Found: 29
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Elexacaftor/Tezacaftor/Ivacaftor Accelerates Wound Repair in Cystic Fibrosis Airway Epithelium.
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- Journal of Personalized Medicine, 2022, v. 12, n. 10, p. 1577, doi. 10.3390/jpm12101577
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- Article
Modulator Therapy in Cystic Fibrosis Patients with cis Variants in F508del Complex Allele: A Short-Term Observational Case Series.
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- Journal of Personalized Medicine, 2022, v. 12, n. 9, p. N.PAG, doi. 10.3390/jpm12091421
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- Article
Advances in Preclinical In Vitro Models for the Translation of Precision Medicine for Cystic Fibrosis.
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- Journal of Personalized Medicine, 2022, v. 12, n. 8, p. 1321, doi. 10.3390/jpm12081321
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- Article
Phenotyping Rare CFTR Mutations Reveal Functional Expression Defects Restored by TRIKAFTA TM.
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- Journal of Personalized Medicine, 2021, v. 11, n. 4, p. 301, doi. 10.3390/jpm11040301
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- Article
Preclinical Studies of a Rare CF-Causing Mutation in the Second Nucleotide Binding Domain (c.3700A>G) Show Robust Functional Rescue in Primary Nasal Cultures by Novel CFTR Modulators.
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- Journal of Personalized Medicine, 2020, v. 10, n. 4, p. 209, doi. 10.3390/jpm10040209
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- Article
The CFTR Mutation c.3453G > C (D1152H) Confers an Anion Selectivity Defect in Primary Airway Tissue that Can be Rescued by Ivacaftor.
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- Journal of Personalized Medicine, 2020, v. 10, n. 2, p. 40, doi. 10.3390/jpm10020040
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- Article
Orkambi® and amplifier co-therapy improves function from a rare CFTR mutation in gene-edited cells and patient tissue.
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- EMBO Molecular Medicine, 2017, v. 9, n. 9, p. 1224, doi. 10.15252/emmm.201607137
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- Article
IGFBP-6 Network in Chronic Inflammatory Airway Diseases and Lung Tumor Progression.
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- International Journal of Molecular Sciences, 2023, v. 24, n. 5, p. 4804, doi. 10.3390/ijms24054804
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- Article
The Oncogenic Theory of Preeclampsia: Is Amniotic Mesenchymal Stem Cells-Derived PLAC1 Involved?
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- International Journal of Molecular Sciences, 2023, v. 24, n. 4, p. 3612, doi. 10.3390/ijms24043612
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- Article
Activity of lumacaftor is not conserved in zebrafish Cftr bearing the major cystic fibrosis‐causing mutation.
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- FASEB Bioadvances, 2019, v. 1, n. 10, p. 661, doi. 10.1096/fba.2019-00039
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- Article
Characterization of anti-proliferative and anti-oxidant effects of nano-sized vesicles from Brassica oleracea L. (Broccoli).
- Published in:
- Scientific Reports, 2022, v. 12, n. 1, p. 1, doi. 10.1038/s41598-022-17899-1
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- Article
Human Amniotic Mesenchymal Stem Cells and Fibroblasts Accelerate Wound Repair of Cystic Fibrosis Epithelium.
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- Life (2075-1729), 2022, v. 12, n. 5, p. 756, doi. 10.3390/life12050756
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- Article
Generation of functional ciliated cholangiocytes from human pluripotent stem cells.
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- Nature Communications, 2021, v. 12, n. 1, p. 1, doi. 10.1038/s41467-021-26764-0
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- Article
Photochemically Activated Notch Signaling Hydrogel Preferentially Differentiates Human Derived Hepatoblasts to Cholangiocytes.
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- Advanced Functional Materials, 2021, v. 31, n. 5, p. 1, doi. 10.1002/adfm.202006116
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- Article
Anticipating New Treatments for Cystic Fibrosis: A Global Survey of Researchers.
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- Journal of Clinical Medicine, 2022, v. 11, n. 5, p. 1283, doi. 10.3390/jcm11051283
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- Article
Anti-Infectives Restore ORKAMBI® Rescue of F508del-CFTR Function in Human Bronchial Epithelial Cells Infected with Clinical Strains of P. aeruginosa.
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- Biomolecules (2218-273X), 2020, v. 10, n. 2, p. 334, doi. 10.3390/biom10020334
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- Article
CFTR interactome mapping using the mammalian membrane two‐hybrid high‐throughput screening system.
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- Molecular Systems Biology, 2022, v. 18, n. 2, p. 1, doi. 10.15252/msb.202110629
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- Article
Molecular Mechanism of Action of Trimethylangelicin Derivatives as CFTR Modulators.
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- Frontiers in Pharmacology, 2018, p. N.PAG, doi. 10.3389/fphar.2018.00719
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- Article
Three-Dimensional Airway Spheroids and Organoids for Cystic Fibrosis Research.
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- Journal of Respiration (JoR), 2021, v. 1, n. 4, p. 229, doi. 10.3390/jor1040022
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- Article
Olive Leaf Extract (OLE) as a Novel Antioxidant That Ameliorates the Inflammatory Response in Cystic Fibrosis.
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- Cells (2073-4409), 2023, v. 12, n. 13, p. 1764, doi. 10.3390/cells12131764
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- Article
High-Throughput Functional Analysis of CFTR and Other Apically Localized Proteins in iPSC-Derived Human Intestinal Organoids.
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- Cells (2073-4409), 2021, v. 10, n. 12, p. 3419, doi. 10.3390/cells10123419
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- Article
Anti-Inflammatory and Anti-Oxidant Effect of Dimethyl Fumarate in Cystic Fibrosis Bronchial Epithelial Cells.
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- Cells (2073-4409), 2021, v. 10, n. 8, p. 2132, doi. 10.3390/cells10082132
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- Article
Cholesterol Interaction Directly Enhances Intrinsic Activity of the Cystic Fibrosis Transmembrane Conductance Regulator (CFTR).
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- Cells (2073-4409), 2019, v. 8, n. 8, p. 804, doi. 10.3390/cells8080804
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- Article
One‐Step Formation of Protein‐Based Tubular Structures for Functional Devices and Tissues.
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- Advanced Healthcare Materials, 2021, v. 10, n. 8, p. 1, doi. 10.1002/adhm.202001746
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- Article
Stage-Specific Generation of Human Pluripotent Stem Cell Derived Lung Models to Measure CFTR Function.
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- Current Protocols, 2022, v. 2, n. 1, p. 1, doi. 10.1002/cpz1.341
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- Article
Comprehensive mapping of cystic fibrosis mutations to CFTR protein identifies mutation clusters and molecular docking predicts corrector binding site.
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- Proteins, 2018, v. 86, n. 8, p. 833, doi. 10.1002/prot.25496
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- Article
Cover Image, Volume 86, Issue 8.
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- Proteins, 2018, v. 86, n. 8, p. C1, doi. 10.1002/prot.25579
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- Article
Editorial: Mechanisms of action of small molecules on CFTR mutants and the impact on cystic fibrosis pathogenesis.
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- Frontiers in Molecular Biosciences, 2024, p. 1, doi. 10.3389/fmolb.2024.1446875
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- Article
Editorial: Mechanisms of action of small molecules on CFTR mutants and the impact on cystic fibrosis pathogenesis.
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- Frontiers in Molecular Biosciences, 2024, p. 1, doi. 10.3389/fmolb.2024.1446875
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- Article