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- Title
Familial opsonization defect associated with fatal infantile dermatitis, infections, and histiocytosis.
- Authors
Scott, H; Moynahan, E J; Risdon, R A; Harvey, B A; Soothill, J F
- Abstract
Members of four generations of a family had a defect of serum opsonization for yeast phagocytosis consistent with dominant inheritance. 2 were healthy, one had chronic osteomyelitis, and the fourth developed a fatal illness in infancy characterized by exfoliative dermatitis, diarrhoea, multiple bacterial infections, and failure to thrive, which resembled the two prevously reported cases with this opsonization defect. At necropsy the infant also had lymphoid depletion, which was possibly secondary, and massive histiocytic infiltration.
- Publication
Archives of disease in childhood, 1975, Vol 50, Issue 4, p311
- ISSN
1468-2044
- Publication type
Journal Article
- DOI
10.1136/adc.50.4.311