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Long-Term Impact of Lumacaftor/Ivacaftor Treatment on Cystic Fibrosis Disease Progression in Children 2–5 Years of Age Homozygous for F508del-CFTR : A Phase 2, Open-Label Clinical Trial.
- Published in:
- Annals of the American Thoracic Society, 2024, v. 21, n. 11, p. 1550, doi. 10.1513/AnnalsATS.202402-201OC
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- Publication type:
- Article
Pleuropneumonia caused by Nocardia cyriacigeorgica in a 14‐year‐old girl with primary ciliary dyskinesia.
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- Pediatric Pulmonology, 2023, v. 58, n. 9, p. 2656, doi. 10.1002/ppul.26536
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- Publication type:
- Article
Mucus obstruction and inflammation in early cystic fibrosis lung disease: Emerging role of the IL‐1 signaling pathway.
- Published in:
- Pediatric Pulmonology, 2019, v. 54, p. S5, doi. 10.1002/ppul.24462
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- Publication type:
- Article
Potential of Intestinal Current Measurement for Personalized Treatment of Patients with Cystic Fibrosis.
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- Journal of Personalized Medicine, 2021, v. 11, n. 5, p. 384, doi. 10.3390/jpm11050384
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- Publication type:
- Article
Effects of elexacaftor/tezacaftor/ ivacaftor therapy on mental health of patients with cystic fibrosis.
- Published in:
- Frontiers in Pharmacology, 2023, p. 1, doi. 10.3389/fphar.2023.1179208
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- Publication type:
- Article
Long-term effects of lumacaftor/ivacaftor on paranasal sinus abnormalities in children with cystic fibrosis detected with magnetic resonance imaging.
- Published in:
- Frontiers in Pharmacology, 2023, v. 14, p. 1, doi. 10.3389/fphar.2023.1161891
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- Publication type:
- Article
Homozygous CFTR mutation M348K in a boy with respiratory symptoms and failure to thrive. Disease-causing mutation or benign alteration?
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- European Journal of Pediatrics, 2012, v. 171, n. 7, p. 1039, doi. 10.1007/s00431-012-1672-1
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- Publication type:
- Article
Antigen‐driven PD‐1<sup>+</sup>TOX<sup>+</sup>BHLHE40<sup>+</sup> and PD‐1<sup>+</sup>TOX<sup>+</sup>EOMES<sup>+</sup> T lymphocytes regulate juvenile idiopathic arthritis in situ.
- Published in:
- European Journal of Immunology, 2021, v. 51, n. 4, p. 915, doi. 10.1002/eji.202048797
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- Publication type:
- Article
ELF5 is a potential respiratory epithelial cell-specific risk gene for severe COVID-19.
- Published in:
- Nature Communications, 2022, v. 13, n. 1, p. 1, doi. 10.1038/s41467-022-31999-6
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- Publication type:
- Article
Gene signature driving invasive mucinous adenocarcinoma of the lung.
- Published in:
- EMBO Molecular Medicine, 2017, v. 9, n. 4, p. 462, doi. 10.15252/emmm.201606711
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- Publication type:
- Article
SARS-CoV-2 infection and transmission in school settings during the second COVID-19 wave: a cross-sectional study, Berlin, Germany, November 2020.
- Published in:
- Eurosurveillance (15607917), 2021, v. 26, n. 34, p. 1, doi. 10.2807/1560-7917.ES.2021.26.34.2100184
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- Publication type:
- Article
Genetic Deletion of Mmp9 Does Not Reduce Airway Inflammation and Structural Lung Damage in Mice with Cystic Fibrosis-like Lung Disease.
- Published in:
- International Journal of Molecular Sciences, 2022, v. 23, n. 21, p. 13405, doi. 10.3390/ijms232113405
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- Publication type:
- Article
Linking Fibrotic Remodeling and Ultrastructural Alterations of Alveolar Epithelial Cells after Deletion of Nedd4-2.
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- International Journal of Molecular Sciences, 2021, v. 22, n. 14, p. 7607, doi. 10.3390/ijms22147607
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- Publication type:
- Article
Congenital Deletion of Nedd4-2 in Lung Epithelial Cells Causes Progressive Alveolitis and Pulmonary Fibrosis in Neonatal Mice.
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- International Journal of Molecular Sciences, 2021, v. 22, n. 11, p. 6146, doi. 10.3390/ijms22116146
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- Publication type:
- Article
Proteases, Mucus, and Mucosal Immunity in Chronic Lung Disease.
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- International Journal of Molecular Sciences, 2021, v. 22, n. 9, p. 5018, doi. 10.3390/ijms22095018
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- Publication type:
- Article
Neutrophil Adaptations upon Recruitment to the Lung: New Concepts and Implications for Homeostasis and Disease.
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- International Journal of Molecular Sciences, 2020, v. 21, n. 3, p. 851, doi. 10.3390/ijms21030851
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- Publication type:
- Article
SLC26A9-mediated chloride secretion prevents mucus obstruction in airway inflammation.
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- Journal of Clinical Investigation, 2012, v. 122, n. 10, p. 3629, doi. 10.1172/JCI60429
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- Publication type:
- Article
Airway mucus, inflammation and remodeling: emerging links in the pathogenesis of chronic lung diseases.
- Published in:
- Cell & Tissue Research, 2017, v. 367, n. 3, p. 537, doi. 10.1007/s00441-016-2562-z
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- Publication type:
- Article
The cystic fibrosis transmembrane conductance regulator (CFTR) inhibits ENaC through an increase in the intracellular Cl<sup>-</sup> concentration.
- Published in:
- EMBO Reports, 2001, v. 2, n. 11, p. 1047, doi. 10.1093/embo-reports/kve232
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- Publication type:
- Article
Magnetic Resonance Imaging of Pulmonary and Paranasal Sinus Abnormalities in Children with Primary Ciliary Dyskinesia Compared to Children with Cystic Fibrosis.
- Published in:
- Annals of the American Thoracic Society, 2024, v. 21, n. 3, p. 438, doi. 10.1513/AnnalsATS.202305-453OC
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- Publication type:
- Article
Elexacaftor/Tezacaftor/Ivacaftor Improves Bronchial Artery Dilatation Detected by Magnetic Resonance Imaging in Patients with Cystic Fibrosis.
- Published in:
- Annals of the American Thoracic Society, 2023, v. 20, n. 11, p. 1595, doi. 10.1513/AnnalsATS.202302-168OC
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- Publication type:
- Article
Effects of Lumacaftor/Ivacaftor on Cystic Fibrosis Disease Progression in Children 2 through 5 Years of Age Homozygous for F508del-CFTR: A Phase 2 Placebo-controlled Clinical Trial.
- Published in:
- Annals of the American Thoracic Society, 2023, v. 20, n. 8, p. 1144, doi. 10.1513/AnnalsATS.202208-684OC
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- Publication type:
- Article
Longitudinal Magnetic Resonance Imaging Detects Onset and Progression of Chronic Rhinosinusitis from Infancy to School Age in Cystic Fibrosis.
- Published in:
- Annals of the American Thoracic Society, 2023, v. 20, n. 5, p. 687, doi. 10.1513/AnnalsATS.202209-763OC
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- Publication type:
- Article
Effects of Lumacaftor-Ivacaftor on Lung Clearance Index, Magnetic Resonance Imaging, and Airway Microbiome in Phe508del Homozygous Patients with Cystic Fibrosis.
- Published in:
- 2021
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- Publication type:
- journal article
Magnetic Resonance Imaging Detects Chronic Rhinosinusitis in Infants and Preschool Children with Cystic Fibrosis.
- Published in:
- 2020
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- Publication type:
- journal article
Cellular distribution and function of ion channels involved in transport processes in rat tracheal epithelium.
- Published in:
- Physiological Reports, 2017, v. 5, n. 12, p. n/a, doi. 10.14814/phy2.13290
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- Publication type:
- Article
Exploring Clinical and Epidemiological Characteristics of Interstitial Lung Diseases: Rationale, Aims, and Design of a Nationwide Prospective Registry—The EXCITING-ILD Registry.
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- BioMed Research International, 2015, v. 2015, p. 1, doi. 10.1155/2015/123876
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- Publication type:
- Article
Age-Related Differences in Structure and Function of Nasal Epithelial Cultures From Healthy Children and Elderly People.
- Published in:
- Frontiers in Immunology, 2022, v. 13, p. 1, doi. 10.3389/fimmu.2022.822437
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- Publication type:
- Article
Effect of genistein on native epithelial tissue from normal individuals and CF patients and on ion channels expressed in Xenopus oocytes.
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- British Journal of Pharmacology, 2000, v. 130, n. 8, p. 1884, doi. 10.1038/sj.bjp.0703520
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- Publication type:
- Article
Homeostatic nuclear RAGE-ATM interaction is essential for efficient DNA repair.
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- Nucleic Acids Research, 2017, v. 45, n. 18, p. 10595, doi. 10.1093/nar/gkx705
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- Publication type:
- Article
Epigenetic reprogramming of airway macrophages promotes polarization and inflammation in muco-obstructive lung disease.
- Published in:
- Nature Communications, 2021, v. 12, n. 1, p. 1, doi. 10.1038/s41467-021-26777-9
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- Publication type:
- Article
Generalized anxiety disorder in Berlin school children after the third COVID-19 wave in Germany: a cohort study between June and September 2021.
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- Child & Adolescent Psychiatry & Mental Health, 2023, v. 17, n. 1, p. 1, doi. 10.1186/s13034-022-00552-0
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- Publication type:
- Article
Health-related quality of life and impact of socioeconomic status among primary and secondary school students after the third COVID-19 wave in Berlin, Germany.
- Published in:
- PLoS ONE, 2024, v. 19, n. 5, p. 1, doi. 10.1371/journal.pone.0302995
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- Publication type:
- Article
Genetic Deletion and Pharmacological Inhibition of PI3K γ Reduces Neutrophilic Airway Inflammation and Lung Damage in Mice with Cystic Fibrosis-Like Lung Disease.
- Published in:
- Mediators of Inflammation, 2015, v. 2015, p. 1, doi. 10.1155/2015/545417
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- Publication type:
- Article
New Developments in Cystic Fibrosis Airway Inflammation.
- Published in:
- Mediators of Inflammation, 2015, v. 2015, p. 1, doi. 10.1155/2015/769425
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- Publication type:
- Article
Free DNA in Cystic Fibrosis Airway Fluids Correlates with Airflow Obstruction.
- Published in:
- Mediators of Inflammation, 2015, v. 2015, p. 1, doi. 10.1155/2015/408935
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- Publication type:
- Article
The serine protease inhibitor SerpinA3N attenuates neuropathic pain by inhibiting T cell-derived leukocyte elastase.
- Published in:
- Nature Medicine, 2015, v. 21, n. 5, p. 518, doi. 10.1038/nm.3852
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- Publication type:
- Article
CXCR2 mediates NADPH oxidase-independent neutrophil extracellular trap formation in cystic fibrosis airway inflammation.
- Published in:
- Nature Medicine, 2011, v. 17, n. 7, p. 899, doi. 10.1038/nm0711-899a
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- Publication type:
- Article
CXCR2 mediates NADPH oxidase–independent neutrophil extracellular trap formation in cystic fibrosis airway inflammation.
- Published in:
- Nature Medicine, 2010, v. 16, n. 9, p. 1018, doi. 10.1038/nm.2209
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- Publication type:
- Article
Increased airway epithelial Na<sup>+</sup> absorption produces cystic fibrosis-like lung disease in mice.
- Published in:
- Nature Medicine, 2004, v. 10, n. 5, p. 487, doi. 10.1038/nm1028
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- Publication type:
- Article
Compromised DNA repair is responsible for diabetes‐associated fibrosis.
- Published in:
- EMBO Journal, 2020, v. 39, n. 11, p. 1, doi. 10.15252/embj.2019103477
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- Publication type:
- Article
Nanoparticle uptake by airway phagocytes after fungal spore challenge in murine allergic asthma and chronic bronchitis.
- Published in:
- BMC Pulmonary Medicine, 2014, v. 14, n. 1, p. 116, doi. 10.1186/1471-2466-14-116
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- Publication type:
- Article
Nanoparticle uptake by airway phagocytes after fungal spore challenge in murine allergic asthma and chronic bronchitis.
- Published in:
- 2014
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- Publication type:
- journal article
Räumlich aufgelöste Analyse der Aktivität der Neutrophilenelastase mit ratiometrischen Fluoreszenzsonden.
- Published in:
- Angewandte Chemie, 2012, v. 124, n. 25, p. 6363, doi. 10.1002/ange.201109226
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- Publication type:
- Article
Rare cause for hemoptysis in an adolescent: Bronchial capillary hemangioma.
- Published in:
- Pediatric Pulmonology, 2017, v. 52, n. 7, p. E40, doi. 10.1002/ppul.23673
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- Publication type:
- Article
Five years of experience with biochemical cystic fibrosis newborn screening based on IRT/PAP in Germany.
- Published in:
- Pediatric Pulmonology, 2015, v. 50, n. 7, p. 655, doi. 10.1002/ppul.23190
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- Publication type:
- Article
Incidence and outcomes of SARS-CoV-2-associated PIMS in Germany: a nationwide analysis.
- Published in:
- 2022
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- Publication type:
- Letter
Studying the pathophysiology of coronavirus disease 2019: a protocol for the Berlin prospective COVID-19 patient cohort (Pa-COVID-19).
- Published in:
- Infection, 2020, v. 48, n. 4, p. 619, doi. 10.1007/s15010-020-01464-x
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- Publication type:
- Article
Mukoviszidose im Kindes- und im Erwachsenenalter.
- Published in:
- Innere Medizin (2731-7080), 2024, v. 65, n. 6, p. 538, doi. 10.1007/s00108-024-01717-z
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- Publication type:
- Article
Immune-mediated inflammatory diseases (IMIDs) in children: key research questions and some answers.
- Published in:
- Molecular & Cellular Pediatrics, 2024, v. 11, n. 1, p. 1, doi. 10.1186/s40348-024-00177-7
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- Publication type:
- Article