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- Title
Difficulties in cochlear implantation in children with Di George syndrome.
- Authors
Porowski, M.; Skarżyński, H.; Mrowka, M.; Skarżyński, P. H.; Ratuszniak, A.
- Abstract
Di George syndrome is a rare congenital malformation. The syndrome is caused by the deletion of a segment of chromosome 22. The symptoms include hearing loss, congenital heart problems and usually multiple other associated conditions. The aim of the study was to show the surgical technique used for cochlear implantation in two patients with Di George syndrome and discuss the results obtained after surgical treatment. Material and Methods: Two patients with Di George syndrome were qualified for CI treatment because of the bilateral sensorineural hearing loss and no effect with hearing aids. They presented complex inner ear malformations with cochlear dysplasia and congenital heart failure. In both cases the technique of cochlear implantation was facial recess. Results and conclusions: The operations went without complications. We did not observe also late complications. After intensive rehabilitation we achieved satisfactory hearing results in both children. The results of cochlear implant surgery in young patients with middle and inner ear malformation in Di George syndrome are good. In each case of this syndrome one should take care of associated conditions, including congenital heart failure. One should be also prepared for problems associated with complex anatomy during the operation.
- Subjects
BELGIUM; CONFERENCES &; conventions; COCHLEAR implants; DIGEORGE syndrome
- Publication
Journal of Hearing Science, 2018, Vol 8, Issue 2, p319
- ISSN
2083-389X
- Publication type
Article