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Effects of triparanol and 20,25-diazacholesterol in CNS of rat: Morphological and biochemical studies.
- Published in:
- Acta Neuropathologica, 1974, v. 29, n. 2, p. 141, doi. 10.1007/BF00684773
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- Publication type:
- Article
Ultrastructural study of neuronal cytoplasmic inclusions produced by hypocholesterolemic Drug, AY 9944.
- Published in:
- Acta Neuropathologica, 1973, v. 26, n. 3, p. 185, doi. 10.1007/BF00684428
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- Publication type:
- Article
Accumulation of smooth cisterns, multivesicular bodies and 'zebra' bodies in neurons.
- Published in:
- Acta Neuropathologica, 1971, v. 18, n. 2, p. 132, doi. 10.1007/BF00687601
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- Publication type:
- Article
Sandhoff disease in Cyprus: population screening by biochemical and DNA analysis indicates a high frequency of carriers in the Maronite community.
- Published in:
- Human Genetics, 2000, v. 107, n. 1, p. 12, doi. 10.1007/s004390050003
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- Publication type:
- Article
Effects of Ozone on the thermal decomposition behavior of Guanidine Nitrate.
- Published in:
- Science & Technology of Energetic Materials, 2022, v. 83, n. 5, p. 117
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- Publication type:
- Article
Expression of Sphingolipid Activator Protein Gene in Brain and Systemic Organs of Developing Mice.
- Published in:
- Developmental Neuroscience, 1994, v. 16, n. 1/2, p. 90, doi. 10.1159/000112093
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- Publication type:
- Article
Biochemical and Molecular Aspects of Late-Onset GM2-Gangliosidosis: B1 Variant as a Prototype.
- Published in:
- Developmental Neuroscience, 1991, v. 13, n. 4/5, p. 288, doi. 10.1159/000112175
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- Publication type:
- Article
Renal cerebroside in globoid cell leukodystrophy (Krabbées disease).
- Published in:
- Lipids, 1971, v. 6, n. 6, p. 433, doi. 10.1007/BF02531383
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- Publication type:
- Article
Transfer technology using inorganic separation layer and apparatus for fabricating flexible OLED displays.
- Published in:
- Journal of the Society for Information Display, 2015, v. 23, n. 11, p. 543, doi. 10.1002/jsid.398
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- Publication type:
- Article
The function of sphingolipids in the nervous system: lessons learnt from mouse models of specific sphingolipid activator protein deficiencies.
- Published in:
- Journal of Neurochemistry, 2007, v. 103, p. 32, doi. 10.1111/j.1471-4159.2007.04709.x
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- Publication type:
- Article
Natural Selection Signatures in the Hondo and Ryukyu Japanese Subpopulations.
- Published in:
- Molecular Biology & Evolution, 2023, v. 40, n. 10, p. 1, doi. 10.1093/molbev/msad231
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- Publication type:
- Article
Mutation in saposin D domain of sphingolipid activator protein gene causes urinary system defects and cerebellar Purkinje cell degeneration with accumulation of hydroxy fatty acid-containing ceramide in mouse.
- Published in:
- Human Molecular Genetics, 2004, v. 13, n. 21, p. 2709, doi. 10.1093/hmg/ddh281
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- Publication type:
- Article
My encounters with Krabbe disease: A personal recollection of a 40-Year journey with young colleagues.
- Published in:
- Journal of Neuroscience Research, 2016, v. 94, n. 11, p. 965, doi. 10.1002/jnr.23735
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- Publication type:
- Article
Genetic background markedly influences vulnerability of the hippocampal neuronal organization in the “twitcher” mouse model of globoid cell leukodystrophy.
- Published in:
- Journal of Neuroscience Research, 2004, v. 77, n. 4, p. 507, doi. 10.1002/jnr.20190
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- Publication type:
- Article
Oligodendrocyte-specific gene expression in mouse brain: Use of a myelin-forming cell type-specific promoter in an adeno-associated virus.
- Published in:
- Journal of Neuroscience Research, 1999, v. 55, n. 4, p. 504, doi. 10.1002/(SICI)1097-4547(19990215)55:4<504::AID-JNR10>3.0.CO;2-0
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- Publication type:
- Article
Suppressed UDP-galactose: Ceramide galactosyltransferase and myelin protein mRNA in twitcher mouse brain.
- Published in:
- Journal of Neuroscience Research, 1998, v. 51, n. 4, p. 536, doi. 10.1002/(SICI)1097-4547(19980215)51:4<536::AID-JNR13>3.0.CO;2-1
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- Publication type:
- Article
Familial Primary Biliary Cirrhosis.
- Published in:
- American Journal of Gastroenterology (Springer Nature), 1981, v. 75, n. 3, p. 188
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- Publication type:
- Article
Infantile and fetal globoid cell leukodystrophy: Analysis of galactosylceramide and galactosylsphingosine.
- Published in:
- Annals of Neurology, 1988, v. 24, n. 4, p. 517, doi. 10.1002/ana.410240407
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- Publication type:
- Article
Chronic GM1 gangliosidosis presenting as dystonia: II. Biochemical studies.
- Published in:
- 1981
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- Publication type:
- journal article
Adrenoleukodystrophy: Elevated C26 fatty acid in cultured skin fibroblasts.
- Published in:
- Annals of Neurology, 1980, v. 7, n. 6, p. 542, doi. 10.1002/ana.410070607
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- Publication type:
- Article
The morquio syndrome: Neuropathologyxs and biochemistry.
- Published in:
- Annals of Neurology, 1978, v. 4, n. 1, p. 26, doi. 10.1002/ana.410040106
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- Publication type:
- Article
Chronic hexosaminidase A and B deficiency.
- Published in:
- Annals of Neurology, 1977, v. 2, n. 2, p. 156, doi. 10.1002/ana.410020212
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- Publication type:
- Article
A Point Mutation in the Coding Sequence of the β-Hexosaminidase α Gene Results in Defective Processing of the Enzyme Protein in an Unusual GM2-Gangliosidosis Variant.
- Published in:
- Journal of Neurochemistry, 1988, v. 51, n. 3, p. 984, doi. 10.1111/j.1471-4159.1988.tb01836.x
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- Publication type:
- Article
Mutation in GM2-Gangliosidosis B1 Variant.
- Published in:
- Journal of Neurochemistry, 1988, v. 50, n. 1, p. 316, doi. 10.1111/j.1471-4159.1988.tb13266.x
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- Publication type:
- Article
New books.
- Published in:
- 1976
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- Publication type:
- Book Review
Effects of Bifidobacterium longum BB536 Administration on Influenza Infection, Influenza Vaccine Antibody Titer, and Cell-Mediated Immunity in the Elderly.
- Published in:
- Bioscience, Biotechnology & Biochemistry, 2010, v. 74, n. 5, p. 939, doi. 10.1271/bbb.90749
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- Publication type:
- Article
Enzyme replacement in grafted nerve of twitcher mouse.
- Published in:
- Nature, 1983, v. 305, n. 5936, p. 713, doi. 10.1038/305713a0
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- Publication type:
- Article
Glycosylceramide Synthesis in the Developing Spinal Cord and Kidney of the Twitcher Mouse, an Enzymatically Authentic Model of Human Krabbe Disease.
- Published in:
- Journal of Neurochemistry, 1982, v. 39, n. 5, p. 1314, doi. 10.1111/j.1471-4159.1982.tb12572.x
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- Publication type:
- Article
Acid Sphingomyelinase of Human Brain: Purification to Homogeneity.
- Published in:
- Journal of Neurochemistry, 1982, v. 38, n. 6, p. 1753, doi. 10.1111/j.1471-4159.1982.tb06659.x
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- Publication type:
- Article
Specificities of Human and Rat Brain Enzymes of Cholesterol Ester Metabolism Toward Very Long Chain Fatty Acids: Implication for Biochemical Pathogenesis of Adrenoleukodystrophy.
- Published in:
- Journal of Neurochemistry, 1981, v. 36, n. 2, p. 776, doi. 10.1111/j.1471-4159.1981.tb01657.x
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- Publication type:
- Article
A CHOLESTEROL-ESTERIFYING ENZYME IN RAT CENTRAL NERVOUS SYSTEM MYELIN.
- Published in:
- Journal of Neurochemistry, 1978, v. 31, n. 4, p. 879, doi. 10.1111/j.1471-4159.1978.tb00123.x
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- Publication type:
- Article
FORMATION AND TURNOVER OF MYELIN GANGLIOSIDE.
- Published in:
- Journal of Neurochemistry, 1970, v. 17, n. 2, p. 209, doi. 10.1111/j.1471-4159.1970.tb02202.x
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- Publication type:
- Article
THE PATTERN OF MAMMALIAN BRAIN GANGLIOSIDES-III.
- Published in:
- Journal of Neurochemistry, 1965, v. 12, n. 12, p. 969, doi. 10.1111/j.1471-4159.1965.tb10256.x
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- Publication type:
- Article
THE PATTERN OF MAMMALIAN BRAIN GANGLIOSIDES-II EVALUATION OF THE EXTRACTION PROCEDURES, POSTMORTEM CHANGES AND THE EFFECT OF FORMALIN PRESERVATION.
- Published in:
- Journal of Neurochemistry, 1965, v. 12, n. 7, p. 629, doi. 10.1111/j.1471-4159.1965.tb04256.x
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- Publication type:
- Article
STUDY ON GANGLIOSIDE METABOLISM-I INCORPORATION OF d-[U-<sup>14</sup>C]GLUCOSE INTO INDIVIDUAL GANGLIOSIDES.
- Published in:
- Journal of Neurochemistry, 1964, v. 11, n. 9, p. 647, doi. 10.1111/j.1471-4159.1964.tb06147.x
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- Publication type:
- Article
STUDIES ON PROTEIN SYNTHESIS IN BRAIN MICROSOMAL SYSTEM.
- Published in:
- Journal of Neurochemistry, 1964, v. 11, n. 6, p. 403, doi. 10.1111/j.1471-4159.1964.tb11599.x
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- Publication type:
- Article
Enhancement of emission efficiency in white OLED device by highly efficient narrow spectrum red-emission material.
- Published in:
- Journal of the Society for Information Display, 2015, v. 23, n. 1, p. 7, doi. 10.1002/jsid.301
- By:
- Publication type:
- Article
Flexible high-resolution full-color top-emitting active-matrix organic light-emitting diode display.
- Published in:
- 2013
- By:
- Publication type:
- Other
Induced Mouse Models of Abnormal Sphingolipid Metabolism1.
- Published in:
- Journal of Biochemistry, 1998, v. 124, n. 1, p. 8, doi. 10.1093/oxfordjournals.jbchem.a022101
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- Publication type:
- Article
Mouse Models of Human Lysosomal Diseases.
- Published in:
- Brain Pathology, 1998, v. 8, n. 1, p. 195, doi. 10.1111/j.1750-3639.1998.tb00145.x
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- Publication type:
- Article
The Twitcher Mouse: A Model for Krabbe Disease and for Experimental Therapies.
- Published in:
- Brain Pathology, 1995, v. 5, n. 3, p. 249, doi. 10.1111/j.1750-3639.1995.tb00601.x
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- Publication type:
- Article
A Learned Society's Perspective on Publishing.
- Published in:
- Journal of Neurochemistry, 2016, v. 139, p. 17, doi. 10.1111/jnc.13674
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- Publication type:
- Article
Two novel (1334delC and 1363G to A, G455R) mutations in exon 12 of the β-hexosaminidase α-chain gene in two Portuguese patients.
- Published in:
- Human Mutation, 1997, v. 10, n. 5, p. 359, doi. 10.1002/(SICI)1098-1004(1997)10:5<359::AID-HUMU4>3.0.CO;2-A
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- Publication type:
- Article
Immunization against Intracerebral Transplantation of a Glioma in Mice.
- Published in:
- Nature, 1962, v. 193, n. 4821, p. 1194, doi. 10.1038/1931194a0
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- Publication type:
- Article
On the occasion of the 100th volume of the Proceedings of the Japan Academy, Series B (PJA-B).
- Published in:
- Proceedings of the Japan Academy, Series B Physical & biological sciences, 2023, v. 99, n. 8, p. 227, doi. 10.2183/pjab.99.016
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- Publication type:
- Article
Dr. Tamio Yamakawa (1921-2018).
- Published in:
- Proceedings of the Japan Academy, Series B Physical & biological sciences, 2019, v. 95, n. 2, p. 86, doi. 10.2183/pjab.95.008
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- Publication type:
- Article
Metabolism of amyloid β peptide and pathogenesis of Alzheimer's disease.
- Published in:
- Proceedings of the Japan Academy, Series B Physical & biological sciences, 2013, v. 89, n. 7, p. 321, doi. 10.2183/pjab.89.321
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- Publication type:
- Article
Bio-recognition and functional lipidomics by glycosphingolipid transfer technology.
- Published in:
- Proceedings of the Japan Academy, Series B Physical & biological sciences, 2013, v. 89, n. 7, p. 302, doi. 10.2183/pjab.89.302
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- Publication type:
- Article
A group of glycosphingolipids found in an invertebrate: Their structures and biological significance.
- Published in:
- Proceedings of the Japan Academy, Series B Physical & biological sciences, 2012, v. 88, n. 9, p. 509, doi. 10.2183/pjab.88.509
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- Publication type:
- Article
Myelin Pathology in the Twitcher Mouse<sup>a</sup>.
- Published in:
- Annals of the New York Academy of Sciences, 1990, v. 605, n. 1, p. 313, doi. 10.1111/j.1749-6632.1990.tb42405.x
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- Publication type:
- Article