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Collagen VI Deficiency Impairs Tendon Fibroblasts Mechanoresponse in Ullrich Congenital Muscular Dystrophy.
- Published in:
- Cells (2073-4409), 2024, v. 13, n. 5, p. 378, doi. 10.3390/cells13050378
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- Publication type:
- Article
Collagen VI sustains cell stemness and chemotherapy resistance in glioblastoma.
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- Cellular & Molecular Life Sciences, 2023, v. 80, n. 8, p. 1, doi. 10.1007/s00018-023-04887-5
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- Publication type:
- Article
Collagen VI promotes recovery from colitis by inducing lymphangiogenesis and drainage of inflammatory cells.
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- Journal of Pathology, 2023, v. 260, n. 4, p. 417, doi. 10.1002/path.6092
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- Publication type:
- Article
Zebrafish ambra1b knockout reveals a novel role for Ambra1 in primordial germ cells survival, sex differentiation and reproduction.
- Published in:
- Biological Research, 2023, v. 56, n. 1, p. 1, doi. 10.1186/s40659-023-00430-9
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- Publication type:
- Article
Ambra1 deficiency impairs mitophagy in skeletal muscle.
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- Journal of Cachexia, Sarcopenia & Muscle, 2022, v. 13, n. 4, p. 2211, doi. 10.1002/jcsm.13010
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- Publication type:
- Article
Emilin-2 is a component of bone marrow extracellular matrix regulating mesenchymal stem cell differentiation and hematopoietic progenitors.
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- Stem Cell Research & Therapy, 2022, v. 13, n. 1, p. 1, doi. 10.1186/s13287-021-02674-2
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- Publication type:
- Article
Congenital muscular dystrophy-associated inflammatory chemokines provide axes for effective recruitment of therapeutic adult stem cell into muscles.
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- Stem Cell Research & Therapy, 2020, v. 11, n. 1, p. N.PAG, doi. 10.1186/s13287-020-01979-y
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- Publication type:
- Article
Lipids and glucose homeostasis upon metabolic challenge: extracellular matrix takes the stage.
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- Journal of Physiology, 2020, v. 598, n. 16, p. 3319, doi. 10.1113/JP280226
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- Publication type:
- Article
Spatio-temporal expression and distribution of collagen VI during zebrafish development.
- Published in:
- Scientific Reports, 2019, v. 9, n. 1, p. 1, doi. 10.1038/s41598-019-56445-4
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- Publication type:
- Article
Fra-2-expressing macrophages promote lung fibrosis in mice.
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- 2019
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- Publication type:
- journal article
A novel murine model for arrhythmogenic cardiomyopathy points to a pathogenic role of Wnt signalling and miRNA dysregulation.
- Published in:
- Cardiovascular Research, 2019, v. 115, n. 4, p. 739, doi. 10.1093/cvr/cvy253
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- Publication type:
- Article
Gelatin–genipin‐based biomaterials for skeletal muscle tissue engineering.
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- Journal of Biomedical Materials Research, Part B: Applied Biomaterials, 2018, v. 106, n. 8, p. 2763, doi. 10.1002/jbm.b.34057
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- Publication type:
- Article
Collagen VI is required for the structural and functional integrity of the neuromuscular junction.
- Published in:
- Acta Neuropathologica, 2018, v. 136, n. 3, p. 483, doi. 10.1007/s00401-018-1860-9
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- Publication type:
- Article
Extracellular Collagen VI Has Prosurvival and Autophagy Instructive Properties in Mouse Fibroblasts.
- Published in:
- Frontiers in Physiology, 2018, p. N.PAG, doi. 10.3389/fphys.2018.01129
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- Publication type:
- Article
Collagen VI Null Mice as a Model for Early Onset Muscle Decline in Aging.
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- Frontiers in Molecular Neuroscience, 2017, p. 1, doi. 10.3389/fnmol.2017.00337
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- Publication type:
- Article
CMG2/ANTXR2 regulates extracellular collagen VI which accumulates in hyaline fibromatosis syndrome.
- Published in:
- Nature Communications, 2017, v. 8, n. 6, p. 15861, doi. 10.1038/ncomms15861
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- Publication type:
- Article
EMILIN3, an extracellular matrix molecule with restricted distribution in skin.
- Published in:
- Experimental Dermatology, 2017, v. 26, n. 5, p. 435, doi. 10.1111/exd.13254
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- Publication type:
- Article
Editorial: Muscle-Tendon-Innervation Unit: Degeneration and Aging--Pathophysiological and Regeneration Mechanisms.
- Published in:
- Frontiers in Aging Neuroscience, 2016, v. 7, p. 1, doi. 10.3389/fnagi.2016.00320
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- Publication type:
- Article
Glycolytic-to-oxidative fiber-type switch and mTOR signaling activation are early-onset features of SBMA muscle modified by high-fat diet.
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- Acta Neuropathologica, 2016, v. 132, n. 1, p. 127, doi. 10.1007/s00401-016-1550-4
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- Publication type:
- Article
Role of macrophages in Wallerian degeneration and axonal regeneration after peripheral nerve injury.
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- Acta Neuropathologica, 2015, v. 130, n. 5, p. 605, doi. 10.1007/s00401-015-1482-4
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- Publication type:
- Article
Lack of Collagen VI Promotes Wound-Induced Hair Growth.
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- Journal of Investigative Dermatology, 2015, v. 135, n. 10, p. 2358, doi. 10.1038/jid.2015.187
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- Publication type:
- Article
The notochord: structure and functions.
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- Cellular & Molecular Life Sciences, 2015, v. 72, n. 16, p. 2989, doi. 10.1007/s00018-015-1897-z
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- Publication type:
- Article
Editorial: Pathophysiological mechanisms of sarcopenia in aging and in muscular dystrophy: a translational approach.
- Published in:
- 2015
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- Publication type:
- Editorial
The Role of Collagens in Peripheral Nerve Myelination and Function.
- Published in:
- Molecular Neurobiology, 2015, v. 52, n. 1, p. 216, doi. 10.1007/s12035-014-8862-y
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- Publication type:
- Article
Type VI Collagen Regulates Pericellular Matrix Properties, Chondrocyte Swelling, and Mechanotransduction in Mouse Articular Cartilage.
- Published in:
- Arthritis & Rheumatology, 2015, v. 67, n. 5, p. 1286, doi. 10.1002/art.39034
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- Publication type:
- Article
Collagen VI regulates peripheral nerve regeneration by modulating macrophage recruitment and polarization.
- Published in:
- Acta Neuropathologica, 2015, v. 129, n. 1, p. 97, doi. 10.1007/s00401-014-1369-9
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- Publication type:
- Article
NIM811, a cyclophilin inhibitor without immunosuppressive activity, is beneficial in collagen VI congenital muscular dystrophy models.
- Published in:
- Human Molecular Genetics, 2014, v. 23, n. 20, p. 5353, doi. 10.1093/hmg/ddu254
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- Publication type:
- Article
Cyclosporin A promotes in vivo myogenic response in collagen VI-deficient myopathic mice.
- Published in:
- Frontiers in Aging Neuroscience, 2014, v. 6, p. 1, doi. 10.3389/fnagi.2014.00244
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- Publication type:
- Article
Aggresome–autophagy involvement in a sarcopenic patient with rigid spine syndrome and a p.C150R mutation in FHL1 gene.
- Published in:
- Frontiers in Aging Neuroscience, 2014, v. 6, p. 1, doi. 10.3389/fnagi.2014.00215
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- Publication type:
- Article
<i>Col6a1</i> Null Mice as a Model to Study Skin Phenotypes in Patients with Collagen VI Related Myopathies: Expression of Classical and Novel Collagen VI Variants during Wound Healing.
- Published in:
- PLoS ONE, 2014, v. 9, n. 8, p. 1, doi. 10.1371/journal.pone.0105686
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- Publication type:
- Article
Zebrafish <i>ambra1a</i> and <i>ambra1b</i> Knockdown Impairs Skeletal Muscle Development.
- Published in:
- PLoS ONE, 2014, v. 9, n. 6, p. 1, doi. 10.1371/journal.pone.0099210
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- Publication type:
- Article
Characterization of the mitochondrial function and genetics in the pathogenesis of collagen VI related disorders (958.1).
- Published in:
- FASEB Journal, 2014, v. 28, p. N.PAG, doi. 10.1096/fasebj.28.1_supplement.958.1
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- Publication type:
- Article
EMILIN2 down-modulates the Wnt signalling pathway and suppresses breast cancer cell growth and migration.
- Published in:
- Journal of Pathology, 2014, v. 232, n. 4, p. 391, doi. 10.1002/path.4316
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- Publication type:
- Article
Skeletal muscle, autophagy, and physical activity: the ménage à trois of metabolic regulation in health and disease.
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- Journal of Molecular Medicine, 2014, v. 92, n. 2, p. 127, doi. 10.1007/s00109-013-1096-z
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- Publication type:
- Article
Human adipose-derived stem cell transplantation as a potential therapy for collagen VI-related congenital muscular dystrophy.
- Published in:
- Stem Cell Research & Therapy, 2014, v. 5, n. 1, p. 21, doi. 10.1186/scrt411
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- Publication type:
- Article
Characterization of a rare case of Ullrich congenital muscular dystrophy due to truncating mutations within the COL6A1 gene C-Terminal domain: a case report.
- Published in:
- BMC Medical Genetics, 2013, v. 14, n. 1, p. 1, doi. 10.1186/1471-2350-14-59
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- Publication type:
- Article
Collagen VI regulates satellite cell self-renewal and muscle regeneration.
- Published in:
- Nature Communications, 2013, v. 4, n. 6, p. 1964, doi. 10.1038/ncomms2964
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- Publication type:
- Article
Changes in Muscle Cell Metabolism and Mechanotransduction Are Associated with Myopathic Phenotype in a Mouse Model of Collagen VI Deficiency.
- Published in:
- PLoS ONE, 2013, v. 8, n. 2, p. 1, doi. 10.1371/journal.pone.0056716
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- Publication type:
- Article
Biodistribution and Molecular Studies on Orally Administered Nanoparticle-AON Complexes Encapsulated with Alginate Aiming at Inducing Dystrophin Rescue in mdx Mice.
- Published in:
- BioMed Research International, 2013, v. 2013, p. 1, doi. 10.1155/2013/527418
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- Publication type:
- Article
Biodistribution and Molecular Studies on Orally Administered Nanoparticle-AON Complexes Encapsulated with Alginate Aiming at Inducing Dystrophin Rescue in mdx Mice.
- Published in:
- 2013
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- Publication type:
- Journal Article
Autophagy is Impaired in the Tibialis Anterior of Dystrophin Null Mice.
- Published in:
- PLoS Currents, 2013, p. 128, doi. 10.1371/currents.md.e1226cefa851a2f079bbc406c0a21e80
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- Publication type:
- Article
Autophagy in Skeletal Muscle Homeostasis and in Muscular Dystrophies.
- Published in:
- Cells (2073-4409), 2012, v. 1, n. 3, p. 325, doi. 10.3390/cells1030325
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- Publication type:
- Article
Altered Trabecular Bone Structure and Delayed Cartilage Degeneration in the Knees of Collagen VI Null Mice.
- Published in:
- PLoS ONE, 2012, v. 7, n. 3, p. 1, doi. 10.1371/journal.pone.0033397
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- Publication type:
- Article
Persistent Dystrophin Protein Restoration 90 Days after a Course of Intraperitoneally Administered Naked 2′ OMePS AON and ZM2 NP-AON Complexes in mdx Mice.
- Published in:
- Journal of Biomedicine & Biotechnology, 2012, v. 2012, p. 1, doi. 10.1155/2012/897076
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- Publication type:
- Article
Persistent Dystrophin Protein Restoration 90 Days after a Course of Intraperitoneally Administered Naked 2′ OMePS AON and ZM2 NP-AON Complexes in mdx Mice.
- Published in:
- 2012
- By:
- Publication type:
- Journal Article
Expression of the Collagen VI α5 and α6 Chains in Normal Human Skin and in Skin of Patients with Collagen VI-Related Myopathies.
- Published in:
- Journal of Investigative Dermatology, 2011, v. 131, n. 1, p. 99, doi. 10.1038/jid.2010.284
- By:
- Publication type:
- Article
Cyclosporine A in Ullrich Congenital Muscular Dystrophy: Long-Term Results.
- Published in:
- Oxidative Medicine & Cellular Longevity, 2011, v. 2011, p. 1, doi. 10.1155/2011/139194
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- Publication type:
- Article
Oxidative stress by monoamine oxidases is causally involved in myofiber damage in muscular dystrophy.
- Published in:
- Human Molecular Genetics, 2010, v. 19, n. 21, p. 4207, doi. 10.1093/hmg/ddq339
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- Publication type:
- Article
Autophagy is defective in collagen VI muscular dystrophies, and its reactivation rescues myofiber degeneration.
- Published in:
- Nature Medicine, 2010, v. 16, n. 11, p. 1313, doi. 10.1038/nm.2247
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- Publication type:
- Article
Identification of a deep intronic mutation in the COL6A2 gene by a novel custom oligonucleotide CGH array designed to explore allelic and genetic heterogeneity in collagen VI-related myopathies.
- Published in:
- BMC Medical Genetics, 2010, v. 11, p. 44, doi. 10.1186/1471-2350-11-44
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- Publication type:
- Article