Works matching DE "CYSTIC fibrosis"

Results: 5000

Cystic Fibrosis and Hemochromatosis Carriers May Be Prone to Glucagon-like Peptide-1 Agonist Pancreatitis: 3 Cases Open Access.

Published in:

JCEM Case Reports, 2025, v. 3, n. 7, p. 1, doi. 10.1210/jcemcr/luaf104

By:

Sydney, Guy Itzhak;
Do, Tammy;
West, William Austin;
Uwaifo, Gabriel Ikponmosa

Publication type:

Article

Cost-Effectiveness Analysis Methods Used in Evaluations of Treatment for Cystic Fibrosis: A Scoping Review.

Published in:

PharmacoEconomics, 2025, v. 43, n. 7, p. 711, doi. 10.1007/s40273-025-01497-w

By:

Seo, Dominique;
Young, David C.;
Onukwugha, Eberechukwu;
Mattingly II, T. Joseph

Publication type:

Article

Cystic Fibrosis Transmembrane Conductance Regulator Modulators in Cystic Fibrosis: A Review of Registry-Based Evidence.

Published in:

Journal of Clinical Medicine, 2025, v. 14, n. 11, p. 3978, doi. 10.3390/jcm14113978

By:

Salvatore, Donatello;
Pepe, Angela

Publication type:

Article

Population Pharmacokinetics of Elexacaftor, Tezacaftor and Ivacaftor in a Real-World Cohort of Adults with Cystic Fibrosis.

Published in:

Clinical Pharmacokinetics, 2025, v. 64, n. 6, p. 959, doi. 10.1007/s40262-025-01516-1

By:

Magnas, Paulette;
Bouazza, Naïm;
Foissac, Frantz;
Froelicher Bournaud, Léo;
Lui, Gabrielle;
Carlier, Nicolas;
Da Silva, Jennifer;
Fesenbeckh, Johanna;
Kanaan, Reem;
Honoré, Isabelle;
Martin, Clémence;
Treluyer, Jean-Marc;
Burgel, Pierre-Régis;
Benaboud, Sihem

Publication type:

Article

Cellular imbalance in proximal and distal lung of CFTR<sup>−/−</sup> sheep in utero and at birth.

Published in:

Molecular Medicine, 2025, v. 31, n. 1, p. 1, doi. 10.1186/s10020-025-01266-7

By:

Leir, Shih-Hsing;
Tkachenko, Svyatoslav;
Paranjapye, Alekh;
Van Wettere, Arnaud J.;
Kerschner, Jenny L.;
Perisse, Iuri Viotti;
Marriott, Cheyenne M.;
Patrick, Tayler;
Liu, Ying;
White, Kenneth L.;
Polejaeva, Irina A.;
Harris, Ann

Publication type:

Article

Persistent Vitamin D Deficiency in Pediatric Patients with Cystic Fibrosis.

Published in:

Nutrients, 2025, v. 17, n. 11, p. 1890, doi. 10.3390/nu17111890

By:

Reyes-Apodaca, Magali;
Lezana-Fernández, José L.;
Vázquez Frias, Rodrigo;
Rendón-Macías, Mario E.;
González-Molina, Aline;
Rodríguez Espino, Benjamín A.;
Núñez-Barrera, Isela;
Medeiros, Mara

Publication type:

Article

Alpha1-Antitrypsin in Lung Diseases: A Cross-Sectional Observational Study.

Published in:

International Journal of Molecular Sciences, 2025, v. 26, n. 11, p. 5400, doi. 10.3390/ijms26115400

By:

Páska, Csilla;
Barta, Imre;
Csoma, Zsuzsanna;
Gajdócsi, Réka;
Szél, Viktória;
Kerpel-Fronius, Anna;
Solymosi, Diána;
Örlős, Zoltán;
Antus, Balázs

Publication type:

Article

Elexacaftor/Tezacaftor/Ivacaftor Supports Treatment for CF with ΔI1023-V1024-CFTR.

Published in:

International Journal of Molecular Sciences, 2025, v. 26, n. 11, p. 5306, doi. 10.3390/ijms26115306

By:

Huang, Yunjie;
Gonzales Cordova, Jorge Moises;
Penrod, Sarah;
Bendy, Lisa Lynn;
Cheng, Pi Chun;
Sanders, Don B.;
Davis, Michael Denning;
Gaston, Benjamin;
Chmiel, James Francis

Publication type:

Article

Cellular imbalance in proximal and distal lung of CFTR<sup>−/−</sup> sheep in utero and at birth.

Published in:

Molecular Medicine, 2025, v. 31, n. 1, p. 1, doi. 10.1186/s10020-025-01266-7

By:

Leir, Shih-Hsing;
Tkachenko, Svyatoslav;
Paranjapye, Alekh;
Van Wettere, Arnaud J.;
Kerschner, Jenny L.;
Perisse, Iuri Viotti;
Marriott, Cheyenne M.;
Patrick, Tayler;
Liu, Ying;
White, Kenneth L.;
Polejaeva, Irina A.;
Harris, Ann

Publication type:

Article

The Aging Patient with Cystic Fibrosis.

Published in:

Drugs & Aging, 2025, v. 42, n. 6, p. 513, doi. 10.1007/s40266-025-01207-3

By:

Sullivan, Lauren J.;
Mingora, Christina M.;
Flume, Patrick A.

Publication type:

Article

The use of forced oscillation technique in children with restrictive physiology.

Published in:

Breathe, 2025, v. 21, n. 2, p. 1, doi. 10.1183/20734735.0106-2024

By:

Gie, Andre;
Swanepoel, Ruan;
van der Zalm, Marieke M.;
Goussard, Pierre

Publication type:

Article

Antibacterial Siderophores of Pandoraea Pathogens and Their Impact on the Diseased Lung Microbiota.

Published in:

Angewandte Chemie, 2025, v. 137, n. 24, p. 1, doi. 10.1002/ange.202505714

By:

Herzog, Elena;
Ishida, Keishi;
Scherlach, Kirstin;
Chen, Xiuqiang;
Bartels, Benjamin;
Niehs, Sarah P.;
Cheaib, Bachar;
Panagiotou, Gianni;
Hertweck, Christian

Publication type:

Article

Species turnover within cystic fibrosis lung microbiota is indicative of acute pulmonary exacerbation onset.

Published in:

Microbiome, 2025, v. 13, n. 1, p. 1, doi. 10.1186/s40168-025-02143-5

By:

Cuthbertson, Leah;
Hatfield, Lauren;
Gavillet, Helen;
Hardman, Michelle;
Marsh, Ryan;
Rivett, Damian W.;
van der Gast, Christopher

Publication type:

Article

The Proof of the Pudding Is in the Eating: Real-Life Intra- and Extrapulmonary Impact of Elexacaftor/Tezacaftor/Ivacaftor.

Published in:

Respiration, 2025, v. 104, n. 6, p. 388, doi. 10.1159/000543009

By:

Vincken, Stefanie;
Verbanck, Sylvia;
Braun, Sue;
Buyck, Nathalie;
Zienebergh, Cindy;
Knoop, Christiane;
Vanderhelst, Eef

Publication type:

Article

Protein oxidation products in cystic fibrosis.

Published in:

European Journal of Clinical & Experimental Medicine, 2025, v. 23, p. 121

By:

Rożek, Aleksandra;
Rachel, Marta;
Mołoń, Mateusz

Publication type:

Article

Executive Summary: State-of-the-Art Review: Transformative Changes in the Care of People With Cystic Fibrosis—Implications for Infectious Diseases Specialists Free.

Published in:

Clinical Infectious Diseases, 2025, v. 80, n. 5, p. 939, doi. 10.1093/cid/ciaf010

By:

Saiman, Lisa;
Murray, Laurie;
Brown, A Whitney

Publication type:

Article

State-of-the-Art Review: Transformative Changes in the Care of People With Cystic Fibrosis: Implications for Infectious Diseases Specialists Free.

Published in:

Clinical Infectious Diseases, 2025, v. 80, n. 5, p. e65, doi. 10.1093/cid/ciaf009

By:

Saiman, Lisa;
Murray, Laurie;
Brown, A Whitney

Publication type:

Article

Unlocking the potential: integrating phytoconstituents and nanotechnology in skin cancer therapy – A comprehensive review.

Published in:

Journal of Complementary & Integrative Medicine, 2025, v. 22, n. 2, p. 237, doi. 10.1515/jcim-2024-0338

By:

Tiwari, Abhishek;
Tiwari, Varsha;
Sharma, Ajay;
Marrisetti, Arya Lakshmi;
Kumar, Manish;
Rochani, Ankit;
Kaushik, Deepak;
Mittal, Vineet;
Jyothi S., Renuka;
Ali, Haider;
Hussain, Md Sadique;
Gupta, Gaurav

Publication type:

Article

Genomic insights and phenotypic characterization of three multidrug resistant Cupriavidus strains from the cystic fibrosis lung Open Access.

Published in:

Journal of Applied Microbiology, 2025, v. 136, n. 5, p. 1, doi. 10.1093/jambio/lxaf093

By:

Kelly, Sean D;
Butler, James;
Green, Heather;
Jones, Andrew M;
Kenna, Dervla T D;
Pai, Sumita;
Muddiman, Katie J;
McComb, Trudie A;
Barrand, Briana M;
Bennett, Vicky;
Fejer, Gyorgy;
Upton, Mathew

Publication type:

Article

In Vitro Activity of Imipenem/Relebactam Alone and in Combination Against Cystic Fibrosis Isolates of Mycobacterium abscessus.

Published in:

Antibiotics (2079-6382), 2025, v. 14, n. 5, p. 486, doi. 10.3390/antibiotics14050486

By:

Sanders, Madeline;
Kim, Sun Woo;
Shinde, Aditi;
Fletcher-Williams, Danielle;
Quach, Eric;
Beringer, Paul

Publication type:

Article

Overcoming Pseudomonas aeruginosa in Chronic Suppurative Lung Disease: Prevalence, Treatment Challenges, and the Promise of Bacteriophage Therapy.

Published in:

Antibiotics (2079-6382), 2025, v. 14, n. 5, p. 427, doi. 10.3390/antibiotics14050427

By:

Singh, Jagdev;
Solomon, Melinda;
Iredell, Jonathan;
Selvadurai, Hiran

Publication type:

Article

Prevalence and Characteristics of Patients with Cystic Fibrosis-Related Diabetes in Croatia.

Published in:

Life (2075-1729), 2025, v. 15, n. 5, p. 815, doi. 10.3390/life15050815

By:

Kirigin Biloš, Lora Stanka;
Baretić, Maja;
Vukić Dugac, Andrea;
Schoenwald, Krešimir;
Bambir, Ivan;
Tješić Drinković, Duška;
Krnić, Nevena;
Altabas, Velimir

Publication type:

Article

A Longitudinal Study of Glucose Tolerance in Cystic Fibrosis: The Central Role of Beta Cell Functional Mass.

Published in:

Journal of Clinical Endocrinology & Metabolism, 2025, v. 110, n. 5, p. e1670, doi. 10.1210/clinem/dgae474

By:

Piona, Claudia;
Mozzillo, Enza;
Tosco, Antonella;
Zusi, Chiara;
Emiliani, Federica;
Volpi, Sonia;
Candia, Francesca Di;
Raia, Valeria;
Boselli, Maria Linda;
Trombetta, Maddalena;
Cipolli, Marco;
Bonadonna, Riccardo C;
Maffeis, Claudio

Publication type:

Article

The Significance of Density Measurement and the Modified Bhalla and Reiff Scores in Predicting Exacerbations and Hospital Admissions in Cystic Fibrosis Patients.

Published in:

Medicina (1010660X), 2025, v. 61, n. 5, p. 808, doi. 10.3390/medicina61050808

By:

Karcıoğlu, Oğuz;
Ardalı Düzgün, Selin

Publication type:

Article

A mutação F508 da Fibrose Cística: Uma Análise Transversal dos Aspectos Clínicos e Qualidade de Vida de Crianças e Adolescentes.

Published in:

Revista Movimenta, 2025, v. 18, n. 1, p. 95

By:

Araújo de Melo, Géssika;
Tomaz Barbosa, Renata Ramos;
Silva Soares, Thalita Henrique;
Freire de Assis, Thais Josy Castro;
Cordeiro Rocha de Carvalho, Sandra Maria;
Nunes Gadelha, Maria do Socorro

Publication type:

Article

Insights on the Pathogenesis of Mycobacterium abscessus Infection in Patients with Cystic Fibrosis.

Published in:

Journal of Clinical Medicine, 2025, v. 14, n. 10, p. 3492, doi. 10.3390/jcm14103492

By:

Basher, Mai;
Gur, Michal;
Meir, Michal

Publication type:

Article

Vancomycin Monitoring for Treatment of Acute Pulmonary Exacerbations of Adult Cystic Fibrosis Patients.

Published in:

Pulmonary Medicine, 2025, v. 2025, p. 1, doi. 10.1155/pm/5683225

By:

Smith, Darrell;
Sanders, James;
Monogue, Marguerite;
Pini, Laura

Publication type:

Article

Perspectives of people with cystic fibrosis considering parenthood surrounding preconception and prenatal genetic counseling and testing.

Published in:

Therapeutic Advances in Respiratory Disease, 2025, p. 1, doi. 10.1177/17534666251340334

By:

Rajanikanth, Gopika;
Prangley, Asher;
Stransky, Olivia M.;
Langfelder-Schwind, Elinor;
Vento, Jodie;
Felter, Elizabeth;
Kazmerski, Traci M.

Publication type:

Article

Secondary messenger signalling influences Pseudomonas aeruginosa adaptation to sinus and lung environments.

Published in:

ISME Journal: Multidisciplinary Journal of Microbial Ecology, 2024, v. 18, n. 1, p. 1, doi. 10.1093/ismejo/wrae065

By:

Ruhluel, Dilem;
Fisher, Lewis;
Barton, Thomas E;
Leighton, Hollie;
Kumar, Sumit;
Amores Morillo, Paula;
O'Brien, Siobhan;
Fothergill, Joanne L;
Neill, Daniel R

Publication type:

Article

Mutations in the transcriptional regulator MAB_2885 confer tedizolid and linezolid resistance through the MmpS-MmpL efflux pumps MAB_2302-MAB_2303 in Mycobacterium abscessus.

Published in:

PLoS Pathogens, 2025, v. 21, n. 5, p. 1, doi. 10.1371/journal.ppat.1013190

By:

Zhang, Huiyun;
Wang, Shiyong;
Zhang, Yu;
Hua, Wenya;
Lin, Siran;
Chen, Xinchang;
Xu, Tao;
Chen, Jiazhen;
Zhang, Wenhong

Publication type:

Article

Impulse Oscillometry is Useful in Detecting Lung Function Abnormalities in Preschoolers with Primary Ciliary Dyskinesia but Not Cystic Fibrosis: A Cross-Sectional Study Results.

Published in:

Pediatric Allergy, Immunology & Pulmonology, 2025, v. 38, n. 2, p. 71, doi. 10.1089/ped.2024.0142

By:

Sunman, Birce;
Yalcin, Ebru;
Alboga, Didem;
Capraz Yavuz, Burcu;
Altay Tanyer, Emine;
Emiralioglu, Nagehan;
Dogru, Deniz;
Özçelik, Uğur

Publication type:

Article

DIFICULDADES VIVENCIADAS POR MÃES DE PESSOAS COM FIBROSE CÍSTICA.

Published in:

Texto & Contexto Enfermagem, 2014, v. 23, n. 2, p. 294, doi. 10.1590/0104-07072014000050013

By:

Tavares, Keila Okuda;
de Barros Carvalho, Maria Dalva;
Pelloso, Sandra Marisa

Publication type:

Article

O SIGNIFICADO DE UMA ORGANIZAÇÃO DE APOIO AOS PORTADORES E FAMILIARES DE FIBROSE CÍSTICA NA PERSPECTIVA DAS FAMÍLIAS.

Published in:: Texto & Contexto Enfermagem, 2011, v. 20, n. 1, p. 127, doi. 10.1590/S0104-07072011000100015
Publication type:: Article

Cystic Fibrosis Patients: Step-Up to Better Breathing.

Published in:

RT: The Journal for Respiratory Care Practitioners, 2012, v. 25, n. 11, p. 14

By:

Cantine, Michael;
Lomas, Paula

Publication type:

Article

Rapid Growth Necessitates Rapid Improvements.

Published in:

RT: The Journal for Respiratory Care Practitioners, 2012, v. 25, n. 5, p. 24

By:

DILLULIO, RENEE

Publication type:

Article

Survival of Older Cystic Fibrosis Patients May Guide Future Treatment.

Published in:: RT: The Journal for Respiratory Care Practitioners, 2010, v. 23, n. 6, p. 27
Publication type:: Article

CF Medications May Have an Additional Long-Term Benefit.

Published in:: RT: The Journal for Respiratory Care Practitioners, 2009, v. 22, n. 8, p. 19
Publication type:: Article

Pharmaxis Releases Positive Results of Phase 3 Cystic Fibrosis Trial.

Published in:: RT: The Journal for Respiratory Care Practitioners, 2009, v. 22, n. 6, p. 34
Publication type:: Article

Airway-clearance Techniques.

Published in:

RT: The Journal for Respiratory Care Practitioners, 2007, v. 20, n. 11, p. 28

By:

Finder, Jonathan

Publication type:

Article

5 例肺囊性纤维化患儿的护理.

Published in:

Chinese Nursing Research, 2023, v. 37, n. 14, p. 2662, doi. 10.12102/j.issn.1009-6493.2023.14.036

By:

张喜燕

Publication type:

Article

Cystic Fibrosis, Trikafta and Christian Hope: As an academic, most of my time is spent writing and speaking on biomedical issues from the standpoint of an individual whose outlook is informed by his background as a biomedical scientist, a biomedical ethicist, and a Christian

Published in:

Stimulus: The New Zealand Journal of Christian Thought & Practice, 2021, v. 28, n. 1, p. 23

By:

Jones, Gareth

Publication type:

Article

Pulmonary exacerbations as a risk factor for lung function decline - experiences of the National Cystic Fibrosis Center.

Published in:

Vojnosanitetski Pregled: Military Medical & Pharmaceutical Journal of Serbia, 2019, v. 76, n. 11, p. 1110, doi. 10.2298/VSP171114005G

By:

Gojšina, Bojana Z.;
Rodić, Milan;
Višekruna, Jelena;
Trajković, Goran Z.;
Sovtić, Aleksandar D.;
Minić, Predrag B.

Publication type:

Article

Solute carriers keep on rockin'.

Published in:

Nature Structural & Molecular Biology, 2015, v. 22, n. 10, p. 752, doi. 10.1038/nsmb.3104

By:

Reithmeier, Reinhart A F;
Moraes, Trevor F

Publication type:

Article

Molecular basis of UG-rich RNA recognition by the human splicing factor TDP-43.

Published in:

Nature Structural & Molecular Biology, 2013, v. 20, n. 12, p. 1443, doi. 10.1038/nsmb.2698

By:

Lukavsky, Peter J;
Daujotyte, Dalia;
Tollervey, James R;
Ule, Jernej;
Stuani, Cristiana;
Buratti, Emanuele;
Baralle, Francisco E;
Damberger, Fred F;
Allain, Frédéric H-T

Publication type:

Article

CFTR regulatory region interacts with NBD1 predominantly via multiple transient helices.

Published in:

Nature Structural & Molecular Biology, 2007, v. 14, n. 8, p. 738, doi. 10.1038/nsmb1278

By:

Baker, Jennifer M. R.;
Hudson, Rhea P.;
Kanelis, Voula;
Wing-Yiu Choy;
Thibodeau, Patrick H.;
Thomas, Philip J.;
Forman-Kay, Julie D.

Publication type:

Article

Cost-of-illness analysis and regression modeling in cystic fibrosis: a retrospective prevalence-based study.

Published in:

2017

By:

Mlčoch, Tomáš;
Klimeš, Jiří;
Fila, Libor;
Vávrová, Věra;
Skalická, Veronika;
Turnovec, Marek;
Krulišová, Veronika;
Jirčíková, Jitka;
Zemková, Dana;
Dědečková, Klára;
Bílková, Alena;
Frühaufová, Vladimíra;
Homola, Lukáš;
Friedmannová, Zuzana;
Drnek, Radovan;
Dřevínek, Pavel;
Doležal, Tomáš;
Macek, Milan;
Mlčoch, Tomáš;
Klimeš, Jiří

Publication type:

journal article

Social/economic costs and health-related quality of life in patients with cystic fibrosis in Europe.

Published in:

2016

By:

Chevreul, Karine;
Michel, Morgane;
Brigham, Karen;
López-Bastida, Julio;
Linertová, Renata;
Oliva-Moreno, Juan;
Serrano-Aguilar, Pedro;
Posada-de-la-Paz, Manuel;
Taruscio, Domenica;
Schieppati, Arrigo;
Iskrov, Georgi;
Péntek, Márta;
Schulenburg, Johann;
Kanavos, Panos;
Persson, Ulf;
Fattore, Giovani;
Brigham, Karen Berg;
von der Schulenburg, Johann Matthias Graf;
BURQOL-RD Research Network

Publication type:

journal article

Social/economic costs and health-related quality of life in patients with rare diseases in Europe.

Published in:

2016

By:

López-Bastida, Julio;
Oliva-Moreno, Juan;
Linertová, Renata;
Serrano-Aguilar, Pedro

Publication type:

Editorial

Adaptation of Pseudomonas aeruginosa to the cystic fibrosis airway: an evolutionary perspective.

Published in:

Nature Reviews Microbiology, 2012, v. 10, n. 12, p. 841, doi. 10.1038/nrmicro2907

By:

Folkesson, Anders;
Jelsbak, Lars;
Yang, Lei;
Johansen, Helle Krogh;
Ciofu, Oana;
Høiby, Niels;
Molin, Søren

Publication type:

Article

Bacterial evolution: Parallel lives.

Published in:

Nature Reviews Microbiology, 2012, v. 10, n. 1, p. 5, doi. 10.1038/nrmicro2722

By:

Molloy, Sheilagh

Publication type:

Article