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Systemic bis-phosphinic acid derivative restores chloride transport in Cystic Fibrosis mice.
- Published in:
- Scientific Reports, 2022, v. 12, n. 1, p. 1, doi. 10.1038/s41598-022-09678-9
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- Publication type:
- Article
Author Correction: New insights into structure and function of bis-phosphinic acid derivatives and implications for CFTR modulation.
- Published in:
- 2021
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- Publication type:
- Correction Notice
Acting on the CFTR Membrane-Spanning Domains Interface Rescues Some Misfolded Mutants.
- Published in:
- International Journal of Molecular Sciences, 2022, v. 23, n. 24, p. 16225, doi. 10.3390/ijms232416225
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- Publication type:
- Article
Differential CFTR-Interactome Proximity Labeling Procedures Identify Enrichment in Multiple SLC Transporters.
- Published in:
- International Journal of Molecular Sciences, 2022, v. 23, n. 16, p. 8937, doi. 10.3390/ijms23168937
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- Publication type:
- Article
Urinary Exosomes of Patients with Cystic Fibrosis Unravel CFTR-Related Renal Disease.
- Published in:
- International Journal of Molecular Sciences, 2020, v. 21, n. 18, p. 6625, doi. 10.3390/ijms21186625
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- Publication type:
- Article
Control of Basal CFTR Gene Expression by Bicarbonate-Sensitive Adenylyl Cyclase in Human Pulmonary Cells.
- Published in:
- Cellular Physiology & Biochemistry (Karger AG), 2008, v. 21, n. 1-3, p. 075, doi. 10.1159/000113749
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- Publication type:
- Article
Structural models of CFTR-AMPK and CFTR-PKA interactions: R-domain flexibility is a key factor in CFTR regulation.
- Published in:
- Journal of Molecular Modeling, 2012, v. 18, n. 1, p. 83, doi. 10.1007/s00894-011-1029-0
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- Publication type:
- Article
Proteomic Analysis of Nasal Epithelial Cells from Cystic Fibrosis Patients.
- Published in:
- PLoS ONE, 2014, v. 9, n. 9, p. 1, doi. 10.1371/journal.pone.0108671
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- Publication type:
- Article
Characterization of Nasal Potential Difference in <i>cftr</i> Knockout and F508del-CFTR Mice.
- Published in:
- PLoS ONE, 2013, v. 8, n. 3, p. 1, doi. 10.1371/journal.pone.0057317
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- Publication type:
- Article
Functional Interaction between CFTR and the Sodium-Phosphate Co-Transport Type 2a in Xenopus laevis Oocytes.
- Published in:
- PLoS ONE, 2012, v. 7, n. 4, p. 1, doi. 10.1371/journal.pone.0034879
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- Publication type:
- Article
Eicosanoid Release Is Increased by Membrane Destabilization and CFTR Inhibition in Calu-3 Cells.
- Published in:
- PLoS ONE, 2009, v. 4, n. 10, p. 1, doi. 10.1371/journal.pone.0007116
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- Publication type:
- Article
Peroxiredoxin 6 Fails to Limit Phospholipid Peroxidation in Lung from Cftr-Knockout Mice Subjected to Oxidative Challenge.
- Published in:
- PLoS ONE, 2009, v. 4, n. 6, p. 1, doi. 10.1371/journal.pone.0006075
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- Publication type:
- Article
Early effects of parathyroid hormone on membrane potential of rat osteoblasts in culture: Role of cAMP and Ca<sup>2+</sup>.
- Published in:
- Journal of Bone & Mineral Research, 1988, v. 3, n. 5, p. 547, doi. 10.1002/jbmr.5650030511
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- Publication type:
- Article
Might Brushed Nasal Cells Be a Surrogate for CFTR Modulator Clinical Response?
- Published in:
- 2019
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- Publication type:
- Letter
rAAV-CFTRΔR rescues the cystic fibrosis phenotype in human intestinal organoids and CF mice.
- Published in:
- American Journal of Respiratory & Critical Care Medicine, 2016, v. 193, n. 3, p. E1, doi. 10.1164/rccm.201505-0914oc
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- Publication type:
- Article
rAAV-CFTRΔR Rescues the Cystic Fibrosis Phenotype in Human Intestinal Organoids and Cystic Fibrosis Mice.
- Published in:
- 2016
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- Publication type:
- journal article
Sensitivity of mass spectrometry analysis depends on the shape of the filtration unit used for filter aided sample preparation (FASP).
- Published in:
- Proteomics, 2016, v. 16, n. 13, p. 1852, doi. 10.1002/pmic.201600103
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- Publication type:
- Article
Global proteomic approach unmasks involvement of keratins 8 and 18 in the delivery of cystic fibrosis transmembrane conductance regulator (CFTR)/ΔF508-CFTR to the plasma membrane.
- Published in:
- Proteomics, 2004, v. 4, n. 12, p. 3833, doi. 10.1002/pmic.200400850
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- Publication type:
- Article
A neutral variant involved in a complexCFTRallele contributes to a severe cystic fibrosis phenotype.
- Published in:
- Human Genetics, 2005, v. 116, n. 6, p. 454, doi. 10.1007/s00439-004-1246-z
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- Publication type:
- Article
Elexacaftor/Tezacaftor/Ivacaftor Disrupts Respiratory Tract Development in a Murine Fetal Lung Explant Model.
- Published in:
- 2022
- By:
- Publication type:
- Letter to the Editor
Expression of the human erythroid Rh glycoprotein (RhAG) enhances both NH<sub>3</sub> and NH transport in HeLa cells.
- Published in:
- Pflügers Archiv: European Journal of Physiology, 2005, v. 450, n. 3, p. 155, doi. 10.1007/s00424-005-1381-y
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- Publication type:
- Article
New sequence‐specific human ribonuclease: purification and properties.
- Published in:
- Nucleic Acids Research, 1998, v. 26, n. 17, p. 4047, doi. 10.1093/nar/26.17.4047
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- Publication type:
- Article
Novel gain-of-function mutants identify a critical region within CFTR membrane-spanning domain 2 controlling cAMP-dependent and ATP-independent channel activation.
- Published in:
- Cellular & Molecular Life Sciences, 2024, v. 81, n. 1, p. 1, doi. 10.1007/s00018-024-05431-9
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- Publication type:
- Article
Pharmacological chaperone-rescued cystic fibrosis CFTR-F508del mutant overcomes PRAF2-gated access to endoplasmic reticulum exit sites.
- Published in:
- Cellular & Molecular Life Sciences, 2022, v. 79, n. 10, p. 1, doi. 10.1007/s00018-022-04554-1
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- Publication type:
- Article
Keratin 8 is a scaffolding and regulatory protein of ERAD complexes.
- Published in:
- Cellular & Molecular Life Sciences, 2022, v. 79, n. 9, p. 1, doi. 10.1007/s00018-022-04528-3
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- Publication type:
- Article
Pharmacological chaperones improve intra-domain stability and inter-domain assembly via distinct binding sites to rescue misfolded CFTR.
- Published in:
- Cellular & Molecular Life Sciences, 2021, v. 78, n. 23, p. 7813, doi. 10.1007/s00018-021-03994-5
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- Publication type:
- Article
Neutrophil Elastase Degrades Cystic Fibrosis Transmembrane Conductance Regulator via Calpains and Disables Channel Function In Vitro and In Vivo.
- Published in:
- American Journal of Respiratory & Critical Care Medicine, 2013, v. 187, n. 2, p. 170, doi. 10.1164/rccm.201205-0875oc
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- Publication type:
- Article
Chloride Transport in Nasal Ciliated Cells of Cystic Fibrosis Heterozygotes.
- Published in:
- American Journal of Respiratory & Critical Care Medicine, 2005, v. 171, n. 9, p. 1026, doi. 10.1164/rccm.200406-740OC
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- Publication type:
- Article
The CF-CIRC study: a French collaborative study to assess the accuracy of Cystic Fibrosis diagnosis in neonatal screening.
- Published in:
- BMC Pediatrics, 2006, v. 6, p. 25, doi. 10.1186/1471-2431-6-25
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- Publication type:
- Article
New insights into structure and function of bis-phosphinic acid derivatives and implications for CFTR modulation.
- Published in:
- Scientific Reports, 2021, v. 11, n. 1, p. 1, doi. 10.1038/s41598-021-83240-x
- By:
- Publication type:
- Article
Emerging Therapeutic Approaches for Cystic Fibrosis. From Gene Editing to Personalized Medicine.
- Published in:
- Frontiers in Pharmacology, 2019, p. N.PAG, doi. 10.3389/fphar.2019.00121
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- Publication type:
- Article
Genetic deletion of keratin 8 corrects the altered bone formation and osteopenia in a mouse model of cystic fibrosis.
- Published in:
- Human Molecular Genetics, 2016, v. 25, n. 7, p. 1281, doi. 10.1093/hmg/ddw009
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- Publication type:
- Article
The testis anion transporter TAT1 (SLC26A8) physically and functionally interacts with the cystic fibrosis transmembrane conductance regulator channel: a potential role during sperm capacitation.
- Published in:
- Human Molecular Genetics, 2012, v. 21, n. 6, p. 1287, doi. 10.1093/hmg/ddr558
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- Publication type:
- Article
Disruption of cytokeratin-8 interaction with F508del-CFTR corrects its functional defect.
- Published in:
- Human Molecular Genetics, 2012, v. 21, n. 3, p. 623, doi. 10.1093/hmg/ddr496
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- Publication type:
- Article
GSH monoethyl ester rescues mitochondrial defects in cystic fibrosis models.
- Published in:
- Human Molecular Genetics, 2011, v. 20, n. 14, p. 2745, doi. 10.1093/hmg/ddr173
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- Publication type:
- Article
Aspirin and some other nonsteroidal anti-inflammatory drugs inhibit cystic fibrosis transmembrane conductance regulator protein gene expression in T-84 cells.
- Published in:
- Mediators of Inflammation, 1999, v. 8, n. 4/5, p. 219, doi. 10.1080/09629359990388
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- Publication type:
- Article
Correlating genotype with phenotype using CFTR‐mediated whole‐cell Cl<sup>−</sup> currents in human nasal epithelial cells.
- Published in:
- Journal of Physiology, 2022, v. 600, n. 6, p. 1515, doi. 10.1113/JP282143
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- Publication type:
- Article
Resveratrol rescues cAMP-dependent anionic transport in the cystic fibrosis pancreatic cell line CFPAC1.
- Published in:
- 2011
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- Publication type:
- journal article
<italic>Cis</italic> variants identified in F508del complex alleles modulate CFTR channel rescue by small molecules.
- Published in:
- Human Mutation, 2018, v. 39, n. 4, p. 506, doi. 10.1002/humu.23389
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- Publication type:
- Article
Characterization of SLC26 A9 in Patients with CF-Like Lung Disease.
- Published in:
- Human Mutation, 2013, v. 34, n. 10, p. 1404, doi. 10.1002/humu.22382
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- Publication type:
- Article
Misprocessing of the CFTR protein leads to mild cystic fibrosis phenotype.
- Published in:
- Human Mutation, 2005, v. 25, n. 4, p. 360, doi. 10.1002/humu.20156
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- Publication type:
- Article
Lanthanum carbonate, like sevelamer-HCl, retards the progression of vascular calcification and atherosclerosis in uremic apolipoprotein E-deficient mice.
- Published in:
- Nephrology Dialysis Transplantation, 2012, v. 27, n. 2, p. 505, doi. 10.1093/ndt/gfr254
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- Publication type:
- Article
In vitro prediction of stop-codon suppression by intravenous gentamicin in patients with cystic fibrosis: a pilot study.
- Published in:
- BMC Medicine, 2007, v. 5, p. 1, doi. 10.1186/1741-7015-5-5
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- Publication type:
- Article
Identification of a novel mutation, 1087delT, in exon 7 of the CFTR gene in a patient with cystic fibrosis.
- Published in:
- Human Mutation, 2000, v. 16, n. 1, p. 95, doi. 10.1002/1098-1004(200007)16:1<95::AID-HUMU30>3.0.CO;2-3
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- Publication type:
- Article
Contribution of proteomics to the study of the role of cytokeratins in disease and physiopathology.
- Published in:
- Proteomics - Clinical Applications, 2008, v. 2, n. 2, p. 264, doi. 10.1002/prca.200780018
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- Publication type:
- Article
New insights into interactions between the nucleotide-binding domain of CFTR and keratin 8.
- Published in:
- Protein Science: A Publication of the Protein Society, 2017, v. 26, n. 2, p. 343, doi. 10.1002/pro.3086
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- Publication type:
- Article