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Effect of genistein and coenzyme Q10 in oxidative damage and mitochondrial membrane potential in an attenuated type II mucopolysaccharidosis cellular model.
- Published in:
- Cell Biochemistry & Function, 2024, v. 42, n. 2, p. 1, doi. 10.1002/cbf.3932
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- Publication type:
- Article
Increased cytokine levels induced by high phenylalanine concentrations in late diagnosis PKU patients compared to early diagnosis: Anti‐inflammatory effect of L‐carnitine.
- Published in:
- Cell Biochemistry & Function, 2023, v. 41, n. 4, p. 490, doi. 10.1002/cbf.3800
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- Publication type:
- Article
Diabetic encephalopathy-related depression: experimental evidence that insulin and clonazepam restore antioxidant status in rat brain.
- Published in:
- Cell Biochemistry & Function, 2014, v. 32, n. 8, p. 711, doi. 10.1002/cbf.3076
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- Publication type:
- Article
Neurological impairment among heterozygote women for X-linked Adrenoleukodystrophy: a case control study on a clinical, neurophysiological and biochemical characteristics.
- Published in:
- 2014
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- Publication type:
- Case Study
Neurological impairment among heterozygote women for X-linked Adrenoleukodystrophy: a case control study on a clinical, neurophysiological and biochemical characteristics.
- Published in:
- 2014
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- Publication type:
- journal article
Induction of Neuroinflammatory Response and Histopathological Alterations Caused by Quinolinic Acid Administration in the Striatum of Glutaryl-CoA Dehydrogenase Deficient Mice.
- Published in:
- Neurotoxicity Research, 2018, v. 33, n. 3, p. 593, doi. 10.1007/s12640-017-9848-0
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- Publication type:
- Article
Increased Oxidative Damage in Carriers of the Germline TP53 p.R337H Mutation.
- Published in:
- PLoS ONE, 2012, v. 7, n. 10, p. 1, doi. 10.1371/journal.pone.0047010
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- Publication type:
- Article
Mutations, Clinical Findings and Survival Estimates in South American Patients with X-Linked Adrenoleukodystrophy.
- Published in:
- PLoS ONE, 2012, v. 7, n. 3, p. 1, doi. 10.1371/journal.pone.0034195
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- Publication type:
- Article
Experimental evidence that pristanic acid disrupts mitochondrial homeostasis in brain of young rats.
- Published in:
- Journal of Neuroscience Research, 2012, v. 90, n. 3, p. 597, doi. 10.1002/jnr.22802
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- Publication type:
- Article
In vivo neuroprotective effect of L-carnitine against oxidative stress in maple syrup urine disease.
- Published in:
- Metabolic Brain Disease, 2011, v. 26, n. 1, p. 21, doi. 10.1007/s11011-011-9238-x
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- Publication type:
- Article
Acute administration of 5-oxoproline induces oxidative damage to lipids and proteins and impairs antioxidant defenses in cerebral cortex and cerebellum of young rats.
- Published in:
- Metabolic Brain Disease, 2010, v. 25, n. 2, p. 145, doi. 10.1007/s11011-010-9190-1
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- Publication type:
- Article
Alterations of Plasmatic Biomarkers of Neurodegeneration in Mucopolysaccharidosis Type II Patients Under Enzyme Replacement Therapy.
- Published in:
- Cell Biochemistry & Biophysics, 2023, v. 81, n. 3, p. 533, doi. 10.1007/s12013-023-01149-w
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- Publication type:
- Article
Evaluation of oxidative stress and mitochondrial function in a type II mucopolysaccharidosis cellular model: in vitro effects of genistein and coenzyme Q10.
- Published in:
- Metabolic Brain Disease, 2023, v. 38, n. 2, p. 519, doi. 10.1007/s11011-022-01062-w
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- Publication type:
- Article
L-carnitine protects DNA oxidative damage induced by phenylalanine and its keto acid derivatives in neural cells: a possible pathomechanism and adjuvant therapy for brain injury in phenylketonuria.
- Published in:
- Metabolic Brain Disease, 2021, v. 36, n. 7, p. 1957, doi. 10.1007/s11011-021-00780-x
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- Publication type:
- Article
Preliminary results of PBA-loaded nanoparticles development and the effect on oxidative stress and neuroinflammation in rats submitted to a chemically induced chronic model of MSUD.
- Published in:
- Metabolic Brain Disease, 2021, v. 36, n. 5, p. 1015, doi. 10.1007/s11011-021-00686-8
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- Publication type:
- Article
Clinical, biochemical and molecular findings of 24 Brazilian patients with glutaric acidemia type 1: 4 novel mutations in the GCDH gene.
- Published in:
- Metabolic Brain Disease, 2021, v. 36, n. 2, p. 205, doi. 10.1007/s11011-020-00632-0
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- Publication type:
- Article
Oxidative damage in glutaric aciduria type I patients and the protective effects of l‐carnitine treatment.
- Published in:
- Journal of Cellular Biochemistry, 2018, v. 119, n. 12, p. 10021, doi. 10.1002/jcb.27332
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- Publication type:
- Article
High vulnerability of the heart and liver to 3‐hydroxypalmitic acid–induced disruption of mitochondrial functions in intact cell systems.
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- Journal of Cellular Biochemistry, 2018, v. 119, n. 9, p. 7678, doi. 10.1002/jcb.27115
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- Publication type:
- Article
Inflammatory profile in X-linked adrenoleukodystrophy patients: Understanding disease progression.
- Published in:
- Journal of Cellular Biochemistry, 2018, v. 119, n. 1, p. 1223, doi. 10.1002/jcb.26295
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- Publication type:
- Article
Globotriaosylsphingosine induces oxidative DNA damage in cultured kidney cells.
- Published in:
- Nephrology, 2017, v. 22, n. 6, p. 490, doi. 10.1111/nep.12977
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- Publication type:
- Article
Promotion of Lipid and Protein Oxidative Damage in Rat Brain by Ethylmalonic Acid.
- Published in:
- Neurochemical Research, 2010, v. 35, n. 2, p. 298, doi. 10.1007/s11064-009-0055-0
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- Publication type:
- Article
Evaluation of biochemical profile and oxidative damage to lipids and proteins in patients with lysosomal acid lipase deficiency.
- Published in:
- Biochemistry & Cell Biology, 2023, v. 101, n. 4, p. 294, doi. 10.1139/bcb-2022-0330
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- Publication type:
- Article
DNA DAMAGE IN HOMOCYSTINURIA: 8-OXO-,8-DIHYDRO-2'-DEOXYGUANOSINE LEVELS IN CYSTATHIONINE-B-SYNTHASE DEFICIENT PATIENTS AND THE IN VITRO PROTECTIVE EFFECT OF N-ACETYL-L-CYSTEINE.
- Published in:
- Clinical & Biomedical Research, 2018, v. 38, n. 1, p. 50, doi. 10.4322/2357-9730.76977
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- Publication type:
- Article
IN VITRO EFFECT OF N-ACETYL-L-CYSTEINE ON GLUTATHIONE AND SULFHYDRYL LEVELS IN X-LINKED ADRENOLEUKODYSTROPHY PATIENTS.
- Published in:
- Clinical & Biomedical Research, 2017, v. 37, n. 1, p. 33, doi. 10.4322/2357-9730.69868
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- Publication type:
- Article
ACIDÚRIAS D-2-HIDROXIGLUTÁRICA E L-2-HIDROXIGLUTÁRICA: UMA REVISÃO DA LITERATURA.
- Published in:
- Clinical & Biomedical Research, 2016, v. 36, n. 2, p. 80, doi. 10.4322/2357-9730.61060
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- Publication type:
- Article
ENCEFALOPATIA DIABÉTICA E DEPRESSÃO: DANO OXIDATIVO NO CÉREBRO.
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- Clinical & Biomedical Research, 2015, v. 35, n. 4, p. 184, doi. 10.4322/2357-9730.59313
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- Publication type:
- Article
Hyperammonemia in Inherited Metabolic Diseases.
- Published in:
- Cellular & Molecular Neurobiology, 2022, v. 42, n. 8, p. 2593, doi. 10.1007/s10571-021-01156-6
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- Publication type:
- Article
Evidence that Oxidative Disbalance and Mitochondrial Dysfunction are Involved in the Pathophysiology of Fatty Acid Oxidation Disorders.
- Published in:
- Cellular & Molecular Neurobiology, 2022, v. 42, n. 3, p. 521, doi. 10.1007/s10571-020-00955-7
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- Publication type:
- Article
Homocysteine and other markers of cardiovascular risk during a manic episode in patients with bipolar disorder.
- Published in:
- Brazilian Journal of Psychiatry / Revista Brasileira de Psiquiatria, 2013, v. 35, n. 2, p. 157, doi. 10.1590/1516-4446-2012-0797
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- Publication type:
- Article
Simvastatin treatment prevents oxidative damage to DNA in whole blood leukocytes of dyslipidemic type 2 diabetic patients.
- Published in:
- Cell Biochemistry & Function, 2010, v. 28, n. 5, p. 360, doi. 10.1002/cbf.1654
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- Publication type:
- Article
Phenolic Enriched Extract of Baccharis trimera Presents Anti-inflammatory and Antioxidant Activities.
- Published in:
- Molecules, 2012, v. 17, n. 1, p. 1113, doi. 10.3390/molecules17011113
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- Publication type:
- Article
Treatment of maple syrup urine disease: Benefits, risks, and challenges of liver transplantation.
- Published in:
- International Journal of Developmental Neuroscience, 2023, v. 83, n. 6, p. 489, doi. 10.1002/jdn.10283
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- Publication type:
- Article
Clinical findings of patients with hyperammonemia affected by urea cycle disorders with hepatic encephalopathy.
- Published in:
- International Journal of Developmental Neuroscience, 2022, v. 82, n. 8, p. 772, doi. 10.1002/jdn.10229
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- Publication type:
- Article
Elevated levels of BDNF and cathepsin‐d as possible peripheral markers of neurodegeneration in plasma of patients with glutaric acidemia type I.
- Published in:
- International Journal of Developmental Neuroscience, 2020, v. 80, n. 1, p. 42, doi. 10.1002/jdn.10006
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- Publication type:
- Article
Molecular and biochemical biomarkers for diagnosis and therapy monitorization of Niemann-Pick type C patients.
- Published in:
- International Journal of Developmental Neuroscience, 2018, v. 66, p. 18, doi. 10.1016/j.ijdevneu.2017.11.007
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- Publication type:
- Article
Urinary biomarkers of oxidative damage in Maple syrup urine disease: The l-carnitine role.
- Published in:
- International Journal of Developmental Neuroscience, 2015, v. 42, p. 10, doi. 10.1016/j.ijdevneu.2015.02.003
- By:
- Publication type:
- Article
Protein and lipid damage in maple syrup urine disease patients: l-carnitine effect
- Published in:
- International Journal of Developmental Neuroscience, 2013, v. 31, n. 1, p. 21, doi. 10.1016/j.ijdevneu.2012.10.109
- By:
- Publication type:
- Article