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Title
Survival probability in ataxia telangiectasia.
Authors
Crawford, T O; Skolasky, R L; Fernandez, R; Rosquist, K J; Lederman, H M
Abstract
Ataxia telangiectasia is a rare, multiorgan neurodegenerative disorder with enhanced vulnerability to cancer and infection. Median survival in two large cohorts of patients with this disease, one prospective and one retrospective, is 25 and 19 years, with a wide range. Life expectancy does not correlate well with severity of neurological impairment.
Publication
Archives of disease in childhood, 2006, Vol 91, Issue 7, p610