Works matching DE "HUNTINGTIN protein"
Results: 645
Dimerization of Polyglutamine within the PRIME20 Model using Stochastic Approximation Monte Carlo.
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- Macromolecular Theory & Simulations, 2023, v. 32, n. 5, p. 1, doi. 10.1002/mats.202200075
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- Article
Heat shock transcription factor-1 suppresses apoptotic cell death and ROS generation in 3-nitropropionic acid-stimulated striatal cells.
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- Molecular & Cellular Biochemistry, 2013, v. 375, n. 1/2, p. 59, doi. 10.1007/s11010-012-1528-z
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- Article
miR-34a-5p as molecular hub of pathomechanisms in Huntington's disease.
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- Molecular Medicine, 2023, v. 29, n. 1, p. 1, doi. 10.1186/s10020-023-00640-7
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- Article
Decreased FAK activity and focal adhesion dynamics impair proper neurite formation of medium spiny neurons in Huntington's disease.
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- Acta Neuropathologica, 2022, v. 144, n. 3, p. 521, doi. 10.1007/s00401-022-02462-z
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- Article
Huntington's disease brain-derived small RNAs recapitulate associated neuropathology in mice.
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- Acta Neuropathologica, 2021, v. 141, n. 4, p. 565, doi. 10.1007/s00401-021-02272-9
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- Article
Poly-glycine–alanine exacerbates C9orf72 repeat expansion-mediated DNA damage via sequestration of phosphorylated ATM and loss of nuclear hnRNPA3.
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- Acta Neuropathologica, 2020, v. 139, n. 1, p. 99, doi. 10.1007/s00401-019-02082-0
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- Article
Demonstration of prion-like properties of mutant huntingtin fibrils in both in vitro and in vivo paradigms.
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- Acta Neuropathologica, 2019, v. 137, n. 6, p. 981, doi. 10.1007/s00401-019-01973-6
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Human-to-mouse prion-like propagation of mutant huntingtin protein.
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- Acta Neuropathologica, 2016, v. 132, n. 4, p. 577, doi. 10.1007/s00401-016-1582-9
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- Article
Axonal transport and secretion of fibrillar forms of α-synuclein, Aβ42 peptide and HTTExon 1.
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- Acta Neuropathologica, 2016, v. 131, n. 4, p. 539, doi. 10.1007/s00401-016-1538-0
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- Article
Coexistence of Huntington's disease and amyotrophic lateral sclerosis: a clinicopathologic study.
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- Acta Neuropathologica, 2012, v. 124, n. 5, p. 749, doi. 10.1007/s00401-012-1005-5
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- Article
Characterizing White Matter in Huntington's Disease.
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- Movement Disorders Clinical Practice, 2020, v. 7, n. 1, p. 52, doi. 10.1002/mdc3.12866
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- Article
Modulation of SETDB1 activity by APQ ameliorates heterochromatin condensation, motor function, and neuropathology in a Huntington's disease mouse model.
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- Journal of Enzyme Inhibition & Medicinal Chemistry, 2021, v. 36, n. 1, p. 856, doi. 10.1080/14756366.2021.1900160
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- Article
Base editing strategies to convert CAG to CAA diminish the disease-causing mutation in Huntington’s disease.
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- eLife, 2024, p. 1, doi. 10.7554/eLife.89782
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- Article
Attenuated huntingtin gene CAG nucleotide repeat size in individuals with Lynch syndrome.
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- Scientific Reports, 2024, v. 14, n. 1, p. 1, doi. 10.1038/s41598-024-54277-5
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- Article
Dose-dependent reduction of somatic expansions but not Htt aggregates by di-valent siRNA-mediated silencing of MSH3 in HdhQ111 mice.
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- Scientific Reports, 2024, v. 14, n. 1, p. 1, doi. 10.1038/s41598-024-52667-3
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- Article
Neuroprotective potency of mangiferin against 3-nitropropionic acid induced Huntington's disease-like symptoms in rats: possible antioxidant and anti-inflammatory mechanisms.
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- Frontiers in Pharmacology, 2023, p. 1, doi. 10.3389/fphar.2023.1189957
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- Article
Theoretical design for covering Engeletin with functionalized nanostructure-lipid carriers as neuroprotective agents against Huntington's disease via the nasal-brain route.
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- Frontiers in Pharmacology, 2023, p. 1, doi. 10.3389/fphar.2023.1218625
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- Article
Non-canonical DNA/RNA structures associated with the pathogenesis of Fragile X-associated tremor/ataxia syndrome and Fragile X syndrome.
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- Frontiers in Genetics, 2022, v. 13, p. 1, doi. 10.3389/fgene.2022.866021
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- Article
Trinucleotide CGG Repeat Diseases: An Expanding Field of Polyglycine Proteins?
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- Frontiers in Genetics, 2022, v. 13, p. 1, doi. 10.3389/fgene.2022.843014
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- Article
The MID1 Protein: A Promising Therapeutic Target in Huntington's Disease.
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- Frontiers in Genetics, 2021, v. 12, p. 1, doi. 10.3389/fgene.2021.761714
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- Article
Huntingtin facilitates selective autophagy.
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- Nature Cell Biology, 2015, v. 17, n. 3, p. 214, doi. 10.1038/ncb3125
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- Article
Effects of Stocking Density on the Growth Performance, Physiological Parameters, Antioxidant Status and Lipid Metabolism of Pelteobagrus fulvidraco in the Integrated Rice-Fish Farming System.
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- Animals (2076-2615), 2023, v. 13, n. 11, p. 1721, doi. 10.3390/ani13111721
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- Article
Characterising the RNA-binding protein atlas of the mammalian brain uncovers RBM5 misregulation in mouse models of Huntington's disease.
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- Nature Communications, 2023, v. 14, n. 1, p. 1, doi. 10.1038/s41467-023-39936-x
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- Article
Uncovering the mechanism for aggregation in repeat expanded RNA reveals a reentrant transition.
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- Nature Communications, 2023, v. 14, n. 1, p. 1, doi. 10.1038/s41467-023-35803-x
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- Article
A novel target for Huntington's disease: ERK at the crossroads of signaling.
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- BioEssays, 2012, v. 34, n. 2, p. 142, doi. 10.1002/bies.201100116
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- Article
The emerging role of the first 17 amino acids of huntingtin in Huntington's disease.
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- Biomolecular Concepts, 2015, v. 6, n. 1, p. 33, doi. 10.1515/bmc-2015-0001
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- Article
Dedication 1966–2007.
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- International Journal of Tryptophan Research, 2009, v. 2, p. 1, doi. 10.1177/11786469090020001
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- Article
Co-expression Network Analysis Revealing the Potential Regulatory Roles of lncRNAs in Alzheimer's Disease.
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- Interdisciplinary Sciences: Computational Life Sciences, 2019, v. 11, n. 4, p. 645, doi. 10.1007/s12539-019-00319-w
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- Article
EvoPPI 1.0: a Web Platform for Within- and Between-Species Multiple Interactome Comparisons and Application to Nine PolyQ Proteins Determining Neurodegenerative Diseases.
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- Interdisciplinary Sciences: Computational Life Sciences, 2019, v. 11, n. 1, p. 45, doi. 10.1007/s12539-019-00317-y
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- Article
Mosquito Cellular Factors and Functions in Mediating the Infectious entry of Chikungunya Virus.
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- PLoS Neglected Tropical Diseases, 2013, v. 7, n. 2, p. 1, doi. 10.1371/journal.pntd.0002050
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- Article
New Treatment Reduces Levels of Protein Linked to Huntington Disease.
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- Psychiatric Times, 2019, v. 36, n. 7, p. 6
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- Article
Clues to γ-secretase, huntingtin and Hirano body normal function using the model organism Dictyostelium discoideum.
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- Journal of Biomedical Science, 2012, v. 19, n. 1, p. 41, doi. 10.1186/1423-0127-19-41
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- Article
A phenolic-rich extract from Ugni molinae berries reduces abnormal protein aggregation in a cellular model of Huntington's disease.
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- PLoS ONE, 2021, v. 16, n. 7, p. 1, doi. 10.1371/journal.pone.0254834
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- Article
Defining the role of the polyasparagine repeat domain of the S. cerevisiae transcription factor Azf1p.
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- PLoS ONE, 2021, v. 16, n. 5, p. 1, doi. 10.1371/journal.pone.0247285
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- Article
Iron activates microglia and directly stimulates indoleamine-2,3-dioxygenase activity in the N171-82Q mouse model of Huntington's disease.
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- PLoS ONE, 2021, v. 16, n. 5, p. 1, doi. 10.1371/journal.pone.0250606
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- Article
Correction: SIRT2 Ablation Has No Effect on Tubulin Acetylation in Brain, Cholesterol Biosynthesis or the Progression of Huntington's Disease Phenotypes In Vivo.
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- 2021
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- Correction Notice
Cerebrospinal fluid endo-lysosomal proteins as potential biomarkers for Huntington's disease.
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- PLoS ONE, 2020, v. 15, n. 8, p. 1, doi. 10.1371/journal.pone.0233820
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- Article
Nascent mutant Huntingtin exon 1 chains do not stall on ribosomes during translation but aggregates do recruit machinery involved in ribosome quality control and RNA.
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- PLoS ONE, 2020, v. 15, n. 7, p. 1, doi. 10.1371/journal.pone.0233583
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- Article
Huntingtin Is Required for Neural But Not Cardiac/Pancreatic Progenitor Differentiation of Mouse Embryonic Stem Cells In vitro.
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- Frontiers in Cellular Neuroscience, 2017, v. 11, p. 1, doi. 10.3389/fncel.2017.00033
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- Article
Proteostasis in striatal cells and selective neurodegeneration in Huntington's disease.
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- Frontiers in Cellular Neuroscience, 2014, v. 8, p. 1, doi. 10.3389/fncel.2014.00218
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- Article
Intranuclear inclusions of polyQ-expanded ATXN1 sequester RNA molecules.
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- Frontiers in Molecular Neuroscience, 2023, p. 1, doi. 10.3389/fnmol.2023.1280546
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- Article
Huntington's Disease as Neurodevelopmental Disorder: Altered Chromatin Regulation, Coding, and Non-Coding RNA Transcription.
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- Frontiers in Neuroscience, 2016, p. 1, doi. 10.3389/fnins.2015.00509
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- Article
Dipeptide repeat proteins inhibit homology-directed DNA double strand break repair in C9ORF72 ALS/FTD.
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- Molecular Neurodegeneration, 2020, v. 15, n. 1, p. 1, doi. 10.1186/s13024-020-00365-9
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- Article
Large-scale transcriptomic analysis reveals that pridopidine reverses aberrant gene expression and activates neuroprotective pathways in the YAC128 HD mouse.
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- Molecular Neurodegeneration, 2018, v. 13, n. 1, p. N.PAG, doi. 10.1186/s13024-018-0259-3
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- Article
Deimmunization for gene therapy: host matching of synthetic zinc finger constructs enables long-term mutant Huntingtin repression in mice.
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- Molecular Neurodegeneration, 2016, v. 11, p. 1, doi. 10.1186/s13024-016-0128-x
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- Article
Making (anti-) sense out of huntingtin levels in Huntington disease.
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- Molecular Neurodegeneration, 2015, v. 10, n. 1, p. 1, doi. 10.1186/s13024-015-0018-7
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- Article
Pathogenic polyglutamine expansion length correlates with polarity of the flanking sequences.
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- Molecular Neurodegeneration, 2014, v. 9, n. 1, p. 1, doi. 10.1186/1750-1326-9-45
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- Article
Characterization of huntingtin interactomes and their dynamic responses in living cells by proximity proteomics.
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- Journal of Neurochemistry, 2023, v. 164, n. 4, p. 512, doi. 10.1111/jnc.15726
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- Article
Issue Information.
- Published in:
- Journal of Neurochemistry, 2023, v. 164, n. 4, p. 445, doi. 10.1111/jnc.15626
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- Article
An imaging mass spectrometry atlas of lipids in the human neurologically normal and Huntington's disease caudate nucleus.
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- Journal of Neurochemistry, 2021, v. 157, n. 6, p. 2158, doi. 10.1111/jnc.15325
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- Article