We found a match
Your institution may have rights to this item. Sign in to continue.
- Title
A nationwide study evaluating the association of autoimmune bullous diseases and acquired haemophilia: description of clinical and prognostic features.
- Authors
Barranca, Alexis; Debarbieux, Sébastien; Tancrède‐Bohin, Emmanuelle; Saillard, Clémence; Sassolas, Bruno; Voisin, Sophie; Fortenfant, Françoise; Bost, Chloe; Claeyssens‐Donadel, Ségolène; Joly, Pascal; Bedane, Christophe; Bulai‐Livideanu, Cristina; Paul, Carle; Konstantinou, Maria Polina
- Abstract
When the clinical manifestations of AHA appeared, six patients had active AIBD, three had AIBD controlled with topical steroids and one had AIBD in partial remission under methotrexate and oral steroids. HB of the oropharynx as an early sign of AHA in AIBD patients have been reported in case reports.3 Rituximab can be effective for both diseases. Dear Editor, Acquired haemophilia A (AHA) is a bleeding disorder caused by neutralizing autoantibodies targeting factor VIII (FVIII).1 AHA has been rarely associated with autoimmune bullous diseases (AIBD).1 The aim of this study was to describe the specific clinical, immunological and prognostic features of patients with an AIBD and secondary AHA.
- Subjects
BULLOUS pemphigoid; AUTOIMMUNE diseases; HEMOPHILIA; HEALTH facilities
- Publication
British Journal of Dermatology, 2022, Vol 186, Issue 5, p899
- ISSN
0007-0963
- Publication type
Article
- DOI
10.1111/bjd.20953