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- Title
Lower cancer incidence in Amsterdam-I criteria families without mismatch repair deficiency: familial colorectal cancer type X.
- Authors
Lindor, Noralane M; Rabe, Kari; Petersen, Gloria M; Haile, Robert; Casey, Graham; Baron, John; Gallinger, Steve; Bapat, Bharati; Aronson, Melyssa; Hopper, John; Jass, Jeremy; LeMarchand, Loic; Grove, John; Potter, John; Newcomb, Polly; Terdiman, Jonathan P; Conrad, Peggy; Moslein, Gabriella; Goldberg, Richard; Ziogas, Argyrios; Anton-Culver, Hoda; de Andrade, Mariza; Siegmund, Kim; Thibodeau, Stephen N; Boardman, Lisa A; Seminara, Daniela
- Abstract
Approximately 60% of families that meet the Amsterdam-I criteria (AC-I) for hereditary nonpolyposis colorectal cancer (HNPCC) have a hereditary abnormality in a DNA mismatch repair (MMR) gene. Cancer incidence in AC-I families with MMR gene mutations is reported to be very high, but cancer incidence for individuals in AC-I families with no evidence of an MMR defect is unknown.
- Publication
JAMA, 2005, Vol 293, Issue 16, p1979
- ISSN
1538-3598
- Publication type
Journal Article
- DOI
10.1001/jama.293.16.1979