Histopathological findings confirmed the diagnosis of porokeratotic adnexal ostial nevus or porokeratotic eccrine ostial and dermal duct nevus. It has been proposed that single GJB2 somatic mutation could cause porokeratotic eccrine ostial and dermal duct nevus.[[4]] KID syndrome could be a more generalized form of porokeratotic eccrine ostial and dermal duct nevus. Widespread porokeratotic adnexal ostial nevus: clinical features and proposal of a new name unifying porokeratotic eccrine ostial and dermal duct nevus and porokeratotic eccrine and hair follicle nevus.