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Ivacaftor Reverses Airway Mucus Abnormalities in a Rat Model Harboring a Humanized G551D-CFTR.
Published in:
2020
By:
- Birket, Susan E.;
- Davis, Joy M.;
- Fernandez-Petty, Courtney M.;
- Henderson, Alexander G.;
- Oden, Ashley M.;
- LiPing Tang;
- Hui Wen;
- Jeong Hong;
- Lianwu Fu;
- Chambers, Andre;
- Fields, Alvin;
- Zhao, Gojun;
- Tearney, Guillermo J.;
- Sorscher, Eric J.;
- Rowe, Steven M.;
- Tang, LiPing;
- Wen, Hui;
- Hong, Jeong;
- Fu, Lianwu
Publication type:
journal article
A small molecule that induces translational readthrough of CFTR nonsense mutations by eRF1 depletion.
Published in:
Nature Communications, 2021, v. 12, n. 1, p. 1, doi. 10.1038/s41467-021-24575-x
By:
- Sharma, Jyoti;
- Du, Ming;
- Wong, Eric;
- Mutyam, Venkateshwar;
- Li, Yao;
- Chen, Jianguo;
- Wangen, Jamie;
- Thrasher, Kari;
- Fu, Lianwu;
- Peng, Ning;
- Tang, Liping;
- Liu, Kaimao;
- Mathew, Bini;
- Bostwick, Robert J.;
- Augelli-Szafran, Corinne E.;
- Bihler, Hermann;
- Liang, Feng;
- Mahiou, Jerome;
- Saltz, Josef;
- Rab, Andras
Publication type:
Article
Prime editing-mediated correction of the CFTR W1282X mutation in iPSCs and derived airway epithelial cells.
Published in:
PLoS ONE, 2023, v. 18, n. 11, p. 1, doi. 10.1371/journal.pone.0295009
By:
- Li, Chao;
- Liu, Zhong;
- Anderson, Justin;
- Liu, Zhongyu;
- Tang, Liping;
- Li, Yao;
- Peng, Ning;
- Chen, Jianguo;
- Liu, Xueming;
- Fu, Lianwu;
- Townes, Tim M.;
- Rowe, Steven M.;
- Bedwell, David M.;
- Guimbellot, Jennifer;
- Zhao, Rui
Publication type:
Article
Traffic-independent function of the Sar1p/COPII machinery in proteasomal sorting of the cystic fibrosis transmembrane conductance regulator.
Published in:
Journal of Cell Biology, 2003, v. 160, n. 2, p. 157, doi. 10.1083/jcb.200210086
By:
- Lianwu Fu;
- Sztul, Elizabeth
Publication type:
Article
Extended stop codon context predicts nonsense codon readthrough efficiency in human cells.
Published in:
Nature Communications, 2024, v. 15, n. 1, p. 1, doi. 10.1038/s41467-024-46703-z
By:
- Mangkalaphiban, Kotchaphorn;
- Fu, Lianwu;
- Du, Ming;
- Thrasher, Kari;
- Keeling, Kim M.;
- Bedwell, David M.;
- Jacobson, Allan
Publication type:
Article
ΔF508 CFTR Surface Stability Is Regulated by DAB2 and CHIP-Mediated Ubiquitination in Post-Endocytic Compartments.
Published in:
PLoS ONE, 2015, v. 10, n. 4, p. 1, doi. 10.1371/journal.pone.0123131
By:
- Fu, Lianwu;
- Rab, Andras;
- Tang, Li ping;
- Bebok, Zsuzsa;
- Rowe, Steven M.;
- Bartoszewski, Rafal;
- Collawn, James F.
Publication type:
Article
Novel Therapy of Bicarbonate, Glutathione, and Ascorbic Acid Improves Cystic Fibrosis Mucus Transport.
Published in:
American Journal of Respiratory Cell & Molecular Biology, 2020, v. 63, n. 3, p. 362, doi. 10.1165/rcmb.2019-0287OC
By:
- Adewale, Adegboyega Timothy;
- Libby, Emily Falk;
- Lianwu Fu;
- Lenzie, Andrew;
- Boitet, Evan R.;
- Birket, Susan E.;
- Petty, Courtney Fernandez;
- Johns, J. Dixon;
- Mazur, Marina;
- Tearney, Guillermo J.;
- Copeland, Dan;
- Durham, Carolyn;
- Rowe, Steven M.
Publication type:
Article
ARFGAP1 promotes AP-2-dependent endocytosis.
Published in:
Nature Cell Biology, 2011, v. 13, n. 5, p. 559, doi. 10.1038/ncb2221
By:
- Bai, Ming;
- Gad, Helge;
- Turacchio, Gabriele;
- Cocucci, Emanuele;
- Yang, Jia-Shu;
- Li, Jian;
- Beznoussenko, Galina V.;
- Nie, Zhongzhen;
- Luo, Ruibai;
- Fu, Lianwu;
- Collawn, James F.;
- Kirchhausen, Tomas;
- Luini, Alberto;
- Hsu, Victor W.
Publication type:
Article
A synonymous codon change alters the drug sensitivity of ?F508 cystic fibrosis transmembrane conductance regulator.
Published in:
FASEB Journal, 2016, v. 30, n. 1, p. 201, doi. 10.1096/fj.15-273714
By:
- Bali, Vedrana;
- Lazrak, Ahmed;
- Guroji, Purushotham;
- Lianwu Fu;
- Matalon, Sadis;
- Bebok, Zsuzsanna
Publication type:
Article
The silent codon change I507-ATC→ATT contributes to the severity of the ΔF508 CFTR channel dysfunction.
Published in:
FASEB Journal, 2013, v. 27, n. 11, p. 4630, doi. 10.1096/fj.13-227330
By:
- Lazrak, Ahmed;
- Lianwu Fu;
- Bali, Vedrana;
- Bartoszewski, Rafal;
- Rab, Andras;
- Havasi, Viktoria;
- Keiles, Steve;
- Kappes, John;
- Kumar, Ranjit;
- Lefkowitz, Elliot;
- Sorscher, Eric J.;
- Matalon, Sadis;
- Collawn, James F.;
- Bebok, Zsuzsanna
Publication type:
Article

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