Rescue of NBD2 Mutants N1303K and S1235R of CFTR by Small-Molecule Correctors and Transcomplementation.
- Published in:
- PLoS ONE, 2015, v. 10, n. 3, p. 1, doi. 10.1371/journal.pone.0119796
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- Publication type:
- Article
Works matching AU Cebotaru, Liudmila
Results: 25
1
2
Correcting the Cystic Fibrosis Disease Mutant, A455E CFTR.
- Published in:
- PLoS ONE, 2014, v. 9, n. 1, p. 1, doi. 10.1371/journal.pone.0085183
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- Publication type:
- Article
3
Dexamethasone Regulates CFTR Expression in Calu-3 Cells with the Involvement of Chaperones HSP70 and HSP90.
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- PLoS ONE, 2012, v. 7, n. 12, p. 1, doi. 10.1371/journal.pone.0047405
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- Publication type:
- Article
4
VX‐809 mitigates disease in a mouse model of autosomal dominant polycystic kidney disease bearing the R3277C human mutation.
- Published in:
- FASEB Journal, 2021, v. 35, n. 11, p. 1, doi. 10.1096/fj.202101315R
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- Article
5
Polycystin-1 dependent regulation of polycystin-2 via GRP94, a member of HSP90 family that resides in the endoplasmic reticulum.
- Published in:
- FASEB Journal, 2021, v. 35, n. 10, p. 1, doi. 10.1096/fj.202100325RR
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- Publication type:
- Article
6
The CFTR-Associated Ligand Arrests the Trafficking of the Mutant ΔF508 CFTR Channel in the ER Contributing to Cystic Fibrosis.
- Published in:
- Cellular Physiology & Biochemistry (Karger AG), 2018, v. 45, n. 2, p. 639, doi. 10.1159/000487120
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- Publication type:
- Article
7
The CFTR-Associated Ligand Arrests the Trafficking of the Mutant ΔF508 CFTR Channel in the ER Contributing to Cystic Fibrosis.
- Published in:
- Cellular Physiology & Biochemistry (Karger AG), 2018, v. 45, n. 2, p. 639, doi. 10.1159/000487120
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- Publication type:
- Article
8
Combination of Correctors Rescues CFTR Transmembrane-Domain Mutants by Mitigating their Interactions with Proteostasis.
- Published in:
- Cellular Physiology & Biochemistry (Karger AG), 2017, v. 42, n. 1, p. 2194, doi. 10.1159/000475578
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- Article
9
Combination of Correctors Rescues CFTR Transmembrane-Domain Mutants by Mitigating their Interactions with Proteostasis.
- Published in:
- Cellular Physiology & Biochemistry (Karger AG), 2017, v. 41, n. 6, p. 2193, doi. 10.1159/000475578
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- Publication type:
- Article
10
CFTR Controls the Activity of NF-κB by Enhancing the Degradation of TRADD.
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- Cellular Physiology & Biochemistry (Karger AG), 2016, v. 40, n. 5, p. 1063, doi. 10.1159/000453162
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- Article
11
CFTR Controls the Activity of NF-κB by Enhancing the Degradation of TRADD.
- Published in:
- Cellular Physiology & Biochemistry (Karger AG), 2016, v. 40, n. 3/4, p. 1063, doi. 10.1159/000453162
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- Publication type:
- Article
12
STIM1<sup>fl/fl</sup> Ksp-Cre Mouse has Impaired Renal Water Balance.
- Published in:
- Cellular Physiology & Biochemistry (Karger AG), 2016, v. 39, n. 1, p. 172, doi. 10.1159/000445614
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- Publication type:
- Article
13
Regulation of CFTR Expression and Arginine Vasopressin Activity Are Dependent on Polycystin-1 in Kidney-Derived Cells.
- Published in:
- Cellular Physiology & Biochemistry (Karger AG), 2016, v. 38, n. 1, p. 28, doi. 10.1159/000438606
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- Publication type:
- Article
14
Polycystin-1, 2, and STIM1 Interact with IP<sub>3</sub>R to Modulate ER Ca Release through the PI3K/Akt Pathway.
- Published in:
- Cellular Physiology & Biochemistry (Karger AG), 2011, v. 27, n. 6, p. 715, doi. 10.1159/000330080
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- Publication type:
- Article
15
The Hypertonic Environment Differentially Regulates Wild-type CFTR and TNR-CFTR Chloride Channels.
- Published in:
- Cellular Physiology & Biochemistry (Karger AG), 2010, v. 26, n. 4/5, p. 577, doi. 10.1159/000322325
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- Publication type:
- Article
16
The CFTR Corrector, VX-809 (Lumacaftor), Rescues ABCA4 Trafficking Mutants: a Potential Treatment for Stargardt Disease.
- Published in:
- Cellular Physiology & Biochemistry (Cell Physiol Biochem Press GmbH & Co. KG), 2019, v. 53, n. 2, p. 400, doi. 10.33594/000000146
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- Publication type:
- Article
17
Restoration of F508-del Function by Transcomplementation: The Partners Meet in the Endoplasmic Reticulum.
- Published in:
- Cellular Physiology & Biochemistry (Cell Physiol Biochem Press GmbH & Co. KG), 2019, v. 52, n. 6, p. 1267, doi. 10.33594/000000089
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- Publication type:
- Article
18
Adeno-Associated Virus (AAV) gene therapy for cystic fibrosis: current barriers and recent developments.
- Published in:
- Expert Opinion on Biological Therapy, 2017, v. 17, n. 10, p. 1265, doi. 10.1080/14712598.2017.1347630
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- Publication type:
- Article
19
Transcription Factor MEF2C Suppresses Endothelial Cell Inflammation via Regulation of NF-κB and KLF2.
- Published in:
- Journal of Cellular Physiology, 2015, v. 230, n. 6, p. 1310, doi. 10.1002/jcp.24870
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- Publication type:
- Article
20
Dual Reporter Comparative Indexing of rAAV Pseudotyped Vectors in Chimpanzee Airway.
- Published in:
- Molecular Therapy, 2010, v. 18, n. 3, p. 594, doi. 10.1038/mt.2009.230
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- Publication type:
- Article
21
Expression of a Truncated Cystic Fibrosis Transmembrane Conductance Regulator with an AAV5-pseudotyped Vector in Primates.
- Published in:
- Molecular Therapy, 2007, v. 15, n. 4, p. 756, doi. 10.1038/sj.mt.6300059
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- Publication type:
- Article
22
498. AAV Δ264CFTR Enhances Maturation of ΔF508CFTR and wt CFTR Expression.
- Published in:
- Molecular Therapy, 2006, v. 13, p. S193, doi. 10.1016/j.ymthe.2006.08.568
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- Publication type:
- Article
23
Tubular and cellular localization of the cardiac L-type calcium channel in rat kidney.
- Published in:
- Kidney International, 2002, v. 61, n. 4, p. 1393, doi. 10.1046/j.1523-1755.2002.00267.x
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- Publication type:
- Article
24
Syntaxin 8 and the Endoplasmic Reticulum Processing of ΔF508-CFTR.
- Published in:
- Cellular Physiology & Biochemistry (Karger AG), 2018, v. 51, n. 3, p. 1489, doi. 10.1159/000495596
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- Publication type:
- Article
25
Correctors Rescue CFTR Mutations in Nucleotide-Binding Domain 1 (NBD1) by Modulating Proteostasis.
- Published in:
- ChemBioChem, 2016, v. 17, n. 6, p. 493, doi. 10.1002/cbic.201500620
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- Publication type:
- Article