Found: 21
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Actin Polymerization Defects Induce Mitochondrial Dysfunction in Cellular Models of Nemaline Myopathies.
- Published in:
- Antioxidants, 2023, v. 12, n. 12, p. 2023, doi. 10.3390/antiox12122023
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- Article
Mitochondrial Quality Control via Mitochondrial Unfolded Protein Response (mtUPR) in Ageing and Neurodegenerative Diseases.
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- Biomolecules (2218-273X), 2023, v. 13, n. 12, p. 1789, doi. 10.3390/biom13121789
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- Article
Antioxidants Prevent Iron Accumulation and Lipid Peroxidation, but Do Not Correct Autophagy Dysfunction or Mitochondrial Bioenergetics in Cellular Models of BPAN.
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- International Journal of Molecular Sciences, 2023, v. 24, n. 19, p. 14576, doi. 10.3390/ijms241914576
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- Article
Patient-Derived Cellular Models for Polytarget Precision Medicine in Pantothenate Kinase-Associated Neurodegeneration.
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- Pharmaceuticals (14248247), 2023, v. 16, n. 10, p. 1359, doi. 10.3390/ph16101359
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- Article
Vicious cycle of lipid peroxidation and iron accumulation in neurodegeneration.
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- Neural Regeneration Research, 2023, v. 18, n. 6, p. 1196, doi. 10.4103/1673-5374.358614
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- Article
Alpha-lipoic acid supplementation corrects pathological alterations in cellular models of pantothenate kinase-associated neurodegeneration with residual PANK2 expression levels.
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- Orphanet Journal of Rare Diseases, 2023, v. 18, n. 1, p. 1, doi. 10.1186/s13023-023-02687-5
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- Article
Neurodegeneration, Mitochondria, and Antibiotics.
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- Metabolites (2218-1989), 2023, v. 13, n. 3, p. 416, doi. 10.3390/metabo13030416
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- Article
mtUPR Modulation as a Therapeutic Target for Primary and Secondary Mitochondrial Diseases.
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- International Journal of Molecular Sciences, 2023, v. 24, n. 2, p. 1482, doi. 10.3390/ijms24021482
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- Article
Pantothenate and L-Carnitine Supplementation Improves Pathological Alterations in Cellular Models of KAT6A Syndrome.
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- Genes, 2022, v. 13, n. 12, p. 2300, doi. 10.3390/genes13122300
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- Article
Therapeutic approach with commercial supplements for pantothenate kinase-associated neurodegeneration with residual PANK2 expression levels.
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- 2022
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- Publication type:
- journal article
Activation of the Mitochondrial Unfolded Protein Response: A New Therapeutic Target?
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- Biomedicines, 2022, v. 10, n. 7, p. N.PAG, doi. 10.3390/biomedicines10071611
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- Article
UPR<sup>mt</sup> activation improves pathological alterations in cellular models of mitochondrial diseases.
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- 2022
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- Publication type:
- journal article
Pterostilbene in Combination With Mitochondrial Cofactors Improve Mitochondrial Function in Cellular Models of Mitochondrial Diseases.
- Published in:
- Frontiers in Pharmacology, 2022, v. 13, p. 1, doi. 10.3389/fphar.2022.862085
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- Article
Mitochondria and Antibiotics: For Good or for Evil?
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- Biomolecules (2218-273X), 2021, v. 11, n. 7, p. 1050, doi. 10.3390/biom11071050
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- Article
Down regulation of the expression of mitochondrial phosphopantetheinyl-proteins in pantothenate kinase-associated neurodegeneration: pathophysiological consequences and therapeutic perspectives.
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- 2021
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- Publication type:
- journal article
From Mitochondria to Atherosclerosis: The Inflammation Path.
- Published in:
- Biomedicines, 2021, v. 9, n. 3, p. 258, doi. 10.3390/biomedicines9030258
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- Publication type:
- Article
Coenzyme Q 10 Analogues: Benefits and Challenges for Therapeutics.
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- Antioxidants, 2021, v. 10, n. 2, p. 236, doi. 10.3390/antiox10020236
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- Publication type:
- Article
Advances in mt-tRNA Mutation-Caused Mitochondrial Disease Modeling: Patients' Brain in a Dish.
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- Frontiers in Genetics, 2021, v. 11, p. N.PAG, doi. 10.3389/fgene.2020.610764
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- Article
Precision Medicine in Rare Diseases.
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- Diseases, 2020, v. 8, n. 4, p. 42, doi. 10.3390/diseases8040042
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- Article
Coenzyme Q 10 : Novel Formulations and Medical Trends.
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- International Journal of Molecular Sciences, 2020, v. 21, n. 22, p. 8432, doi. 10.3390/ijms21228432
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- Article
Atherosclerosis and Coenzyme Q10.
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- International Journal of Molecular Sciences, 2019, v. 20, n. 20, p. 5195, doi. 10.3390/ijms20205195
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- Article