Found: 40
Select item for more details and to access through your institution.
Myelin Disruption, Neuroinflammation, and Oxidative Stress Induced by Sulfite in the Striatum of Rats Are Mitigated by the pan-PPAR agonist Bezafibrate.
- Published in:
- Cells (2073-4409), 2023, v. 12, n. 12, p. 1557, doi. 10.3390/cells12121557
- By:
- Publication type:
- Article
Pathogenesis of brain damage in glutaric acidemia type I: Lessons from the genetic mice model.
- Published in:
- International Journal of Developmental Neuroscience, 2019, v. 78, p. 215, doi. 10.1016/j.ijdevneu.2019.05.005
- By:
- Publication type:
- Article
Nuclear Factor Erythroid-Related Factor 2 Signaling in the Neuropathophysiology of Inherited Metabolic Disorders.
- Published in:
- Frontiers in Cellular Neuroscience, 2021, v. 15, p. 1, doi. 10.3389/fncel.2021.785057
- By:
- Publication type:
- Article
Impairment of brain redox homeostasis caused by the major metabolites accumulating in hyperornithinemia-hyperammonemia-homocitrullinuria syndrome in vivo.
- Published in:
- Metabolic Brain Disease, 2012, v. 27, n. 4, p. 521, doi. 10.1007/s11011-012-9327-5
- By:
- Publication type:
- Article
Evidence that 2-methylacetoacetate induces oxidative stress in rat brain.
- Published in:
- Metabolic Brain Disease, 2010, v. 25, n. 3, p. 261, doi. 10.1007/s11011-010-9204-z
- By:
- Publication type:
- Article
Induction of S100B secretion in C6 astroglial cells by the major metabolites accumulating in glutaric acidemia type I.
- Published in:
- Metabolic Brain Disease, 2010, v. 25, n. 2, p. 191, doi. 10.1007/s11011-010-9203-0
- By:
- Publication type:
- Article
Inhibition of creatine kinase activity by lysine in rat cerebral cortex.
- Published in:
- Metabolic Brain Disease, 2009, v. 24, n. 2, p. 349, doi. 10.1007/s11011-009-9131-z
- By:
- Publication type:
- Article
Influence of ketone bodies on oxidative stress parameters in brain of developing rats in vitro.
- Published in:
- Metabolic Brain Disease, 2008, v. 23, n. 4, p. 411, doi. 10.1007/s11011-008-9108-3
- By:
- Publication type:
- Article
Disturbance of Mitochondrial Dynamics, Endoplasmic Reticulum–Mitochondria Crosstalk, Redox Homeostasis, and Inflammatory Response in the Brain of Glutaryl-CoA Dehydrogenase-Deficient Mice: Neuroprotective Effects of Bezafibrate.
- Published in:
- Molecular Neurobiology, 2022, v. 59, n. 8, p. 4839, doi. 10.1007/s12035-022-02887-3
- By:
- Publication type:
- Article
Insights from Animal Models on the Pathophysiology of Hyperphenylalaninemia: Role of Mitochondrial Dysfunction, Oxidative Stress and Inflammation.
- Published in:
- Molecular Neurobiology, 2021, v. 58, n. 6, p. 2897, doi. 10.1007/s12035-021-02304-1
- By:
- Publication type:
- Article
Guanosine Neuroprotection of Presynaptic Mitochondrial Calcium Homeostasis in a Mouse Study with Amyloid-β Oligomers.
- Published in:
- Molecular Neurobiology, 2020, v. 57, n. 11, p. 4790, doi. 10.1007/s12035-020-02064-4
- By:
- Publication type:
- Article
Free Radical Scavengers Prevent Argininosuccinic Acid-Induced Oxidative Stress in the Brain of Developing Rats: a New Adjuvant Therapy for Argininosuccinate Lyase Deficiency?
- Published in:
- Molecular Neurobiology, 2020, v. 57, n. 2, p. 1233, doi. 10.1007/s12035-019-01825-0
- By:
- Publication type:
- Article
Disruption of Brain Redox Homeostasis, Microglia Activation and Neuronal Damage Induced by Intracerebroventricular Administration of S-Adenosylmethionine to Developing Rats.
- Published in:
- Molecular Neurobiology, 2019, v. 56, n. 4, p. 2760, doi. 10.1007/s12035-018-1275-6
- By:
- Publication type:
- Article
Long Lasting High Lysine Diet Aggravates White Matter Injury in Glutaryl-CoA Dehydrogenase Deficient (Gcdh−/−) Mice.
- Published in:
- Molecular Neurobiology, 2019, v. 56, n. 1, p. 648, doi. 10.1007/s12035-018-1077-x
- By:
- Publication type:
- Article
Glycine Administration Alters MAPK Signaling Pathways and Causes Neuronal Damage in Rat Brain: Putative Mechanisms Involved in the Neurological Dysfunction in Nonketotic Hyperglycinemia.
- Published in:
- Molecular Neurobiology, 2018, v. 55, n. 1, p. 741, doi. 10.1007/s12035-016-0319-z
- By:
- Publication type:
- Article
Higher Vulnerability of Menadione-Exposed Cortical Astrocytes of Glutaryl-CoA Dehydrogenase Deficient Mice to Oxidative Stress, Mitochondrial Dysfunction, and Cell Death: Implications for the Neurodegeneration in Glutaric Aciduria Type I.
- Published in:
- Molecular Neurobiology, 2017, v. 54, n. 6, p. 4795, doi. 10.1007/s12035-016-0023-z
- By:
- Publication type:
- Article
Intracerebral Glycine Administration Impairs Energy and Redox Homeostasis and Induces Glial Reactivity in Cerebral Cortex of Newborn Rats.
- Published in:
- Molecular Neurobiology, 2016, v. 53, n. 9, p. 5864, doi. 10.1007/s12035-015-9493-7
- By:
- Publication type:
- Article
Oxidative Stress, Disrupted Energy Metabolism, and Altered Signaling Pathways in Glutaryl-CoA Dehydrogenase Knockout Mice: Potential Implications of Quinolinic Acid Toxicity in the Neuropathology of Glutaric Acidemia Type I.
- Published in:
- Molecular Neurobiology, 2016, v. 53, n. 9, p. 6459, doi. 10.1007/s12035-015-9548-9
- By:
- Publication type:
- Article
Induction of a Proinflammatory Response in Cortical Astrocytes by the Major Metabolites Accumulating in HMG-CoA Lyase Deficiency: the Role of ERK Signaling Pathway in Cytokine Release.
- Published in:
- Molecular Neurobiology, 2016, v. 53, n. 6, p. 3586, doi. 10.1007/s12035-015-9289-9
- By:
- Publication type:
- Article
d-Serine administration provokes lipid oxidation and decreases the antioxidant defenses in rat striatum
- Published in:
- International Journal of Developmental Neuroscience, 2010, v. 28, n. 4, p. 297, doi. 10.1016/j.ijdevneu.2010.03.002
- By:
- Publication type:
- Article
Evidence that the major metabolites accumulating in hyperornithinemia–hyperammonemia–homocitrullinuria syndrome induce oxidative stress in brain of young rats
- Published in:
- International Journal of Developmental Neuroscience, 2009, v. 27, n. 7, p. 635, doi. 10.1016/j.ijdevneu.2009.08.004
- By:
- Publication type:
- Article
Striatum is more vulnerable to oxidative damage induced by the metabolites accumulating in 3-hydroxy-3-methylglutaryl-CoA lyase deficiency as compared to liver
- Published in:
- International Journal of Developmental Neuroscience, 2009, v. 27, n. 4, p. 351, doi. 10.1016/j.ijdevneu.2009.03.001
- By:
- Publication type:
- Article
Lysine induces lipid and protein damage and decreases reduced glutathione concentrations in brain of young rats
- Published in:
- International Journal of Developmental Neuroscience, 2008, v. 26, n. 7, p. 693, doi. 10.1016/j.ijdevneu.2008.07.011
- By:
- Publication type:
- Article
Experimental Evidence that Methylmalonic Acid Provokes Oxidative Damage and Compromises Antioxidant Defenses in Nerve Terminal and Striatum of Young Rats.
- Published in:
- Cellular & Molecular Neurobiology, 2011, v. 31, n. 5, p. 775, doi. 10.1007/s10571-011-9675-4
- By:
- Publication type:
- Article
Experimental Evidence that Phenylalanine Provokes Oxidative Stress in Hippocanipus and Cerebral Cortex of Developing Rats.
- Published in:
- Cellular & Molecular Neurobiology, 2010, v. 30, n. 2, p. 317, doi. 10.1007/s10571-009-9455-6
- By:
- Publication type:
- Article
Glycine Provokes Lipid Oxidative Damage and Reduces the Antioxidant Defenses in Brain Cortex of Young Rats.
- Published in:
- Cellular & Molecular Neurobiology, 2009, v. 29, n. 2, p. 253, doi. 10.1007/s10571-008-9318-6
- By:
- Publication type:
- Article
Increased susceptibility to quinolinic acid‐induced seizures and long‐term changes in brain oscillations in an animal model of glutaric acidemia type I.
- Published in:
- Journal of Neuroscience Research, 2022, v. 100, n. 4, p. 992, doi. 10.1002/jnr.24980
- By:
- Publication type:
- Article
Experimental Evidence that 3-Methylglutaric Acid Disturbs Mitochondrial Function and Induced Oxidative Stress in Rat Brain Synaptosomes: New Converging Mechanisms.
- Published in:
- Neurochemical Research, 2016, v. 41, n. 10, p. 2619, doi. 10.1007/s11064-016-1973-2
- By:
- Publication type:
- Article
Neurochemical Evidence that Lysine Inhibits Synaptic Na,K-ATPase Activity and Provokes Oxidative Damage in Striatum of Young Rats In vivo.
- Published in:
- Neurochemical Research, 2011, v. 36, n. 2, p. 205, doi. 10.1007/s11064-010-0302-4
- By:
- Publication type:
- Article
Reticular Dysgenesis and Mitochondriopathy Induced by Adenylate Kinase 2 Deficiency with Atypical Presentation.
- Published in:
- Scientific Reports, 2019, v. 9, n. 1, p. N.PAG, doi. 10.1038/s41598-019-51922-2
- By:
- Publication type:
- Article
ETHE1 and MOCS1 deficiencies: Disruption of mitochondrial bioenergetics, dynamics, redox homeostasis and endoplasmic reticulum-mitochondria crosstalk in patient fibroblasts.
- Published in:
- Scientific Reports, 2019, v. 9, n. 1, p. N.PAG, doi. 10.1038/s41598-019-49014-2
- By:
- Publication type:
- Article
Increased Glutamate Receptor and Transporter Expression in the Cerebral Cortex and Striatum of <i>Gcdh</i><sup>-/-</sup> Mice: Possible Implications for the Neuropathology of Glutaric Acidemia Type I.
- Published in:
- PLoS ONE, 2014, v. 9, n. 3, p. 1, doi. 10.1371/journal.pone.0090477
- By:
- Publication type:
- Article
S-adenosylmethionine induces mitochondrial dysfunction, permeability transition pore opening and redox imbalance in subcellular preparations of rat liver.
- Published in:
- Journal of Bioenergetics & Biomembranes, 2021, v. 53, n. 5, p. 525, doi. 10.1007/s10863-021-09914-3
- By:
- Publication type:
- Article
Ethylmalonic acid impairs bioenergetics by disturbing succinate and glutamate oxidation and induces mitochondrial permeability transition pore opening in rat cerebellum.
- Published in:
- Journal of Neurochemistry, 2021, v. 158, n. 2, p. 262, doi. 10.1111/jnc.15363
- By:
- Publication type:
- Article
Ethylmalonic acid impairs bioenergetics by disturbing succinate and glutamate oxidation and induces mitochondrial permeability transition pore opening in rat cerebellum.
- Published in:
- Journal of Neurochemistry, 2021, v. 158, n. 1, p. 262, doi. 10.1111/jnc.15363
- By:
- Publication type:
- Article
Evidence that 3-hydroxy-3-methylglutaric and 3-methylglutaric acids induce DNA damage in rat striatum.
- Published in:
- Metabolic Brain Disease, 2015, v. 30, n. 4, p. 1055, doi. 10.1007/s11011-015-9675-z
- By:
- Publication type:
- Article
Mitochondrial energetics is impaired in very long-chain acyl-CoA dehydrogenase deficiency and can be rescued by treatment with mitochondria-targeted electron scavengers.
- Published in:
- Human Molecular Genetics, 2019, v. 28, n. 6, p. 928, doi. 10.1093/hmg/ddy403
- By:
- Publication type:
- Article
Lipopolysaccharide-Elicited Systemic Inflammation Induces Selective Vulnerability of Cerebral Cortex and Striatum of Developing Glutaryl-CoA Dehydrogenase Deficient (Gcdh<sup>−/−</sup>) Mice to Oxidative Stress.
- Published in:
- Neurotoxicity Research, 2020, v. 38, n. 4, p. 1024, doi. 10.1007/s12640-020-00291-0
- By:
- Publication type:
- Article
Experimental Evidence that In Vivo Intracerebral Administration of L-2-Hydroxyglutaric Acid to Neonatal Rats Provokes Disruption of Redox Status and Histopathological Abnormalities in the Brain.
- Published in:
- Neurotoxicity Research, 2018, v. 33, n. 3, p. 681, doi. 10.1007/s12640-018-9874-6
- By:
- Publication type:
- Article
Induction of Neuroinflammatory Response and Histopathological Alterations Caused by Quinolinic Acid Administration in the Striatum of Glutaryl-CoA Dehydrogenase Deficient Mice.
- Published in:
- Neurotoxicity Research, 2018, v. 33, n. 3, p. 593, doi. 10.1007/s12640-017-9848-0
- By:
- Publication type:
- Article