Works matching Prion diseases

Results: 4235

A CONTRIBUIÇÃO GENÉTICA NO DESENVOLVIMENTO DE DOENÇAS PRIÔNICAS: REVISÃO SISTEMÁTICA.

Published in:

Revista Foco (Interdisciplinary Studies Journal), 2023, v. 16, n. 6, p. 1, doi. 10.54751/revistafoco.v16n6-096

By:

Bitu de Freitas, Yuri Borges;
Ribeiro Pimentel, Ana Luiza Machado;
Albuquerque Amorim Ayres, Celina Kalena;
Siqueira Bocchi, Giovanna;
Costa Diniz, Henrique;
Rezende Albernaz, Vítor;
Veloso Correia, Davi;
Costa Alves, Bruna

Publication type:

Article

Lidské prionové nemoci v ČR: 22 let zkušeností Národní referenční laboratoře pro diagnostiku lidských prionových chorob.

Published in:

Neurologie Pro Praxi, 2024, v. 25, n. 1, p. 9, doi. 10.36290/neu.2024.002

By:

Jankovská, Nikol;
Matěj, Radoslav

Publication type:

Article

Humánne priónové ochorenia - „state of the art" 2023.

Published in:

Neurologie Pro Praxi, 2024, v. 25, n. 1, p. 19, doi. 10.36290/neu.2024.005

By:

Kurča, Egon;
Sivák, Štefan;
Skáčik, Pavol

Publication type:

Article

Distinct Transmissibility Features of TSE Sources Derived from Ruminant Prion Diseases by the Oral Route in a Transgenic Mouse Model (TgOvPrP4) Overexpressing the Ovine Prion Protein.

Published in:

PLoS ONE, 2014, v. 9, n. 5, p. 1, doi. 10.1371/journal.pone.0096215

By:

Arsac, Jean-Noël;
Baron, Thierry

Publication type:

Article

Seeded Fibrillation as Molecular Basis of the Species Barrier in Human Prion Diseases.

Published in:

PLoS ONE, 2013, v. 8, n. 8, p. 1, doi. 10.1371/journal.pone.0072623

By:

Luers, Lars;
Bannach, Oliver;
Stöhr, Jan;
Wördehoff, Michael Marius;
Wolff, Martin;
Nagel-Steger, Luitgard;
Riesner, Detlev;
Willbold, Dieter;
Birkmann, Eva

Publication type:

Article

MicroRNA Alterations in the Brain and Body Fluids of Humans and Animal Prion Disease Models: Current Status and Perspectives.

Published in:

Frontiers in Aging Neuroscience, 2018, p. N.PAG, doi. 10.3389/fnagi.2018.00220

By:

Kanata, Eirini;
Thüne, Katrin;
Xanthopoulos, Konstantinos;
Ferrer, Isidre;
Dafou, Dimitra;
Zerr, Inga;
Sklaviadis, Theodoros;
Llorens, Franc

Publication type:

Article

Increased Abundance of M Cells in the Gut Epithelium Dramatically Enhances Oral Prion Disease Susceptibility.

Published in:

PLoS Pathogens, 2016, v. 12, n. 12, p. 1, doi. 10.1371/journal.ppat.1006075

By:

Donaldson, David S.;
Sehgal, Anuj;
Rios, Daniel;
Williams, Ifor R.;
Mabbott, Neil A.

Publication type:

Article

A Single Subcutaneous Injection of Cellulose Ethers Administered Long before Infection Confers Sustained Protection against Prion Diseases in Rodents.

Published in:

PLoS Pathogens, 2016, v. 12, n. 12, p. 1, doi. 10.1371/journal.ppat.1006045

By:

Teruya, Kenta;
Oguma, Ayumi;
Nishizawa, Keiko;
Kawata, Maki;
Sakasegawa, Yuji;
Kamitakahara, Hiroshi;
Doh-ura, Katsumi

Publication type:

Article

Toll-like receptor 2 confers partial neuroprotection during prion disease.

Published in:

PLoS ONE, 2018, v. 13, n. 12, p. 1, doi. 10.1371/journal.pone.0208559

By:

Carroll, James A.;
Race, Brent;
Williams, Katie;
Chesebro, Bruce

Publication type:

Article

Mineral licks as environmental reservoirs of chronic wasting disease prions.

Published in:

PLoS ONE, 2018, v. 13, n. 5, p. 1, doi. 10.1371/journal.pone.0196745

By:

Plummer, Ian H.;
Johnson, Chad J.;
Chesney, Alexandra R.;
Pedersen, Joel A.;
Samuel, Michael D.

Publication type:

Article

Clinical Use of Improved Diagnostic Testing for Detection of Prion Disease.

Published in:

Viruses (1999-4915), 2021, v. 13, n. 5, p. 789, doi. 10.3390/v13050789

By:

Figgie Jr., Mark P.;
Appleby, Brian S.;
Caughey, Byron

Publication type:

Article

Early and Non-Invasive Detection of Chronic Wasting Disease Prions in Elk Feces by Real-Time Quaking Induced Conversion.

Published in:

PLoS ONE, 2016, v. 11, n. 11, p. 1, doi. 10.1371/journal.pone.0166187

By:

Cheng, Yo Ching;
Hannaoui, Samia;
John, Theodore R.;
Dudas, Sandor;
Czub, Stefanie;
Gilch, Sabine

Publication type:

Article

Epigenetic Changes in Prion and Prion-like Neurodegenerative Diseases: Recent Advances, Potential as Biomarkers, and Future Perspectives.

Published in:

2022

By:

Hernaiz, Adelaida;
Toivonen, Janne Markus;
Bolea, Rosa;
Martín-Burriel, Inmaculada

Publication type:

Literature Review

Gene expression and epigenetic markers of prion diseases.

Published in:

Cell & Tissue Research, 2023, v. 392, n. 1, p. 285, doi. 10.1007/s00441-022-03603-2

By:

Viré, Emmanuelle A.;
Mead, Simon

Publication type:

Article

Therapeutic strategies for identifying small molecules against prion diseases.

Published in:

Cell & Tissue Research, 2023, v. 392, n. 1, p. 337, doi. 10.1007/s00441-021-03573-x

By:

Uliassi, Elisa;
Nikolic, Lea;
Bolognesi, Maria Laura;
Legname, Giuseppe

Publication type:

Article

Cell adhesion molecule CD44 is dispensable for reactive astrocyte activation during prion disease.

Published in:

Scientific Reports, 2024, v. 14, n. 1, p. 1, doi. 10.1038/s41598-024-63464-3

By:

Bradford, Barry M.;
Walmsley-Rowe, Lauryn;
Reynolds, Joe;
Verity, Nicholas;
Mabbott, Neil A.

Publication type:

Article

Unraveling the key to the resistance of canids to prion diseases.

Published in:

PLoS Pathogens, 2017, v. 13, n. 11, p. 1, doi. 10.1371/journal.ppat.1006716

By:

Fernández-Borges, Natalia;
Parra, Beatriz;
Vidal, Enric;
Eraña, Hasier;
Sánchez-Martín, Manuel A.;
de Castro, Jorge;
Elezgarai, Saioa R.;
Pumarola, Martí;
Mayoral, Tomás;
Castilla, Joaquín

Publication type:

Article

Dysregulation of neuroprotective astrocytes, a spectrum of microglial activation states, and altered hippocampal neurogenesis are revealed by single-cell RNA sequencing in prion disease.

Published in:

Acta Neuropathologica Communications, 2022, v. 10, n. 1, p. 1, doi. 10.1186/s40478-022-01450-4

By:

Slota, Jessy A.;
Sajesh, Babu V.;
Frost, Kathy F.;
Medina, Sarah J.;
Booth, Stephanie A.

Publication type:

Article

The degree of astrocyte activation is predictive of the incubation time to prion disease.

Published in:

Acta Neuropathologica Communications, 2021, v. 9, n. 1, p. 1, doi. 10.1186/s40478-021-01192-9

By:

Makarava, Natallia;
Mychko, Olga;
Chang, Jennifer Chen-Yu;
Molesworth, Kara;
Baskakov, Ilia V.

Publication type:

Article

Epidemiological characteristics of human prion diseases.

Published in:

Infectious Diseases of Poverty, 2016, v. 5, p. 1, doi. 10.1186/s40249-016-0143-8

By:

Cao Chen;
Xiao-Ping Dong

Publication type:

Article

Insight From Animals Resistant to Prion Diseases: Deciphering the Genotype – Morphotype – Phenotype Code for the Prion Protein.

Published in:

Frontiers in Cellular Neuroscience, 2020, v. 14, p. N.PAG, doi. 10.3389/fncel.2020.00254

By:

Myers, Ryan;
Cembran, Alessandro;
Fernandez-Funez, Pedro

Publication type:

Article

Detection limitations of prion seeding activities in blood samples from patients with sporadic prion disease.

Published in:

BMC Neurology, 2024, v. 24, n. 1, p. 1, doi. 10.1186/s12883-024-03590-7

By:

Nonaka, Toshiaki;
Iwasaki, Yasushi;
Horiuchi, Hiroyuki;
Satoh, Katsuya

Publication type:

Article

Common therapeutic strategies for prion and Alzheimer's diseases.

Published in:

Biological Chemistry, 2016, v. 397, n. 11, p. 1115, doi. 10.1515/hsz-2016-0190

By:

Elezgarai, Saioa R.;
Biasini, Emiliano

Publication type:

Article

Clinically Unsuspected Prion Disease Among Patients With Dementia Diagnoses in an Alzheimer’s Disease Database.

Published in:

American Journal of Alzheimer's Disease & Other Dementias, 2015, v. 30, n. 8, p. 752, doi. 10.1177/1533317515602218

By:

Maddox, Ryan A.;
Blase, J. L.;
Mercaldo, N. D.;
Harvey, A. R.;
Schonberger, L. B.;
Kukull, W. A.;
Belay, E. D.

Publication type:

Article

A Preliminary Study for the Determination of Prion Disease for Farm Animals in Ethiopia.

Published in:

Journal of Animal Production / Hayvansal Üretim, 2020, v. 61, n. 1, p. 17, doi. 10.29185/hayuretim.583573

By:

TEFERDEGN, Eden Yitna;
ÜN, Cemal;
TAŞKIN, Turğay

Publication type:

Article

Cryptic Peptides of the Kringle Domains Preferentially Bind to Disease-Associated Prion Protein.

Published in:

Journal of Alzheimer's Disease, 2009, v. 16, n. 2, p. 421, doi. 10.3233/JAD-2009-0980

By:

Hatcher, Kristen;
Zheng, Jian;
Chen, Shu G.

Publication type:

Article

Mice deficient in p52/NF-κB as a model for studying prion disease.

Published in:

Translational Neuroscience, 2012, v. 3, n. 2, p. 167, doi. 10.2478/s13380-012-0014-0

By:

Poljak, Ljiljana

Publication type:

Article

Incidence of and Mortality Due to Human Prion Diseases in Taiwan: A Prospective 20-Year Nationwide Surveillance Study from 1998 to 2017.

Published in:

Clinical Epidemiology, 2020, v. 12, p. 1073, doi. 10.2147/CLEP.S274093

By:

Sun, Yu;
Liu, Chih-Ching;
Fan, Ling-Yun;
Huang, Chung-Te;
Chen, Ta-Fu;
Lu, Chien-Jung;
Guo, Wan-Yuo;
Chang, Yang-Chyuan;
Chiu, Ming-Jang

Publication type:

Article

Enfermedades priónicas: historia, diversidad e importancia socioeconómica como paradigma de las Enfermedades Raras.

Published in:

Araucaria, 2021, v. 23, n. 46, p. 429, doi. 10.12795/araucaria.2021.i46.21

By:

Charco, Jorge M.;
Barrio, Tomás;
Eraña, Hasier

Publication type:

Article

In Vivo Longitudinal H MRS Study of Transgenic Mouse Models of Prion Disease in the Hippocampus and Cerebellum at 14.1 T.

Published in:

Neurochemical Research, 2015, v. 40, n. 12, p. 2639, doi. 10.1007/s11064-015-1643-9

By:

Cudalbu, Cristina;
Craveiro, Melanie;
Mlynárik, Vladimir;
Bremer, Juliane;
Aguzzi, Adriano;
Gruetter, Rolf

Publication type:

Article

Inherited prion disease with 4-octapeptide repeat insertion: disease requires the interaction of multiple genetic risk factors.

Published in:

Brain: A Journal of Neurology, 2011, v. 134, n. 6, p. 1829, doi. 10.1093/brain/awr079

By:

Kaski, Diego N.;
Pennington, Catherine;
Beck, Jon;
Poulter, Mark;
Uphill, James;
Bishop, Matthew T.;
Linehan, Jaqueline M.;
O’Malley, Catherine;
Wadsworth, Jonathan D. F.;
Joiner, Susan;
Knight, Richard S. G.;
Ironside, James W.;
Brandner, Sebastian;
Collinge, John;
Mead, Simon

Publication type:

Article

Agent strain variation in human prion disease: insights from a molecular and pathological review of the National Institutes of Health series of experimentally transmitted disease.

Published in:

Brain: A Journal of Neurology, 2010, v. 133, n. 10, p. 3030, doi. 10.1093/brain/awq234

By:

Parchi, Piero;
Cescatti, Maura;
Notari, Silvio;
Schulz-Schaeffer, Walter J.;
Capellari, Sabina;
Giese, Armin;
Wen-Quan Zou;
Kretzschmar, Hans;
Ghetti, Bernardino;
Brown, Paul

Publication type:

Article

Prospective 10-year surveillance of human prion diseases in Japan.

Published in:

Brain: A Journal of Neurology, 2010, v. 133, n. 10, p. 3043, doi. 10.1093/brain/awq216

By:

Nozaki, Ichiro;
Hamaguchi, Tsuyoshi;
Sanjo, Nobuo;
Noguchi-Shinohara, Moeko;
Sakai, Kenji;
Nakamura, Yosikazu;
Sato, Takeshi;
Kitamoto, Tetsuyuki;
Mizusawa, Hidehiro;
Moriwaka, Fumio;
Shiga, Yusei;
Kuroiwa, Yoshiyuki;
Nishizawa, Masatoyo;
Kuzuhara, Shigeki;
Inuzuka, Takashi;
Takeda, Masatoshi;
Kuroda, Shigetoshi;
Abe, Koji;
Murai, Hiroyuki;
Murayama, Shigeo

Publication type:

Article

Magnetic resonance diagnostic markers in clinically sporadic prion disease: a combined brain magnetic resonance imaging and spectroscopy study.

Published in:

Brain: A Journal of Neurology, 2009, v. 132, n. 10, p. 2669, doi. 10.1093/brain/awp210

By:

Lodi, Raffaele;
Parchi, Piero;
Tonon, Caterina;
Manners, David;
Capellari, Sabina;
Strammiello, Rosaria;
Rinaldi, Rita;
Testa, Claudia;
Malucelli, Emil;
Mostacci, Barbara;
Rizzo, Giovanni;
Pierangeli, Giulia;
Cortelli, Pietro;
Montagna, Pasquale;
Barbiroli, Bruno

Publication type:

Article

The Evolution of Experimental Rodent Models for Prion Diseases.

Published in:

Journal of Neurochemistry, 2025, v. 169, n. 3, p. 1, doi. 10.1111/jnc.70039

By:

DeFranco, Joseph P.;
Telling, Glenn C.

Publication type:

Article

Strain‐dependent role of copper in prion disease through binding to histidine residues in the N‐terminal domain of prion protein.

Published in:

Journal of Neurochemistry, 2023, v. 167, n. 3, p. 394, doi. 10.1111/jnc.15971

By:

Hara, Hideyuki;
Miyata, Hironori;
Chida, Junji;
Sakaguchi, Suehiro

Publication type:

Article

Oscillations in Neuronal Activity: A Neuron-Centered Spatiotemporal Model of the Unfolded Protein Response in Prion Diseases.

Published in:

Bulletin of Mathematical Biology, 2024, v. 86, n. 7, p. 1, doi. 10.1007/s11538-024-01307-y

By:

Miller, Elliot M.;
Chan, Tat Chung D.;
Montes-Matamoros, Carlos;
Sharif, Omar;
Pujo-Menjouet, Laurent;
Lindstrom, Michael R.

Publication type:

Article

Perspectives on CRISPR Genome Editing to Prevent Prion Diseases in High-Risk Individuals.

Published in:

Biomedicines, 2024, v. 12, n. 8, p. 1725, doi. 10.3390/biomedicines12081725

By:

Medd, Milan M.;
Cao, Qi

Publication type:

Article

Feasibility of Remote Assessment of Human Prion Diseases for Research and Surveillance.

Published in:

Dementia & Geriatric Cognitive Disorders, 2019, v. 47, n. 1/2, p. 79, doi. 10.1159/000497055

By:

Appleby, Brian S.;
Glisic, Kathleen;
Rhoads, Daniel D.;
Bizzi, Alberto;
Cohen, Mark L.;
Mahajan, Supriya

Publication type:

Article

Differential Expression of Metallothioneins in Human Prion Diseases.

Published in:

Dementia & Geriatric Cognitive Disorders, 2000, v. 11, n. 5, p. 251, doi. 10.1159/000017247

By:

Kawashima, Toshiro;
Doh-ura, Katsumi;
Torisu, Miho;
Uchida, Yoko;
Furuta, Akiko;
Iwaki, Toru

Publication type:

Article

Loss of Homeostatic Microglia Signature in Prion Diseases.

Published in:

Cells (2073-4409), 2022, v. 11, n. 19, p. 2948, doi. 10.3390/cells11192948

By:

Wang, Yue;
Hartmann, Kristin;
Thies, Edda;
Mohammadi, Behnam;
Altmeppen, Hermann;
Sepulveda-Falla, Diego;
Glatzel, Markus;
Krasemann, Susanne

Publication type:

Article

MicroRNAs in Prion Diseases—From Molecular Mechanisms to Insights in Translational Medicine.

Published in:

Cells (2073-4409), 2021, v. 10, n. 7, p. 1620, doi. 10.3390/cells10071620

By:

Contiliani, Danyel Fernandes;
Ribeiro, Yasmin de Araújo;
de Moraes, Vitor Nolasco;
Pereira, Tiago Campos

Publication type:

Article

Plasma total prion protein as a potential biomarker for neurodegenerative dementia: diagnostic accuracy in the spectrum of prion diseases.

Published in:

Neuropathology & Applied Neurobiology, 2020, v. 46, n. 3, p. 240, doi. 10.1111/nan.12573

By:

Llorens, F.;
Villar‐Piqué, A.;
Schmitz, M.;
Diaz‐Lucena, D.;
Wohlhage, M.;
Hermann, P.;
Goebel, S.;
Schmidt, I.;
Glatzel, M.;
Hauw, J.‐J.;
Sikorska, B.;
Liberski, P. P.;
Riggert, J.;
Ferrer, I.;
Zerr, I.

Publication type:

Article

Dysfunction of the PI3 K- Akt- GSK-3 pathway is a common feature in cell culture and in vivo models of prion disease.

Published in:

Neuropathology & Applied Neurobiology, 2014, v. 40, n. 3, p. 311, doi. 10.1111/nan.12066

By:

Simon, D.;
Herva, M. E.;
Benitez, M. J.;
Garrido, J. J.;
Rojo, A. I.;
Cuadrado, A.;
Torres, J. M.;
Wandosell, F.

Publication type:

Article

Phenotypic variability in human prion diseases.

Published in:

Neuropathology & Applied Neurobiology, 2005, v. 31, n. 6, p. 565, doi. 10.1111/j.1365-2990.2005.00697.x

By:

Ironside, J. W.;
Ritchie, D. L.;
Head, M. W.

Publication type:

Article

Ultrastructural pathology of prion diseases revisited: brain biopsy studies.

Published in:

Neuropathology & Applied Neurobiology, 2005, v. 31, n. 1, p. 88, doi. 10.1111/j.1365-2990.2004.00595.x

By:

Liberski, P. P.;
Streichenberger, N.;
Giraud, P.;
Soutrenon, M.;
Meyronnet, D.;
Sikorska, B.;
Kopp, N.

Publication type:

Article

Phenotypic variability in the brains of a family with a prion disease characterized by a 144-base pair insertion in the prion protein gene.

Published in:

Neuropathology & Applied Neurobiology, 2003, v. 29, n. 2, p. 98, doi. 10.1046/j.1365-2990.2003.00423.x

By:

King, A.;
Doey, L.;
Rossor, M.;
Mead, S.;
Collinge, J.;
Lantos, P.

Publication type:

Article

Differential expression of transforming growth factor-β isoforms in human prion diseases.

Published in:

Neuropathology & Applied Neurobiology, 1998, v. 24, n. 4, p. 284, doi. 10.1046/j.1365-2990.1998.00117.x

By:

Tashiro;
Doh-ura;
Iwaki;
Tashiro

Publication type:

Article

PrP<sup>ST</sup>, a Soluble, Protease Resistant and Truncated PrP Form Features in the Pathogenesis of a Genetic Prion Disease.

Published in:

PLoS ONE, 2013, v. 8, n. 7, p. 1, doi. 10.1371/journal.pone.0069583

By:

Friedman-Levi, Yael;
Mizrahi, Michal;
Frid, Kati;
Binyamin, Orli;
Gabizon, Ruth

Publication type:

Article

Analyses of the Survival Time and the Influencing Factors of Chinese Patients with Prion Diseases Based on the Surveillance Data from 2008–2011

Published in:

PLoS ONE, 2013, v. 8, n. 5, p. 1, doi. 10.1371/journal.pone.0062553

By:

Chen, Cao;
Wang, Ji-Chun;
Shi, Qi;
Zhou, Wei;
Zhang, Xiao-Mei;
Zhang, Jin;
Tian, Chan;
Gao, Chen;
Dong, Xiao-Ping

Publication type:

Article