The mtDNA T8993G (NARP) mutation results in an impairment of oxidative phosphorylation that can be improved by antioxidants.Published in:Human Molecular Genetics, 2004, v. 13, n. 8, p. 869, doi. 10.1093/hmg/ddh103By:Mattiazzi, Marina;Vijayvergiya, Chetan;Gajewski, Carl D.;DeVivo, Darryl C.;Lenaz, Giorgio;Wiedmann, Martin;Manfredi, GiovanniPublication type:Article
Neural mitochondrial Ca<sup>2+</sup> capacity impairment precedes the onset of motor symptoms in G93A Cu/Zn-superoxide dismutase mutant mice.Published in:Journal of Neurochemistry, 2006, v. 96, n. 5, p. 1349, doi. 10.1111/j.1471-4159.2006.03619.xBy:Damiano, Maria;Starkov, Anatoly A.;Petri, Susanne;Kipiani, Kathuna;Kiaei, Mahmoud;Mattiazzi, Marina;Flint Beal, M.;Manfredi, GiovanniPublication type:Article