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- Title
Systemic amyloidosis AL with temporal artery involvement revealing lymphoplasmacytic malignancy in a man presenting as polymyalgia rheumatica.
- Authors
Lafforgue, P; Senbel, E; Figarella-Branger, D; Boucraut, J; Horschowsky, N; Pellissier, J F; Acquaviva, P C
- Abstract
A 68 year old man presented with a clinical and biological picture that suggested polymyalgia rheumatica. Temporal artery biopsy disclosed no inflammatory change but massive light chain amyloid deposits in the media. Further exploration showed a malignant lymphoplasmacytic haemopathy with a triclonal gammopathy and a muscular, rectal, and probable cardiac amyloidosis. Cryoglobulinaemia and high concentrations of soluble interleukin 2 receptor (sIL-2R) were also found. This is the fifth case with confirmed involvement of the temporal artery. The especially high sIL-2R concentration was thought to reflect the tumour mass rather than lymphocyte activation.
- Publication
Annals of the rheumatic diseases, 1993, Vol 52, Issue 2, p158
- ISSN
0003-4967
- Publication type
Journal Article
- DOI
10.1136/ard.52.2.158