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- Title
Adrenocortical carcinoma in a 6-month-old infant.
- Authors
Rahar, Seema; Chauhan, Devender; Singh, Shashikant; Ahuja, Arvind; Bhardwaj, Minakshi; Sen, Amita
- Abstract
Adrenocortical carcinoma (ACC) is a rare malignant tumor arising from the adrenal cortex and it is even rarer in infancy. These tumors are usually hormonally active. We report a case of ACC in a 6-month-old infant who was brought by her mother with complaints of hirsutism and abnormally looking genitalia. Serum 17-alpha-hydroxyprogesterone and serum cortisol levels were raised. Subsequently, imaging studies revealed a large well-circumscribed soft-tissue mass in the right suprarenal region. The tumor was excised, and on histopathology in conjunction with immunohistochemistry, a diagnosis of ACC was given. Only four other cases of ACC have been reported till date in the literature, with an age of 6 months or younger. Hereby, we present a case of ACC in a young infant.
- Subjects
ADRENAL tumors; HYDROCORTISONE; HYPERTRICHOSIS; IMMUNOHISTOCHEMISTRY; PROGESTERONE; RARE diseases; ULTRASONIC imaging; EARLY diagnosis
- Publication
Journal of Indian Association of Pediatric Surgeons, 2020, Vol 25, Issue 5, p310
- ISSN
0971-9261
- Publication type
Article
- DOI
10.4103/jiaps.JIAPS_155_19