Found: 33
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Satellite cell senescence underlies myopathy in a mouse model of limb-girdle muscular dystrophy 2H.
- Published in:
- Journal of Clinical Investigation, 2012, v. 122, n. 5, p. 1764, doi. 10.1172/JCI59581
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- Publication type:
- Article
Osteopontin promotes fibrosis in dystrophic mouse muscle by modulating immune cell subsets and intramuscular TGF-beta.
- Published in:
- 2009
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- Publication type:
- journal article
Calpain activation impairs neuromuscular transmission in a mouse model of the slow-channel myasthenic syndrome.
- Published in:
- 2007
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- Publication type:
- journal article
Expression of a calpastatin transgene slows muscle wasting and obviates changes in myosin isoform expression during murine muscle disuse.
- Published in:
- Journal of Physiology, 2002, v. 545, n. 3, p. 819, doi. 10.1113/jphysiol.2002.024935
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- Publication type:
- Article
Skipping to new gene therapies for muscular dystrophy.
- Published in:
- Nature Medicine, 2003, v. 9, n. 8, p. 997, doi. 10.1038/nm0803-997
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- Publication type:
- Article
Genetic modifiers of muscular dystrophy act on sarcolemmal resealing and recovery from injury.
- Published in:
- PLoS Genetics, 2017, v. 13, n. 10, p. 1, doi. 10.1371/journal.pgen.1007070
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- Publication type:
- Article
A nitric oxide synthase transgene ameliorates muscular dystrophy in mdx mice.
- Published in:
- Journal of Cell Biology, 2001, v. 155, n. 1, p. 123, doi. 10.1083/jcb.200105110
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- Publication type:
- Article
A reporter mouse for optical imaging of inflammation in mdx muscles.
- Published in:
- Skeletal Muscle, 2015, v. 5, n. 1, p. 1, doi. 10.1186/s13395-015-0042-x
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- Publication type:
- Article
Calpain 3 cleaves filamin C and regulates its ability to interact with gamma- and delta-sarcoglycans.
- Published in:
- 2003
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- Publication type:
- journal article
Calpain 3 cleaves filamin C and regulates its ability to interact with γ- and δ-sarcoglycans.
- Published in:
- Muscle & Nerve, 2003, v. 28, n. 4, p. 472, doi. 10.1002/mus.10465
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- Publication type:
- Article
Ventilatory dysfunction in mdx mice: Impact of tumor necrosis factoralpha deletion.
- Published in:
- Muscle & Nerve, 2003, v. 28, n. 3, p. 336, doi. 10.1002/mus.10431
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- Publication type:
- Article
Calpain II expression is increased by changes in mechanical loading of muscle in vivo.
- Published in:
- Journal of Cellular Biochemistry, 1997, v. 64, n. 1, p. 55, doi. 10.1002/(SICI)1097-4644(199701)64:1<55::AID-JCB9>3.0.CO;2-Z
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- Publication type:
- Article
Polyrotaxane Nanocarriers Can Deliver CRISPR/Cas9 Plasmid to Dystrophic Muscle Cells to Successfully Edit the DMD Gene.
- Published in:
- Advanced Therapeutics, 2019, v. 2, n. 7, p. N.PAG, doi. 10.1002/adtp.201900061
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- Publication type:
- Article
Regulatory T cells suppress muscle inflammation and injury in muscular dystrophy.
- Published in:
- Science Translational Medicine, 2014, v. 6, n. 258, p. 1, doi. 10.1126/scitranslmed.3009925
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- Publication type:
- Article
Calpain 3 and CaMKIIb signaling are required to induce HSP70 necessary for adaptive muscle growth after atrophy.
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- Human Molecular Genetics, 2018, v. 27, n. 9, p. 1642, doi. 10.1093/hmg/ddy071
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- Publication type:
- Article
High levels of sarcospan are well tolerated and act as a sarcolemmal stabilizer to address skeletal muscle and pulmonary dysfunction in DMD.
- Published in:
- Human Molecular Genetics, 2016, v. 25, n. 24, p. 5395, doi. 10.1093/hmg/ddw356
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- Publication type:
- Article
Failure to up-regulate transcription of genes necessary for muscle adaptation underlies limb girdle muscular dystrophy 2A (calpainopathy).
- Published in:
- Human Molecular Genetics, 2016, v. 25, n. 11, p. 2194, doi. 10.1093/hmg/ddw086
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- Publication type:
- Article
The E3 ubiquitin ligase TRIM32 regulates myoblast proliferation by controlling turnover of NDRG2.
- Published in:
- Human Molecular Genetics, 2015, v. 24, n. 10, p. 2873, doi. 10.1093/hmg/ddv049
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- Publication type:
- Article
The common missense mutation D489N in TRIM32 causing limb girdle muscular dystrophy 2H leads to loss of the mutated protein in knock-in mice resulting in a Trim32-null phenotype.
- Published in:
- Human Molecular Genetics, 2011, v. 20, n. 20, p. 3925, doi. 10.1093/hmg/ddr311
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- Publication type:
- Article
Pathogenity of some limb girdle muscular dystrophy mutations can result from reduced anchorage to myofibrils and altered stability of calpain 3.
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- Human Molecular Genetics, 2011, v. 20, n. 17, p. 3331, doi. 10.1093/hmg/ddr239
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- Publication type:
- Article
Dantrolene Enhances Antisense-Mediated Exon Skipping in Human and Mouse Models of Duchenne Muscular Dystrophy.
- Published in:
- Science Translational Medicine, 2012, v. 4, n. 164, p. 1, doi. 10.1126/scitranslmed.3005054
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- Publication type:
- Article
Myostatin inhibition promotes fast fibre hypertrophy but causes loss of AMP‐activated protein kinase signalling and poor exercise tolerance in a model of limb‐girdle muscular dystrophy R1/2A.
- Published in:
- Journal of Physiology, 2020, v. 598, n. 18, p. 3927, doi. 10.1113/JP279943
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- Publication type:
- Article
Enhancement of Neurite Outgrowth Following Calpain Inhibition Is Mediated by Protein Kinase C.
- Published in:
- Journal of Neurochemistry, 1995, v. 65, n. 2, p. 517, doi. 10.1046/j.1471-4159.1995.65020517.x
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- Publication type:
- Article
Nanoparticles systemically biodistribute to regenerating skeletal muscle in DMD.
- Published in:
- Journal of Nanobiotechnology, 2023, v. 21, n. 1, p. 1, doi. 10.1186/s12951-023-01994-0
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- Publication type:
- Article
Myogenic Akt signaling attenuates muscular degeneration, promotes myofiber regeneration and improves muscle function in dystrophin-deficient mdx mice.
- Published in:
- Human Molecular Genetics, 2011, v. 20, n. 7, p. 1324, doi. 10.1093/hmg/ddr015
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- Publication type:
- Article
Mitochondrial abnormalities, energy deficit and oxidative stress are features of calpain 3 deficiency in skeletal muscle.
- Published in:
- Human Molecular Genetics, 2009, v. 18, n. 17, p. 3194, doi. 10.1093/hmg/ddp257
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- Publication type:
- Article
Deficiency of the E3 ubiquitin ligase TRIM32 in mice leads to a myopathy with a neurogenic component.
- Published in:
- Human Molecular Genetics, 2009, v. 18, n. 7, p. 1353, doi. 10.1093/hmg/ddp036
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- Publication type:
- Article
Novel role of calpain-3 in the triad-associated protein complex regulating calcium release in skeletal muscle.
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- Human Molecular Genetics, 2008, v. 17, n. 21, p. 3271, doi. 10.1093/hmg/ddn223
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- Publication type:
- Article
Mdm muscular dystrophy: interactions with calpain 3 and a novel functional role for titin's N2A domain.
- Published in:
- Human Molecular Genetics, 2005, v. 14, n. 19, p. 2801, doi. 10.1093/hmg/ddi313
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- Publication type:
- Article
Calpain 3 participates in sarcomere remodeling by acting upstream of the ubiquitin–proteasome pathway.
- Published in:
- Human Molecular Genetics, 2005, v. 14, n. 15, p. 2125, doi. 10.1093/hmg/ddi217
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- Publication type:
- Article
Null mutation of calpain 3 (p94) in mice causes abnormal sarcomere formation in vivo and in vitro.
- Published in:
- Human Molecular Genetics, 2004, v. 13, n. 13, p. 1373, doi. 10.1093/hmg/ddh153
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- Publication type:
- Article
Overexpression of a calpastatin transgene in mdx muscle reduces dystrophic pathology.
- Published in:
- Human Molecular Genetics, 2002, v. 11, n. 21, p. 2645, doi. 10.1093/hmg/11.21.2645
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- Publication type:
- Article
Calcium Influx into Human Neuroblastoma Cells Induces ALZ-50 Immunoreactivity: Involvement of Calpain-Mediated Hydrolysis of Protein Kinase C.
- Published in:
- Journal of Neurochemistry, 1996, v. 66, n. 4, p. 1539, doi. 10.1046/j.1471-4159.1996.66041539.x
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- Publication type:
- Article