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Reply to migration is not the perfect answer: Optimized methodology to assess LCI agreement between corrected legacy multiple breath nitrogen washout data and that directly collected on updated software.
- Published in:
- Pediatric Pulmonology, 2023, v. 58, n. 7, p. 1861, doi. 10.1002/ppul.26430
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- Publication type:
- Article
Migration is not the perfect answer: How the cross‐talk error correction for multiple breath nitrogen washout (MBWN<sub>2</sub>) parameters differs on directly collected vs. legacy data.
- Published in:
- Pediatric Pulmonology, 2023, v. 58, n. 1, p. 328, doi. 10.1002/ppul.26169
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- Publication type:
- Article
Entering the era of highly effective modulator therapies.
- Published in:
- Pediatric Pulmonology, 2021, v. 56, p. S79, doi. 10.1002/ppul.24968
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- Publication type:
- Article
Evaluation of a multiple breath nitrogen washout system in children.
- Published in:
- Pediatric Pulmonology, 2020, v. 55, n. 8, p. 2108, doi. 10.1002/ppul.24862
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- Publication type:
- Article
Horses for courses: Learning from functional tests of pulmonary health?
- Published in:
- Pediatric Pulmonology, 2020, v. 55, n. 8, p. 1855, doi. 10.1002/ppul.24818
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- Publication type:
- Article
Combination antifungal therapy for Scedosporium species in cystic fibrosis.
- Published in:
- Pediatric Pulmonology, 2020, v. 55, n. 8, p. 1993, doi. 10.1002/ppul.24789
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- Publication type:
- Article
A systematic review to identify and collate factors influencing patient journeys through clinical trials.
- Published in:
- JRSM Open, 2023, v. 14, n. 6, p. 1, doi. 10.1177/20542704231166621
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- Publication type:
- Article
Gene therapy for the treatment of cystic fibrosis.
- Published in:
- Application of Clinical Genetics, 2012, v. 5, p. 29, doi. 10.2147/TACG.S8873
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- Publication type:
- Article
Pseudomonas aeruginosa in cystic fibrosis: pathogenesis and new treatments.
- Published in:
- 2011
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- Publication type:
- Journal Article
Pseudomonas aeruginosa in cystic fibrosis: pathogenesis and new treatments.
- Published in:
- British Journal of Hospital Medicine (17508460), 2011, v. 72, n. 11, p. 614, doi. 10.12968/hmed.2011.72.11.614
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- Publication type:
- Article
Lytic Bacteriophage Is a Promising Adjunct to Common Antibiotics across Cystic Fibrosis Clinical Strains and Culture Models of Pseudomonas aeruginosa Infection.
- Published in:
- Antibiotics (2079-6382), 2023, v. 12, n. 3, p. 593, doi. 10.3390/antibiotics12030593
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- Publication type:
- Article
Colistin kills bacteria by targeting lipopolysaccharide in the cytoplasmic membrane.
- Published in:
- eLife, 2021, p. 1, doi. 10.7554/eLife.65836
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- Publication type:
- Article
Ivacaftor in People With Cystic Fibrosis and a 3849+10kb CT or D1152H Residual Function Mutation.
- Published in:
- Annals of the American Thoracic Society, 2021, v. 18, n. 3, p. E1, doi. 10.1513/annalsats.202006-659oc
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- Publication type:
- Article
Ivacaftor in People with Cystic Fibrosis and a → or Residual Function Mutation.
- Published in:
- 2021
- By:
- Publication type:
- journal article
CpG-free plasmids confer reduced inflammation and sustained pulmonary gene expression.
- Published in:
- Nature Biotechnology, 2008, v. 26, n. 5, p. 549, doi. 10.1038/nbt1399
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- Publication type:
- Article
Highlights of the North American Cystic Fibrosis Conference 2011.
- Published in:
- Journal of the Royal Society of Medicine, 2012, v. 105, p. 9, doi. 10.1258/jrsm.2012.12s002
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- Publication type:
- Article
Highlights of the North American Cystic Fibrosis Conference 2011.
- Published in:
- 2012
- By:
- Publication type:
- research
New therapeutic approaches for cystic fibrosis lung disease.
- Published in:
- 2002
- By:
- Publication type:
- journal article
Bronchoscopy in Cystic Fibrosis Infants Diagnosed by Newborn Screening.
- Published in:
- Pediatric Pulmonology, 2011, v. 46, n. 7, p. 696, doi. 10.1002/ppul.21434
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- Publication type:
- Article
Time required to obtain endobronchial biopsies in children during fiberoptic bronchoscopy.
- Published in:
- Pediatric Pulmonology, 2009, v. 44, n. 1, p. 76, doi. 10.1002/ppul.20949
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- Publication type:
- Article
Bone marrow stem cells do not repopulate the healthy upper respiratory tract.
- Published in:
- Pediatric Pulmonology, 2002, v. 34, n. 4, p. 251, doi. 10.1002/ppul.10163
- By:
- Publication type:
- Article
Current and future treatment options for cystic fibrosis lung disease: latest evidence and clinical implications.
- Published in:
- Therapeutic Advances in Chronic Disease, 2016, v. 7, n. 3, p. 170, doi. 10.1177/2040622316641352
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- Publication type:
- Article
Chronicity Counts: The Impact of Pseudomonas aeruginosa , Staphylococcus aureus , and Coinfection in Cystic Fibrosis.
- Published in:
- 2024
- By:
- Publication type:
- Letter
Improvement in Lung Clearance Index and Chest Computed Tomography Scores with Elexacaftor/Tezacaftor/Ivacaftor Treatment in People with Cystic Fibrosis Aged 12 Years and Older -- The RECOVER Trial.
- Published in:
- American Journal of Respiratory & Critical Care Medicine, 2023, v. 208, n. 9, p. 917, doi. 10.1164/rccm.202308-1317oc
- By:
- Publication type:
- Article
Raised Intracranial Pressure in Three Children with Cystic Fibrosis Receiving ElexacaftorTezacaftor-Ivacaftor Modulator Therapy.
- Published in:
- American Journal of Respiratory & Critical Care Medicine, 2023, v. 208, n. 1, p. 103, doi. 10.1164/rccm.202303-0380LE
- By:
- Publication type:
- Article
Long-Term Safety and Efficacy of Elexacaftor/Tezacaftor/Ivacaftor in Children Aged ≥6 Years with Cystic Fibrosis and at Least One F508del Allele: A Phase 3, Open-Label Clinical Trial.
- Published in:
- American Journal of Respiratory & Critical Care Medicine, 2023, v. 208, n. 1, p. 68, doi. 10.1164/rccm.202301-0021OC
- By:
- Publication type:
- Article
in the Cystic Fibrosis Airway: Does It Deserve Its Reputation as a Predatory "Bully"?
- Published in:
- 2021
- By:
- Publication type:
- Letter
Ivacaftor in Infants Aged 4 to <12 Months with Cystic Fibrosis and a Gating Mutation. Results of a Two-Part Phase 3 Clinical Trial.
- Published in:
- 2021
- By:
- Publication type:
- journal article
Whole-Gene Sequencing of Reveals a High Prevalence of the Intronic Variant c.3874-4522A>G in Cystic Fibrosis.
- Published in:
- 2020
- By:
- Publication type:
- Letter
Impact of T2R38 Receptor Polymorphisms on Pseudomonas aeruginosa Infection in Cystic Fibrosis.
- Published in:
- 2018
- By:
- Publication type:
- Letter
Tezacaftor/Ivacaftor in Subjects with Cystic Fibrosis and F508del/F508del-CFTR or F508del/G551D-CFTR.
- Published in:
- 2018
- By:
- Publication type:
- journal article
Clinical Trials of Novel Treatments for Cystic Fibrosis.
- Published in:
- 2016
- By:
- Publication type:
- journal article
A Phase I/IIa Safety and Efficacy Study of Nebulized Liposome-mediated Gene Therapy for Cystic Fibrosis Supports a Multidose Trial.
- Published in:
- 2015
- By:
- Publication type:
- journal article
Diversity and prevalence of type VI secretion system effectors in clinical Pseudomonas aeruginosa isolates.
- Published in:
- Frontiers in Microbiology, 2023, v. 13, p. 1, doi. 10.3389/fmicb.2022.1042505
- By:
- Publication type:
- Article
Pseudomonas aeruginosa induces p38MAP kinase-dependent IL-6 and CXCL8 release from bronchial epithelial cells via a Syk kinase pathway.
- Published in:
- PLoS ONE, 2021, v. 16, n. 2, p. 1, doi. 10.1371/journal.pone.0246050
- By:
- Publication type:
- Article
Quantification of Periciliary Fluid Height in Human Airway Biopsies Is Feasible, but Not Suitable as a Biomarker.
- Published in:
- American Journal of Respiratory Cell & Molecular Biology, 2011, v. 44, n. 3, p. 309, doi. 10.1165/rcmb.2009-0265OC
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- Publication type:
- Article
Nasal Abnormalities in Cystic Fibrosis Mice Independent of Infection and Inflammation.
- Published in:
- American Journal of Respiratory Cell & Molecular Biology, 2008, v. 39, n. 1, p. 19, doi. 10.1165/rcmb.2007-0284OC
- By:
- Publication type:
- Article
Variability in Bacteriophage and Antibiotic Sensitivity in Serial Pseudomonas aeruginosa Isolates from Cystic Fibrosis Airway Cultures over 12 Months.
- Published in:
- Microorganisms, 2021, v. 9, n. 3, p. 660, doi. 10.3390/microorganisms9030660
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- Publication type:
- Article
Going the Extra Mile: Why Clinical Research in Cystic Fibrosis Must Include Children.
- Published in:
- Children, 2022, v. 9, n. 7, p. N.PAG, doi. 10.3390/children9071080
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- Publication type:
- Article
An Update on CFTR Modulators as New Therapies for Cystic Fibrosis.
- Published in:
- Pediatric Drugs, 2022, v. 24, n. 4, p. 321, doi. 10.1007/s40272-022-00509-y
- By:
- Publication type:
- Article
Increased incidence and severity of the systemic inflammatory response syndrome in patients deficient in mannose-binding lectin.
- Published in:
- 2004
- By:
- Publication type:
- journal article
Lung clearance index in primary ciliary dyskinesia and bronchiectasis.
- Published in:
- 2014
- By:
- Publication type:
- Journal Article
Lung Clearance Index in Primary Ciliary Dyskinesia and Bronchiectasis.
- Published in:
- American Journal of Respiratory & Critical Care Medicine, 2014, v. 189, n. 9, p. 1147, doi. 10.1164/rccm.201402-0206le
- By:
- Publication type:
- Article
Lung Clearance Index and High-Resolution Computed Tomography Scores in Primary Ciliary Dyskinesia.
- Published in:
- American Journal of Respiratory & Critical Care Medicine, 2013, v. 188, n. 5, p. 545, doi. 10.1164/rccm.201304-0800OC
- By:
- Publication type:
- Article
Efficacy and safety of ivacaftor in patients aged 6 to 11 years with cystic fibrosis with a G551D mutation.
- Published in:
- 2013
- By:
- Publication type:
- journal article
Efficacy and Safety of Ivacaftor in Patients Aged 6 to 11 Years with Cystic Fibrosis with a C551D Mutation.
- Published in:
- American Journal of Respiratory & Critical Care Medicine, 2013, v. 187, n. 11, p. 1219, doi. 10.1164/rccm.201301-0153oc
- By:
- Publication type:
- Article
Assessment of F/HN-Pseudotyped Lentivirus as a Clinically Relevant Vector for Lung Gene Therapy.
- Published in:
- American Journal of Respiratory & Critical Care Medicine, 2012, v. 186, n. 9, p. 846, doi. 10.1164/rccm.201206-1056OC
- By:
- Publication type:
- Article
The Th17 Pathway in Cystic Fibrosis Lung Disease.
- Published in:
- American Journal of Respiratory & Critical Care Medicine, 2011, v. 184, n. 2, p. 252, doi. 10.1164/rccm.201102-0236OC
- By:
- Publication type:
- Article
Biomarkers for Cystic Fibrosis.
- Published in:
- American Journal of Respiratory & Critical Care Medicine, 2007, v. 175, n. 8, p. 750, doi. 10.1164/rccm.200702-226ED
- By:
- Publication type:
- Article
Potential Difference Measurements in the Lower Airway of Children with and without Cystic Fibrosis.
- Published in:
- American Journal of Respiratory & Critical Care Medicine, 2005, v. 171, n. 9, p. 1015, doi. 10.1164/rccm.200408-1116OC
- By:
- Publication type:
- Article