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- Title
A Case of Intratemporal Rhabdomyosarcoma in a Child Presenting with VII<sup>th</sup>, IX<sup>th</sup>, and X<sup>th</sup> Cranial Nerve Paralysis.
- Authors
Tomoaki MURAKAMI; Masashi HAMADA; Kyoko ODAGIRI; Takashi KOIKE; Hiromasa YABE
- Abstract
Objective: Rhabdomyosarcoma is the most common soft tissue tumor in children, with average age of onset being 5 years, and approximately 70% cases diagnosed below 10 years of age. It accounts for 37% of primary head and neck malignancies in children. Chemotherapy with surgery, and radiation is selected as the primary treatment. We report a rare case of rhabdomyosarcoma in the temporal bone presenting with glossopharyngeal and vagus nerve paralysis as well as facial palsy. Case report: The patient was a 6-year-old boy, and his initial symptom was dizziness followed by facial palsy and hoarseness. Although a severe type of otitis media was suspected in the first clinic, CT and MRI showed a temporal bone tumor with parameningeal extension. Biopsy with cortical mastoidectomy revealed an embryonal-type rhabdomyosarcoma. Pretreatment re-excision was abandoned because of parameningeal involvement. The tumor disappeared after a series of chemotherapy, however, meningeal dissemination occurred, and he eventually died even after an additional administration of anti-cancer agents and intensive modulated radiation therapy. Conclusion: In the case of facial palsy concomitant with other cranial nerve paralysis, care must be taken into neoplastic origin. Early image diagnosis may offer a chance of complete resection in addition to chemo-radiotherapy.
- Subjects
RHABDOMYOSARCOMA; CHILDREN; GLOSSOPHARYNGEAL nerve; CHEMORADIOTHERAPY; VAGUS nerve
- Publication
Tokai Journal of Experimental & Clinical Medicine, 2022, Vol 47, Issue 2, p85
- ISSN
0385-0005
- Publication type
Article