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- Title
Risk factors for early death in children with haemophagocytic lymphohistiocytosis.
- Authors
Trottestam, Helena; Berglöf, Elisabet; Horne, AnnaCarin; Onelöv, Erik; Beutel, Karin; Lehmberg, Kai; Sieni, Elena; Silfverberg, Thomas; Aricò, Maurizio; Janka, Gritta; Henter, Jan-Inge
- Abstract
Haemophagocytic lymphohistiocytosis (HLH) is a life-threatening disturbance of immunoregulation. HLH comprises primary and acquired forms with different disease severity. A large proportion of deaths occur early into treatment. We investigated association with early death for laboratory and clinical parameters before the start of and 2 weeks into therapy.
- Publication
Acta paediatrica (Oslo, Norway : 1992), 2012, Vol 101, Issue 3, p313
- ISSN
1651-2227
- Publication type
Journal Article
- DOI
10.1111/j.1651-2227.2011.02501.x