons.
- Published in:
- Journal of Neuroscience, 2020, v. 40, n. 9, p. 1975, doi. 10.1523/jneurosci.1345-19.2019
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- Publication type:
- Article
KLF-1 orchestrates a xenobiotic detoxification program essential for longevity of mitochondrial mutants.
- Published in:
- Nature Communications, 2019, v. 10, n. 1, p. N.PAG, doi. 10.1038/s41467-019-11275-w
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- Publication type:
- Article
Loss of genomic integrity induced by lysosphingolipid imbalance drives ageing in the heart.
- Published in:
- EMBO Reports, 2019, v. 20, n. 4, p. N.PAG, doi. 10.15252/embr.201847407
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- Publication type:
- Article
CLPP deficiency protects against metabolic syndrome but hinders adaptive thermogenesis.
- Published in:
- EMBO Reports, 2018, v. 19, n. 5, p. 1, doi. 10.15252/embr.201745126
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- Publication type:
- Article
DARS2 protects against neuroinflammation and apoptotic neuronal loss, but is dispensable for myelin producing cells.
- Published in:
- Human Molecular Genetics, 2017, v. 26, n. 21, p. 4181, doi. 10.1093/hmg/ddx307
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- Publication type:
- Article
Deficiency of WARS2, encoding mitochondrial tryptophanyl tRNA synthetase, causes severe infantile onset leukoencephalopathy.
- Published in:
- American Journal of Medical Genetics. Part A, 2017, v. 173, n. 9, p. 2505, doi. 10.1002/ajmg.a.38339
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- Publication type:
- Article
Origins of mtDNA mutations in ageing.
- Published in:
- Essays in Biochemistry, 2017, v. 61, n. 3, p. 325, doi. 10.1042/EBC20160090
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- Publication type:
- Article
Human R1441C LRRK2 regulates the synaptic vesicle proteome and phosphoproteome in a Drosophila model of Parkinson's disease.
- Published in:
- Human Molecular Genetics, 2016, v. 25, n. 24, p. 5365, doi. 10.1093/hmg/ddw352
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- Publication type:
- Article
CLPP coordinates mitoribosomal assembly through the regulation of ERAL1 levels.
- Published in:
- EMBO Journal, 2016, v. 35, n. 23, p. 2566, doi. 10.15252/embj.201694253
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- Publication type:
- Article
Loss of CLPP alleviates mitochondrial cardiomyopathy without affecting the mammalian UPR<sup>mt</sup>.
- Published in:
- EMBO Reports, 2016, v. 17, n. 7, p. 953, doi. 10.15252/embr.201642077
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- Publication type:
- Article
Oxygen reactivity of mammalian sulfite oxidase provides a concept for the treatment of sulfite oxidase deficiency.
- Published in:
- Biochemical Journal, 2015, v. 469, n. 2, p. 211, doi. 10.1042/BJ20140768
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- Publication type:
- Article
Spastin Binds to Lipid Droplets and Affects Lipid Metabolism.
- Published in:
- PLoS Genetics, 2015, v. 11, n. 4, p. 1, doi. 10.1371/journal.pgen.1005149
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- Publication type:
- Article
Defects in [beta]-Cell Ca2+ Dynamics in Age-Induced Diabetes.
- Published in:
- 2014
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- Publication type:
- Journal Article
Defects in β-Cell Ca<sup>2+</sup> Dynamics in Age-Induced Diabetes.
- Published in:
- Diabetes, 2014, v. 63, n. 12, p. 4100, doi. 10.2337/db13-1855
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- Publication type:
- Article
Loss of UCP2 Attenuates Mitochondrial Dysfunction without Altering ROS Production and Uncoupling Activity.
- Published in:
- PLoS Genetics, 2014, v. 10, n. 6, p. 1, doi. 10.1371/journal.pgen.1004385
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- Publication type:
- Article
Embelin inhibits endothelial mitochondrial respiration and impairs neoangiogenesis during tumor growth and wound healing.
- Published in:
- EMBO Molecular Medicine, 2014, v. 6, n. 5, p. 624, doi. 10.1002/emmm.201303016
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- Publication type:
- Article
Succinate Dehydrogenase Upregulation Destabilize Complex I and Limits the Lifespan of <i>gas-1</i> Mutant.
- Published in:
- PLoS ONE, 2013, v. 8, n. 3, p. 1, doi. 10.1371/journal.pone.0059493
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- Publication type:
- Article
A Tissue-Specific Approach to the Analysis of Metabolic Changes in Caenorhabditis elegans.
- Published in:
- PLoS ONE, 2011, v. 6, n. 12, p. 1, doi. 10.1371/journal.pone.0028417
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- Publication type:
- Article
Highlight: The Biology of Aging: Mechanisms and Intervention.
- Published in:
- Biological Chemistry, 2010, v. 391, n. 10, p. 1113, doi. 10.1515/BC.2010.127
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- Publication type:
- Article
Mitochondrial DNA level, but not active replicase, is essential for Caenorhabditis elegans development.
- Published in:
- Nucleic Acids Research, 2009, v. 37, n. 6, p. 1817, doi. 10.1093/nar/gkp018
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- Publication type:
- Article
Strong Purifying Selection in Transmission of Mammalian Mitochondrial DNA.
- Published in:
- PLoS Biology, 2008, v. 6, n. 1, p. e10, doi. 10.1371/journal.pbio.0060010
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- Publication type:
- Article
Mitochondrial DNA polymerase gamma is essential for mammalian embryogenesis.
- Published in:
- Human Molecular Genetics, 2005, v. 14, n. 13, p. 1775, doi. 10.1093/hmg/ddi184
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- Publication type:
- Article
Premature ageing in mice expressing defective mitochondrial DNA polymerase.
- Published in:
- Nature, 2004, v. 429, n. 6990, p. 417, doi. 10.1038/nature02517
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- Publication type:
- Article
Mitochondrial transcription factors B1 and B2 activate transcription of human mtDNA.
- Published in:
- Nature Genetics, 2002, v. 31, n. 3, p. 289, doi. 10.1038/ng909
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- Publication type:
- Article
Induced synthesis of albumin-like protein in damaged rat reticulocytes.
- Published in:
- British Journal of Haematology, 2001, v. 115, n. 1, p. 205, doi. 10.1046/j.1365-2141.2001.03062.x
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- Publication type:
- Article