Works matching AU Wegner, Florian


Results: 105
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    Phenotypes and malignancy risk of different FUS mutations in genetic amyotrophic lateral sclerosis.

    Published in:
    Annals of Clinical & Translational Neurology, 2019, v. 6, n. 12, p. 2384, doi. 10.1002/acn3.50930
    By:
    • Naumann, Marcel;
    • Peikert, Kevin;
    • Günther, Rene;
    • Kooi, Anneke J.;
    • Aronica, Eleonora;
    • Hübers, Annemarie;
    • Danel, Veronique;
    • Corcia, Philippe;
    • Pan‐Montojo, Francisco;
    • Cirak, Sebahattin;
    • Haliloglu, Göknur;
    • Ludolph, Albert C.;
    • Goswami, Anand;
    • Andersen, Peter M.;
    • Prudlo, Johannes;
    • Wegner, Florian;
    • Van Damme, Philip;
    • Weishaupt, Jochen H.;
    • Hermann, Andreas
    Publication type:
    Article
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    Evaluation of Cognitive Deficits and Structural Hippocampal Damage in Encephalitis With Leucine-Rich, Glioma-Inactivated 1 Antibodies.

    Published in:
    JAMA Neurology, 2017, v. 74, n. 1, p. 50, doi. 10.1001/jamaneurol.2016.4226
    By:
    • Finke, Carsten;
    • Prüss, Harald;
    • Heine, Josephine;
    • Reuter, Sigrid;
    • Kopp, Ute A.;
    • Wegner, Florian;
    • Then Bergh, Florian;
    • Koch, Sebastian;
    • Jansen, Olav;
    • Münte, Thomas;
    • Deuschl, Günther;
    • Ruprecht, Klemens;
    • Stöcker, Winfried;
    • Wandinger, Klaus-Peter;
    • Paul, Friedemann;
    • Bartsch, Thorsten
    Publication type:
    Article
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    Intraspinal administration of human spinal cord-derived neural progenitor cells in the G93A-SOD1 mouse model of ALS delays symptom progression, prolongs survival and increases expression of endogenous neurotrophic factors.

    Published in:
    Journal of Tissue Engineering & Regenerative Medicine, 2017, v. 11, n. 3, p. 751, doi. 10.1002/term.1972
    By:
    • Knippenberg, Sarah;
    • Rath, Klaus Jan;
    • Böselt, Sebastian;
    • Thau‐Habermann, Nadine;
    • Schwarz, Sigrid C.;
    • Dengler, Reinhard;
    • Wegner, Florian;
    • Petri, Susanne
    Publication type:
    Article
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    Altered calcium dynamics and glutamate receptor properties in iPSC-derived motor neurons from ALS patients with C9orf72, FUS, SOD1 or TDP43 mutations.

    Published in:
    Human Molecular Genetics, 2019, v. 28, n. 17, p. 2835, doi. 10.1093/hmg/ddz107
    By:
    • Bursch, Franziska;
    • Kalmbach, Norman;
    • Naujock, Maximilian;
    • Staege, Selma;
    • Eggenschwiler, Reto;
    • Abo-Rady, Masin;
    • Japtok, Julia;
    • Guo, Wenting;
    • Hensel, Niko;
    • Reinhardt, Peter;
    • Boeckers, Tobias M;
    • Cantz, Tobias;
    • Sterneckert, Jared;
    • Bosch, Ludo Van Den;
    • Hermann, Andreas;
    • Petri, Susanne;
    • Wegner, Florian
    Publication type:
    Article
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    Corrigendum: SLP-2 interacts with Parkin in mitochondria and prevents mitochondrial dysfunction in Parkin-deficient human iPSC-derived neurons and Drosophila.

    Published in:
    Human Molecular Genetics, 2019, v. 28, n. 7, p. 1225, doi. 10.1093/hmg/ddy408
    By:
    • Zanon, Alessandra;
    • Kalvakuri, Sreehari;
    • Rakovic, Aleksandar;
    • Foco, Luisa;
    • Guida, Marianna;
    • Schwienbacher, Christine;
    • Serafin, Alice;
    • Rudolph, Franziska;
    • Trilck, Michaela;
    • Grünewald, Anne;
    • Stanslowsky, Nancy;
    • Wegner, Florian;
    • Giorgio, Valentina;
    • Lavdas, Alexandros A;
    • Bodmer, Rolf;
    • Pramstaller, Peter P;
    • Klein, Christine;
    • Hicks, Andrew A;
    • Pichler, Irene;
    • Philip, Seibler
    Publication type:
    Article
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    SLP-2 interacts with Parkin in mitochondria and prevents mitochondrial dysfunction in Parkin-deficient human iPSC-derived neurons and Drosophila.

    Published in:
    Human Molecular Genetics, 2017, v. 26, n. 13, p. 2412, doi. 10.1093/hmg/ddx132
    By:
    • Zanon, Alessandra;
    • Kalvakuri, Sreehari;
    • Rakovic, Aleksandar;
    • Foco, Luisa;
    • Guida, Marianna;
    • Schwienbacher, Christine;
    • Serafin, Alice;
    • Rudolph, Franziska;
    • Trilck, Michaela;
    • Grünewald, Anne;
    • Stanslowsky, Nancy;
    • Wegner, Florian;
    • Giorgio, Valentina;
    • Lavdas, Alexandros A.;
    • Bodmer, Rolf;
    • Pramstaller, Peter P.;
    • Klein, Christine;
    • Hicks, Andrew A.;
    • Pichler, Irene;
    • Seibler, Philip
    Publication type:
    Article
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    Neuronal Dysfunction in iPSC-Derived Medium Spiny Neurons from Chorea-Acanthocytosis Patients Is Reversed by Src Kinase Inhibition and F-Actin Stabilization.

    Published in:
    Journal of Neuroscience, 2016, v. 36, n. 47, p. 12027, doi. 10.1523/JNEUROSCI.0456-16.2016
    By:
    • Stanslowsky, Nancy;
    • Reinhardt, Peter;
    • Glass, Hannes;
    • Kalmbach, Norman;
    • Naujock, Maximilian;
    • Hensel, Niko;
    • Lübben, Verena;
    • Pal, Arun;
    • Venneri, Anna;
    • Lupo, Francesca;
    • De Franceschi, Lucia;
    • Claus, Peter;
    • Sterneckert, Jared;
    • Storch, Alexander;
    • Hermann, Andreas;
    • Wegner, Florian
    Publication type:
    Article
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    Cerebrospinal fluid JC virus antibody index for diagnosis of natalizumab-associated progressive multifocal leukoencephalopathy.

    Published in:
    Annals of Neurology, 2014, v. 76, n. 6, p. 792, doi. 10.1002/ana.24153
    By:
    • Warnke, Clemens;
    • Geldern, Gloria;
    • Markwerth, Philipp;
    • Dehmel, Thomas;
    • Hoepner, Robert;
    • Gold, Ralf;
    • Pawlita, Michael;
    • Kümpfel, Tania;
    • Mäurer, Mathias;
    • Stangel, Martin;
    • Wegner, Florian;
    • Hohlfeld, Reinhard;
    • Straeten, Vera;
    • Limmroth, Volker;
    • Weber, Thomas;
    • Hermsen, Derik;
    • Kleinschnitz, Christoph;
    • Hartung, Hans‐Peter;
    • Wattjes, Mike P.;
    • Svenningson, Anders
    Publication type:
    Article
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    Anti-leucine rich glioma inactivated 1 protein and anti-N-methyl-D-aspartate receptor encephalitis show distinct patterns of brain glucose metabolism in <sup>18</sup>F-fluoro-2-deoxy-d-glucose positron emission tomography.

    Published in:
    BMC Neurology, 2014, v. 14, n. 1, p. 1, doi. 10.1186/1471-2377-14-136
    By:
    • Wegner, Florian;
    • Wilke, Florian;
    • Raab, Peter;
    • Tayeb, Said Ben;
    • Boeck, Anna-Lena;
    • Haense, Cathleen;
    • Trebst, Corinna;
    • Voss, Elke;
    • Schrader, Christoph;
    • Logemann, Frank;
    • Ahrens, Jörg;
    • Leffler, Andreas;
    • Rodriguez-Raecke, Rea;
    • Dengler, Reinhard;
    • Geworski, Lilli;
    • Bengel, Frank M.;
    • Berding, Georg;
    • Stangel, Martin;
    • Nabavi, Elham
    Publication type:
    Article
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    Improved bi-allelic modification of a transcriptionally silent locus in patient-derived iPSC by Cas9 nickase.

    Published in:
    Scientific Reports, 2016, p. 38198, doi. 10.1038/srep38198
    By:
    • Eggenschwiler, Reto;
    • Moslem, Mohsen;
    • Fráguas, Mariane Serra;
    • Galla, Melanie;
    • Papp, Oliver;
    • Naujock, Maximilian;
    • Fonfara, Ines;
    • Gensch, Ingrid;
    • Wähner, Annabell;
    • Beh-Pajooh, Abbas;
    • Mussolino, Claudio;
    • Tauscher, Marcel;
    • Steinemann, Doris;
    • Wegner, Florian;
    • Petri, Susanne;
    • Schambach, Axel;
    • Charpentier, Emmanuelle;
    • Cathomen, Toni;
    • Cantz, Tobias
    Publication type:
    Article
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