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Nucleosides accelerate inflammatory osteolysis, acting as distinct innate immune activators.
- Published in:
- Journal of Bone & Mineral Research, 2011, v. 26, n. 8, p. 1913, doi. 10.1002/jbmr.400
- By:
- Publication type:
- Article
Subacute TGFβ Exposure Drives Airway Hyperresponsiveness in Cystic Fibrosis Mice through the PI3K Pathway.
- Published in:
- American Journal of Respiratory Cell & Molecular Biology, 2020, v. 62, n. 5, p. 657, doi. 10.1165/rcmb.2019-0158OC
- By:
- Publication type:
- Article
Restoration of W1282X CFTR Activity by Enhanced Expression.
- Published in:
- American Journal of Respiratory Cell & Molecular Biology, 2007, v. 37, n. 3, p. 347, doi. 10.1165/rcmb.2006-0176OC
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- Publication type:
- Article
No Detectable Improvements in Cystic Fibrosis Transmembrane Conductance Regulator by Nasal Aminoglycosides in Patients with Cystic Fibrosis with Stop Mutations.
- Published in:
- American Journal of Respiratory Cell & Molecular Biology, 2007, v. 37, n. 1, p. 57, doi. 10.1165/rcmb.2006-0173OC
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- Publication type:
- Article
Adenosine Receptors and Phosphodiesterase Inhibitors Stimulate Cl<sup>-</sup> Secretion in Calu-3 Cells.
- Published in:
- American Journal of Respiratory Cell & Molecular Biology, 2003, v. 29, n. 3, p. 410, doi. 10.1165/rcmb.2002-0247OC
- By:
- Publication type:
- Article
Current state of the art MRI for the longitudinal assessment of cystic fibrosis.
- Published in:
- 2020
- By:
- Publication type:
- journal article
Assessment of pulmonary structure-function relationships in young children and adolescents with cystic fibrosis by multivolume proton-MRI and CT.
- Published in:
- 2018
- By:
- Publication type:
- journal article
3123 TGFbeta, Early Cytokine Dysregulation, and Airway Smooth Muscle Dysfunction in Cystic Fibrosis.
- Published in:
- 2019
- By:
- Publication type:
- Abstract
Joint hierarchical Gaussian process model with application to personalized prediction in medical monitoring.
- Published in:
- Stat, 2018, v. 7, n. 1, p. N.PAG, doi. 10.1002/sta4.178
- By:
- Publication type:
- Article
Evaluating the Impact of Stopping Chronic Therapies after Modulator Drug Therapy in Cystic Fibrosis: The SIMPLIFY Clinical Trial Study Design.
- Published in:
- 2021
- By:
- Publication type:
- journal article
Clinical Effectiveness of Lumacaftor/Ivacaftor in Patients with Cystic Fibrosis Homozygous for F508del-CFTR. A Clinical Trial.
- Published in:
- 2021
- By:
- Publication type:
- journal article
Constrictive Bronchiolitis in Cystic Fibrosis Adolescents with Refractory Pulmonary Decline.
- Published in:
- 2016
- By:
- Publication type:
- journal article
Ultrashort Echo-Time Magnetic Resonance Imaging Is a Sensitive Method for the Evaluation of Early Cystic Fibrosis Lung Disease.
- Published in:
- 2016
- By:
- Publication type:
- journal article
Bayesian regularization for a nonstationary Gaussian linear mixed effects model.
- Published in:
- Statistics in Medicine, 2022, v. 41, n. 4, p. 681, doi. 10.1002/sim.9279
- By:
- Publication type:
- Article
Dynamic predictive probabilities to monitor rapid cystic fibrosis disease progression.
- Published in:
- 2020
- By:
- Publication type:
- journal article
Cystic Fibrosis–Related Diabetes Workshop: Research Priorities Spanning Disease Pathophysiology, Diagnosis, and Outcomes.
- Published in:
- Diabetes, 2023, v. 72, n. 6, p. 677, doi. 10.2337/db22-0949
- By:
- Publication type:
- Article
Phenotypic Alteration of an Established Human Airway Cell Line by Media Selection.
- Published in:
- International Journal of Molecular Sciences, 2023, v. 24, n. 2, p. 1246, doi. 10.3390/ijms24021246
- By:
- Publication type:
- Article
Data driven decision making to characterize clinical personas of parents of children with cystic fibrosis: a mixed methods study.
- Published in:
- 2020
- By:
- Publication type:
- journal article
Aerosolized agents for airway clearance in cystic fibrosis.
- Published in:
- Pediatric Pulmonology, 2019, v. 54, n. 6, p. 858, doi. 10.1002/ppul.24306
- By:
- Publication type:
- Article
Rapid therapeutic advances in CFTR modulator science.
- Published in:
- Pediatric Pulmonology, 2018, v. 53, p. S4, doi. 10.1002/ppul.24157
- By:
- Publication type:
- Article
Predicting future lung function decline in cystic fibrosis patients: Statistical methods and clinical connections.
- Published in:
- Pediatric Pulmonology, 2016, v. 51, n. 2, p. 217, doi. 10.1002/ppul.23357
- By:
- Publication type:
- Article
An Animated Functional Data Analysis Interface to Cluster Rapid Lung Function Decline and Enhance Center-Level Care in Cystic Fibrosis.
- Published in:
- Journal of Healthcare Engineering, 2021, p. 1, doi. 10.1155/2021/6671833
- By:
- Publication type:
- Article
An Animated Functional Data Analysis Interface to Cluster Rapid Lung Function Decline and Enhance Center-Level Care in Cystic Fibrosis.
- Published in:
- Journal of Healthcare Engineering, 2021, p. 1, doi. 10.1155/2021/6671833
- By:
- Publication type:
- Article
Sweat Chloride Testing.
- Published in:
- 2019
- By:
- Publication type:
- Case Study
The Caregiver Quality of Life Cystic Fibrosis (CQOLCF) scale: modification and validation of an instrument to measure quality of life in cystic fibrosis family caregivers.
- Published in:
- 2003
- By:
- Publication type:
- journal article
Pharmaceuticals Targeting Nonsense Mutations in Genetic Diseases.
- Published in:
- BioDrugs, 2009, v. 23, n. 3, p. 165, doi. 10.2165/00063030-200923030-00003
- By:
- Publication type:
- Article
TGF-Beta Downregulation of Distinct Chloride Channels in Cystic Fibrosis-Affected Epithelia.
- Published in:
- PLoS ONE, 2014, v. 9, n. 9, p. 1, doi. 10.1371/journal.pone.0106842
- By:
- Publication type:
- Article
Multicenter Intestinal Current Measurements in Rectal Biopsies from CF and Non-CF Subjects to Monitor CFTR Function.
- Published in:
- PLoS ONE, 2013, v. 8, n. 9, p. 1, doi. 10.1371/journal.pone.0073905
- By:
- Publication type:
- Article
Optimizing Nasal Potential Difference Analysis for CFTR Modulator Development: Assessment of Ivacaftor in CF Subjects with the <i>G551D-CFTR</i> Mutation.
- Published in:
- PLoS ONE, 2013, v. 8, n. 7, p. 1, doi. 10.1371/journal.pone.0066955
- By:
- Publication type:
- Article
Feasibility, tolerability and safety of pediatric hyperpolarized <sup>129</sup>Xe magnetic resonance imaging in healthy volunteers and children with cystic fibrosis.
- Published in:
- 2016
- By:
- Publication type:
- journal article
CFTR Potentiators: Not an Open and Shut Case.
- Published in:
- Science Translational Medicine, 2014, v. 6, n. 246, p. 1, doi. 10.1126/scitranslmed.3009674
- By:
- Publication type:
- Article
Ivacaftor treatment of cystic fibrosis patients with the G551D mutation: a review of the evidence.
- Published in:
- Therapeutic Advances in Respiratory Disease, 2013, v. 7, n. 5, p. 288, doi. 10.1177/1753465813502115
- By:
- Publication type:
- Article
Clinical Effectiveness of Elexacaftor/Tezacaftor/Ivacaftor in People with Cystic Fibrosis: A Clinical Trial.
- Published in:
- 2022
- By:
- Publication type:
- journal article
Clinical Effectiveness of Elexacaftor/Tezacftor/Ivacaftor in People with Cystic Fibrosis.
- Published in:
- American Journal of Respiratory & Critical Care Medicine, 2022, v. 205, n. 5, p. 1, doi. 10.1164/rccm.202108-1986oc
- By:
- Publication type:
- Article
Recombinant Acid Ceramidase Reduces Inflammation and Infection in Cystic Fibrosis.
- Published in:
- 2020
- By:
- Publication type:
- journal article
Regional Structure-Function in Cystic Fibrosis Lung Disease Using Hyperpolarized <sup>129</sup>Xe and Ultrashort Echo Magnetic Resonance Imaging.
- Published in:
- 2020
- By:
- Publication type:
- research
Current Status and Future Opportunities in Lung Precision Medicine Research with a Focus on Biomarkers. An American Thoracic Society/National Heart, Lung, and Blood Institute Research Statement.
- Published in:
- 2018
- By:
- Publication type:
- journal article
Effects of an Antioxidant-enriched Multivitamin in Cystic Fibrosis. A Randomized, Controlled, Multicenter Clinical Trial.
- Published in:
- 2018
- By:
- Publication type:
- journal article
MicroRNA-145, Cystic Fibrosis Transmembrane Conductance Regulator, and Transforming Growth Factor-β. An (Un)tangled Regulatory Web.
- Published in:
- 2018
- By:
- Publication type:
- editorial
Home Monitoring of Patients with Cystic Fibrosis to Identify and Treat Acute Pulmonary Exacerbations. eICE Study Results.
- Published in:
- 2017
- By:
- Publication type:
- journal article
Phenotypes of Rapid Cystic Fibrosis Lung Disease Progression during Adolescence and Young Adulthood.
- Published in:
- 2017
- By:
- Publication type:
- journal article
Cystic Fibrosis Transmembrane Conductance Regulator Function in Airway Smooth Muscle. A Novel Role in Cystic Fibrosis Airway Obstruction.
- Published in:
- 2016
- By:
- Publication type:
- commentary
Personalized Medicine in Cystic Fibrosis.
- Published in:
- American Journal of Respiratory & Critical Care Medicine, 2012, v. 186, n. 7, p. 593, doi. 10.1164/rccm.201204-0785PP
- By:
- Publication type:
- Article
Flexible semiparametric joint modeling: an application to estimate individual lung function decline and risk of pulmonary exacerbations in cystic fbrosis.
- Published in:
- Emerging Themes in Epidemiology, 2017, v. 14, p. 1, doi. 10.1186/s12982-017-0067-1
- By:
- Publication type:
- Article
Clinically-approved CFTR modulators rescue Nrf2 dysfunction in cystic fibrosis airway epithelia.
- Published in:
- 2019
- By:
- Publication type:
- journal article
Capturing the Direct Binding of CFTR Correctors to CFTR by Using Click Chemistry.
- Published in:
- ChemBioChem, 2015, v. 16, n. 14, p. 2017, doi. 10.1002/cbic.201500123
- By:
- Publication type:
- Article
A personalized medicine approach to optimize care for a pediatric cystic fibrosis patient with atypical clinical symptoms.
- Published in:
- Pediatric Pulmonology, 2024, v. 59, n. 1, p. 229, doi. 10.1002/ppul.26719
- By:
- Publication type:
- Article
Built environment factors predictive of early rapid lung function decline in cystic fibrosis.
- Published in:
- Pediatric Pulmonology, 2023, v. 58, n. 5, p. 1501, doi. 10.1002/ppul.26352
- By:
- Publication type:
- Article
Phosphorylation-Dependent Regulation of Apical Membrane Chloride Channels in Normal and Cystic Fibrosis Airway Epithelium<sup>a</sup>.
- Published in:
- Annals of the New York Academy of Sciences, 1989, v. 574, n. 1, p. 44, doi. 10.1111/j.1749-6632.1989.tb25131.x
- By:
- Publication type:
- Article
Functional Impacts of Aminoglycoside Treatment on Speech Perception and Extended High-Frequency Hearing Loss in a Pediatric Cystic Fibrosis Cohort.
- Published in:
- American Journal of Audiology, 2021, v. 30, p. 834, doi. 10.1044/2020_AJA-20-00059
- By:
- Publication type:
- Article