Found: 102
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The significance of cytoplasmic inclusions in late infantile and juvenile amaurotic idiocy.
- Published in:
- Acta Neuropathologica, 1973, v. 23, n. 1, p. 32, doi. 10.1007/BF00689002
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- Publication type:
- Article
Accumulation of smooth cisterns, multivesicular bodies and 'zebra' bodies in neurons.
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- Acta Neuropathologica, 1971, v. 18, n. 2, p. 132, doi. 10.1007/BF00687601
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- Publication type:
- Article
Familial spongy degeneration of the central nervous system (Van Bogaert-Bertrand disease).
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- Acta Neuropathologica, 1969, v. 12, n. 2, p. 103, doi. 10.1007/BF00692500
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- Publication type:
- Article
Clinicopathological Correlates in a PRNP P102L Mutation Carrier with Rapidly Progressing Parkinsonism-Dystonia.
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- Movement Disorders Clinical Practice, 2016, v. 3, n. 4, p. 355, doi. 10.1002/mdc3.12307
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- Publication type:
- Article
Two distinct conformers of PrPD type 1 of sporadic Creutzfeldt–Jakob disease with codon 129VV genotype faithfully propagate in vivo.
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- Acta Neuropathologica Communications, 2021, v. 9, n. 1, p. 1, doi. 10.1186/s40478-021-01132-7
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- Publication type:
- Article
A novel mechanism of phenotypic heterogeneity in Creutzfeldt-Jakob disease.
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- Acta Neuropathologica Communications, 2020, v. 8, n. 1, p. 1, doi. 10.1186/s40478-020-00966-x
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- Publication type:
- Article
Soluble amyloid-β in the brain: The scarlet pimpernel.
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- Journal of Alzheimer's Disease, 2006, v. 9, n. 3, p. 127, doi. 10.3233/JAD-2006-9S315
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- Publication type:
- Article
Characterization of the F198S prion protein mutation: Enhanced glycosylation and defective refolding.
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- Journal of Alzheimer's Disease, 2005, v. 7, n. 2, p. 159, doi. 10.3233/JAD-2005-7209
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- Publication type:
- Article
Soluble amyloid beta-protein is increased in frontotemporal dementia with tau gene mutations.
- Published in:
- 2004
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- Publication type:
- journal article
Soluble amyloid β-protein is increased in frontotemporal dementia with tau gene mutations.
- Published in:
- Journal of Alzheimer's Disease, 2004, v. 6, n. 1, p. 45, doi. 10.3233/JAD-2004-6106
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- Publication type:
- Article
Variable Protease-Sensitive Prionopathy Transmission to Bank Voles.
- Published in:
- 2019
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- Publication type:
- journal article
Recent US Case of Variant Creutzfeldt-Jakob Disease-Global Implications.
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- 2015
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- Publication type:
- journal article
Recent US Case of Variant Creutzfeldt-Jakob Disease--Global Implications.
- Published in:
- 2015
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- Publication type:
- Case Study
Transmission characteristics of variably protease-sensitive prionopathy.
- Published in:
- 2014
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- Publication type:
- journal article
Constant Transmission Properties of Variant Creutzfeldt-Jakob Disease in 5 Countries.
- Published in:
- Emerging Infectious Diseases, 2012, v. 18, n. 10, p. 1574, doi. 10.3201/eid1810.120792
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- Publication type:
- Article
Assessing Prion Infectivity of Human Urine in Sporadic Creutzfeldt-Jakob Disease.
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- Emerging Infectious Diseases, 2012, v. 18, n. 1, p. 21, doi. 10.3201/eid1801.110589
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- Publication type:
- Article
Efficient transmission of human prion diseases to a glycan-free prion protein-expressing host.
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- Brain: A Journal of Neurology, 2024, v. 147, n. 4, p. 1539, doi. 10.1093/brain/awad399
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- Publication type:
- Article
A case cluster of variant Creutzfeldt-Jakob disease linked to the Kingdom of Saudi Arabia.
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- Brain: A Journal of Neurology, 2016, v. 139, n. 10, p. 2609, doi. 10.1093/brain/aww206
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- Publication type:
- Article
Prion replication?once again blaming the dendritic cell.
- Published in:
- Nature Medicine, 1999, v. 5, n. 11, p. 1235, doi. 10.1038/15186
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- Publication type:
- Article
A discriminative event‐based model for subtype diagnosis of sporadic Creutzfeldt‐Jakob disease using brain MRI.
- Published in:
- Alzheimer's & Dementia: The Journal of the Alzheimer's Association, 2023, v. 19, n. 8, p. 3261, doi. 10.1002/alz.12939
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- Publication type:
- Article
Sensitive detection of pathological seeds of α-synuclein, tau and prion protein on solid surfaces.
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- PLoS Pathogens, 2024, v. 20, n. 4, p. 1, doi. 10.1371/journal.ppat.1012175
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- Publication type:
- Article
Variant Creutzfeldt-Jakob disease death, United States.
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- 2005
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- Publication type:
- journal article
Chronic wasting disease and potential transmission to humans.
- Published in:
- 2004
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- Publication type:
- journal article
Immunohistochemical localization of glial fibrillary acidic protein in human glial neoplasms.
- Published in:
- 1980
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- Publication type:
- journal article
Absence of protease-resistant prion protein in the cerebrospinal fluid of Creutzfeldt-Jakob disease.
- Published in:
- Journal of Pathology, 2001, v. 194, n. 1, p. 9, doi. 10.1002/path.872
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- Publication type:
- Article
NEURONAL INTRACYTOPLASMIC PRP DEPOSITS IN DOMINANTLY INHERITED CREUTZFELDT-JAKOB DISEASE ASSOCIATED WITH THE PRNP E200K-129V HAPLOTYPE.
- Published in:
- Alzheimer's & Dementia: The Journal of the Alzheimer's Association, 2016, v. 12, p. P1116, doi. 10.1016/j.jalz.2016.06.2320
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- Publication type:
- Article
Early onset and rapid course of Alzheimer disease associated with the I143T PSEN1 mutation.
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- Alzheimer's & Dementia: The Journal of the Alzheimer's Association, 2014, v. 10, p. P629, doi. 10.1016/j.jalz.2014.05.1095
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- Publication type:
- Article
Transmission of Alzheimer amyloidosis to chimpanzees and monkeys: Revisited
- Published in:
- 2010
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- Publication type:
- Abstract
Protease-sensitive prionopathy in a cognitively normal 93-year-old
- Published in:
- 2010
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- Publication type:
- Abstract
P2-207: Co-distribution of Aβ plaques and spongiform degeneration in familial Creutzfeldt-Jakob disease with E200K-129M haplotype
- Published in:
- 2008
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- Publication type:
- Abstract
Variants of PLCXD3 are not associated with variant or sporadic Creutzfeldt-Jakob disease in a large international study.
- Published in:
- BMC Medical Genetics, 2016, v. 17, p. 1, doi. 10.1186/s12881-016-0278-2
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- Publication type:
- Article
Variably Protease-Sensitive Prionopathy: a Novel Disease of the Prion Protein.
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- Journal of Molecular Neuroscience, 2011, v. 45, n. 3, p. 422, doi. 10.1007/s12031-011-9543-1
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- Publication type:
- Article
Novel strain properties distinguishing sporadic prion diseases sharing prion protein genotype and prion type.
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- Scientific Reports, 2017, p. 38280, doi. 10.1038/srep38280
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- Publication type:
- Article
Gerstmann-Sträussler-Scheinker disease subtypes efficiently transmit in bank voles as genuine prion diseases.
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- Scientific Reports, 2016, p. 20443, doi. 10.1038/srep20443
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- Publication type:
- Article
Small Ruminant Nor98 Prions Share Biochemical Features with Human Gerstmann-Sträussler-Scheinker Disease and Variably Protease-Sensitive Prionopathy.
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- PLoS ONE, 2013, v. 8, n. 6, p. 1, doi. 10.1371/journal.pone.0066405
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- Publication type:
- Article
Glycoform-Selective Prion Formation in Sporadic and Familial Forms of Prion Disease.
- Published in:
- PLoS ONE, 2013, v. 8, n. 3, p. 1, doi. 10.1371/journal.pone.0058786
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- Publication type:
- Article
Multiorgan Detection and Characterization of Protease- Resistant Prion Protein in a Case of Variant CJD Examined in the United States.
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- PLoS ONE, 2010, v. 5, n. 1, p. 1, doi. 10.1371/journal.pone.0008765
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- Publication type:
- Article
Gerstmann-Sträussler-Scheinker disease revisited: accumulation of covalently-linked multimers of internal prion protein fragments.
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- Acta Neuropathologica Communications, 2019, v. 7, n. 1, p. N.PAG, doi. 10.1186/s40478-019-0734-2
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- Publication type:
- Article
Co-occurrence of chronic traumatic encephalopathy and prion disease.
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- Acta Neuropathologica Communications, 2018, v. 6, n. 1, p. N.PAG, doi. 10.1186/s40478-018-0643-9
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- Publication type:
- Article
Gerstmann–Sträussler–Scheinker Disease with F198S Mutation Induces Independent Tau and Prion Protein Pathologies in Bank Voles.
- Published in:
- Biomolecules (2218-273X), 2022, v. 12, n. 10, p. N.PAG, doi. 10.3390/biom12101537
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- Publication type:
- Article
Publisher Correction: Early preclinical detection of prions in the skin of prion-infected animals.
- Published in:
- Nature Communications, 2019, v. 10, n. 1, p. 1, doi. 10.1038/s41467-019-08648-6
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- Publication type:
- Article
Early preclinical detection of prions in the skin of prion-infected animals.
- Published in:
- Nature Communications, 2019, v. 10, n. 1, p. 1, doi. 10.1038/s41467-018-08130-9
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- Publication type:
- Article
Sporadic Creutzfeldt-Jakob disease in a native Puerto Rican patient.
- Published in:
- 2015
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- Publication type:
- Journal Article
Sporadic Creutzfeldt-Jakob Disease in a Native Puerto Rican Patient.
- Published in:
- Puerto Rico Health Sciences Journal, 2015, v. 34, n. 1, p. 40
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- Publication type:
- Article
Chronic Wasting Disease of Elk: Transmissibility to Humans Examined by Transgenic Mouse Models.
- Published in:
- Journal of Neuroscience, 2005, v. 25, n. 35, p. 7944, doi. 10.1523/JNEUROSCI.2467-05.2005
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- Publication type:
- Article
Protease-Resistant Human Prion Protein and Ferritin Are Cotransported across Caco-2 Epithelial Cells: Implications for Species Barrier in Prion Uptake from the Intestine.
- Published in:
- Journal of Neuroscience, 2004, v. 24, n. 50, p. 11280, doi. 10.1523/JNEUROSCI.2864-04.2004
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- Publication type:
- Article
Cell-free propagation of prion strains.
- Published in:
- EMBO Journal, 2008, v. 27, n. 19, p. 2557, doi. 10.1038/emboj.2008.181
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- Publication type:
- Article
Evaluation of a New Criterion for Detecting Prion Disease With Diffusion Magnetic Resonance Imaging.
- Published in:
- JAMA Neurology, 2020, v. 77, n. 9, p. 1141, doi. 10.1001/jamaneurol.2020.1319
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- Publication type:
- Article
Co-existence of scrapie prion protein types 1 and 2 in sporadic Creutzfeldt–Jakob disease: its effect on the phenotype and prion-type characteristics.
- Published in:
- Brain: A Journal of Neurology, 2009, v. 132, n. 10, p. 2643, doi. 10.1093/brain/awp196
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- Publication type:
- Article
Classification of sporadic Creutzfeldt–Jakob disease revisited.
- Published in:
- Brain: A Journal of Neurology, 2006, v. 129, n. 9, p. 2266, doi. 10.1093/brain/awl224
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- Publication type:
- Article