Found: 24
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Improving the Pharmacological Properties of Ciclopirox for Its Use in Congenital Erythropoietic Porphyria.
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- Journal of Personalized Medicine, 2021, v. 11, n. 6, p. 485, doi. 10.3390/jpm11060485
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- Article
Enfermedades priónicas: historia, diversidad e importancia socioeconómica como paradigma de las Enfermedades Raras.
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- Araucaria, 2021, v. 23, n. 46, p. 429, doi. 10.12795/araucaria.2021.i46.21
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- Article
Prion-Associated Neurodegeneration Causes Both Endoplasmic Reticulum Stress and Proteasome Impairment in a Murine Model of Spontaneous Disease.
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- International Journal of Molecular Sciences, 2021, v. 22, n. 1, p. 465, doi. 10.3390/ijms22010465
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Post-translational modifications in PrP expand the conformational diversity of prions in vivo.
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- Scientific Reports, 2017, p. 43295, doi. 10.1038/srep43295
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- Article
Detection of Pathognomonic Biomarker PrPSc and the Contribution of Cell Free-Amplification Techniques to the Diagnosis of Prion Diseases.
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- Biomolecules (2218-273X), 2020, v. 10, n. 3, p. 469, doi. 10.3390/biom10030469
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- Article
Classical BSE dismissed as the cause of CWD in Norwegian red deer despite strain similarities between both prion agents.
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- Veterinary Research, 2024, v. 55, n. 1, p. 1, doi. 10.1186/s13567-024-01320-y
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- Article
Recombinant PrP<sup>Sc</sup> shares structural features with brain-derived PrP<sup>Sc</sup>: Insights from limited proteolysis.
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- PLoS Pathogens, 2018, v. 14, n. 1, p. 1, doi. 10.1371/journal.ppat.1006797
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Understanding the key features of the spontaneous formation of bona fide prions through a novel methodology that enables their swift and consistent generation.
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- Acta Neuropathologica Communications, 2023, v. 11, n. 1, p. 1, doi. 10.1186/s40478-023-01640-8
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- Article
Bona fide atypical scrapie faithfully reproduced for the first time in a rodent model.
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- Acta Neuropathologica Communications, 2022, v. 10, n. 1, p. 1, doi. 10.1186/s40478-022-01477-7
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- Article
Dogs are resistant to prion infection, due to the presence of aspartic or glutamic acid at position 163 of their prion protein.
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- FASEB Journal, 2020, v. 34, n. 3, p. 3969, doi. 10.1096/fj.201902646R
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Recombinant PrP and Its Contribution to Research on Transmissible Spongiform Encephalopathies.
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- Pathogens, 2017, v. 6, n. 4, p. 67, doi. 10.3390/pathogens6040067
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- Article
Repurposing ciclopirox as a pharmacological chaperone in a model of congenital erythropoietic porphyria.
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- Science Translational Medicine, 2018, v. 10, n. 459, p. 1, doi. 10.1126/scitranslmed.aat7467
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- Article
Transgenic Mouse Bioassay: Evidence That Rabbits Are Susceptible to a Variety of Prion Isolates.
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- PLoS Pathogens, 2015, v. 11, n. 8, p. 1, doi. 10.1371/journal.ppat.1004977
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- Article
Description of the first Spanish case of Gerstmann–Sträussler–Scheinker disease with A117V variant: clinical, histopathological and biochemical characterization.
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- Journal of Neurology, 2022, v. 269, n. 8, p. 4253, doi. 10.1007/s00415-022-11051-9
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- Article
Sporadic Creutzfeldt–Jakob disease with extremely long 14‐year survival period.
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- European Journal of Neurology, 2021, v. 28, n. 9, p. 2901, doi. 10.1111/ene.14946
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- Article
Unraveling the key to the resistance of canids to prion diseases.
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- PLoS Pathogens, 2017, v. 13, n. 11, p. 1, doi. 10.1371/journal.ppat.1006716
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- Article
Cofactors influence the biological properties of infectious recombinant prions.
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- Acta Neuropathologica, 2018, v. 135, n. 2, p. 179, doi. 10.1007/s00401-017-1782-y
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- Article
Homozygous R136S mutation in PRNP gene causes inherited early onset prion disease.
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- Alzheimer's Research & Therapy, 2021, v. 13, n. 1, p. 1, doi. 10.1186/s13195-021-00912-6
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- Article
Development of a new largely scalable in vitro prion propagation method for the production of infectious recombinant prions for high resolution structural studies.
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- PLoS Pathogens, 2019, v. 15, n. 10, p. 1, doi. 10.1371/journal.ppat.1008117
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A Single Amino Acid Substitution, Found in Mammals with Low Susceptibility to Prion Diseases, Delays Propagation of Two Prion Strains in Highly Susceptible Transgenic Mouse Models.
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- Molecular Neurobiology, 2019, v. 56, n. 9, p. 6501, doi. 10.1007/s12035-019-1535-0
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- Article
Insights into the Bidirectional Properties of the Sheep–Deer Prion Transmission Barrier.
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- Molecular Neurobiology, 2019, v. 56, n. 8, p. 5287, doi. 10.1007/s12035-018-1443-8
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- Article
An Amino Acid Substitution Found in Animals with Low Susceptibility to Prion Diseases Confers a Protective Dominant-Negative Effect in Prion-Infected Transgenic Mice.
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- Molecular Neurobiology, 2018, v. 55, n. 7, p. 6182, doi. 10.1007/s12035-017-0832-8
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- Article
Infectivity versus Seeding in Neurodegenerative Diseases Sharing a Prion-Like Mechanism.
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- International Journal of Cell Biology, 2013, p. 1, doi. 10.1155/2013/583498
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- Article
Glycans are not necessary to maintain the pathobiological features of bovine spongiform encephalopathy.
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- PLoS Pathogens, 2022, v. 18, n. 10, p. 1, doi. 10.1371/journal.ppat.1010900
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- Article