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- Title
Neurosurgical management of occult spinal dysraphism associated with OEIS complex.
- Authors
Takato Morioka; Kimiaki Hashiguchi; Fumiaki Yoshida; Kenichi Matsumoto; Shinji Nagata; Takashi Yoshiura; Kouji Masumoto; Tomoaki Taguchi; Tomio Sasaki
- Abstract
Abstract Introduction OEIS complex has been described as a combination of defects consisting of omphalocele (O), exstrophy of the cloaca (E), imperforate anus (I), and spinal defects (S). As the first three defects are life-threatening and treated on a priority basis, neurosurgical intervention for spinal defects is deferred until recuperation from abdominogenital repair. However, the best timing for neurosurgical operation has not been precisely described. Materials and methods We reviewed our neurosurgical management of three cases (case 1: myelomeningocele; cases 2 and 3: terminal myelocystocele). At 2–6 (3.6 on average) months after birth, neurosurgical procedures, including reduction of the size of the lumbosacral cystic lesion and untethering of the spinal cord, were performed. Results During this period, the patients’ weights increased from 1,911 to 3,368 g on average, and the lumbosacral cystic lesion was markedly enlarged. In all cases, no neurological deterioration was seen, and ventriculoperitoneal shunt was not indicated. Conclusion Thus, neurosurgical procedures can be performed in patients weighing 3–4 kg and/or at an age of 3 months, after confirming recuperated conditions from abdominogenital repair. Careful observation should be made of the size of the lumbosacral cystic lesion and neurological deterioration.
- Publication
Child's Nervous System, 2008, Vol 24, Issue 6, p723
- ISSN
0256-7040
- Publication type
Academic Journal
- DOI
10.1007/s00381-007-0519-y