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Cellular Chaperones As Therapeutic Targets in ALS to Restore Protein Homeostasis and Improve Cellular Function.
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- Frontiers in Molecular Neuroscience, 2017, p. 1, doi. 10.3389/fnmol.2017.00251
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- Article
Astrocytes display cell autonomous and diverse early reactive states in familial amyotrophic lateral sclerosis.
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- 2022
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- Publication type:
- journal article
Humanized mutant FUS drives progressive motor neuron degeneration without aggregation in 'FUSDelta14' knockin mice.
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- 2017
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- Publication type:
- journal article
Enhanced Expression of TRAP1 Protects Mitochondrial Function in Motor Neurons under Conditions of Oxidative Stress.
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- International Journal of Molecular Sciences, 2022, v. 23, n. 3, p. 1789, doi. 10.3390/ijms23031789
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- Article
Activation of the heat shock response in a primary cellular model of motoneuron neurodegeneration-evidence for neuroprotective and neurotoxic effects.
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- Cellular & Molecular Biology Letters, 2009, v. 14, n. 2, p. 319, doi. 10.2478/s11658-009-0002-8
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- Article
Microglial Expression of theWnt Signaling Modulator DKK2 Differs between Human Alzheimer's Disease Brains andMouse Neurodegeneration Models.
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- eNeuro, 2023, v. 10, n. 1, p. 1, doi. 10.1523/ENEURO.0306-22.2022
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- Publication type:
- Article
Treatment with arimoclomol, a coinducer of heat shock proteins, delays disease progression in ALS mice.
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- Nature Medicine, 2004, v. 10, n. 4, p. 402, doi. 10.1038/nm1021
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- Article
Analysis of motor dysfunction in Down Syndrome reveals motor neuron degeneration.
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- 2018
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- Abstract
Molecular Chaperone Mediated Late-Stage Neuroprotection in the SOD1<sup>G93A</sup> Mouse Model of Amyotrophic Lateral Sclerosis.
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- PLoS ONE, 2013, v. 8, n. 8, p. 1, doi. 10.1371/journal.pone.0073944
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- Publication type:
- Article
Plasma Neurofilament Heavy Chain Levels Correlate to Markers of Late Stage Disease Progression and Treatment Response in SOD1<sup>G93A</sup> Mice that Model ALS.
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- PLoS ONE, 2012, v. 7, n. 7, p. 1, doi. 10.1371/journal.pone.0040998
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- Article
Excitability properties of mouse motor axons in the mutant SOD1(G93A) model of amyotrophic lateral sclerosis.
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- 2010
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- Publication type:
- journal article
Excitability properties of mouse motor axons in the mutant SOD1<sup>G93A</sup> model of amyotrophic lateral sclerosis.
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- Muscle & Nerve, 2010, v. 41, n. 6, p. 774, doi. 10.1002/mus.21579
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- Publication type:
- Article
Mice with endogenous TDP‐43 mutations exhibit gain of splicing function and characteristics of amyotrophic lateral sclerosis.
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- EMBO Journal, 2018, v. 37, n. 11, p. 1, doi. 10.15252/embj.201798684
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- Publication type:
- Article
Expression of Kv3.1b potassium channel is widespread in macaque motor cortex pyramidal cells: A histological comparison between rat and macaque.
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- Journal of Comparative Neurology, 2017, v. 525, n. 9, p. 2164, doi. 10.1002/cne.24192
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- Publication type:
- Article
Targeting protein homeostasis in sporadic inclusion body myositis.
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- Science Translational Medicine, 2016, v. 8, n. 331, p. 1, doi. 10.1126/scitranslmed.aad4583
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- Publication type:
- Article
Activated leukocyte cell adhesion molecule modulates neurotrophin signaling.
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- Journal of Neurochemistry, 2012, v. 121, n. 4, p. 575, doi. 10.1111/j.1471-4159.2012.07658.x
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- Publication type:
- Article
Mitochondrial deficits and abnormal mitochondrial retrograde axonal transport play a role in the pathogenesis of mutant Hsp27-induced Charcot Marie Tooth Disease.
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- Human Molecular Genetics, 2017, v. 26, n. 17, p. 3313, doi. 10.1093/hmg/ddx216
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- Publication type:
- Article
Expression of a pathogenic mutation of SOD1 sensitizes aprataxin-deficient cells and mice to oxidative stress and triggers hallmarks of premature ageing
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- Human Molecular Genetics, 2015, v. 24, n. 3, p. 828, doi. 10.1093/hmg/ddu500
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- Publication type:
- Article
Inhibiting p38 MAPK alpha rescues axonal retrograde transport defects in a mouse model of ALS.
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- Cell Death & Disease, 2018, v. 9, n. 6, p. 1, doi. 10.1038/s41419-018-0624-8
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- Publication type:
- Article
Regional Differences in Heat Shock Protein 25 Expression in Brain and Spinal Cord Astrocytes of Wild-Type and SOD1 G93A Mice.
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- Cells (2073-4409), 2021, v. 10, n. 5, p. 1257, doi. 10.3390/cells10051257
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- Publication type:
- Article
Sectioning and Counting of Motor Neurons in the L3 to L6 Region of the Adult Mouse Spinal Cord.
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- Current Protocols, 2022, v. 2, n. 5, p. 1, doi. 10.1002/cpz1.428
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- Publication type:
- Article
Late stage treatment with arimoclomol delays disease progression and prevents protein aggregation in the SOD1<sup>G93A</sup> mouse model of ALS.
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- Journal of Neurochemistry, 2008, v. 107, n. 2, p. 339, doi. 10.1111/j.1471-4159.2008.05595.x
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- Publication type:
- Article
A novel p.Glu175X premature stop mutation in the C-terminal end of HSP27 is a cause of CMT2.
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- Journal of the Peripheral Nervous System, 2012, v. 17, n. 2, p. 201, doi. 10.1111/j.1529-8027.2012.00400.x
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- Publication type:
- Article
Behavioral and Other Phenotypes in a Cytoplasmic Dynein Light Intermediate Chain 1 Mutant Mouse.
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- Journal of Neuroscience, 2011, v. 31, n. 14, p. 5483, doi. 10.1523/JNEUROSCI.5244-10.2011
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- Article