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- Title
Abnormal Dentition in a Boy with Incontinentia Pigmenti: Case Report.
- Authors
Afshar, H.; Daneshpazhooh, M.; Kiani, A.; Aref, P.; Baniameri, Z.
- Abstract
Incontinentia pigmenti (IP) is an X-linked dominant genodermatosis characterized by typical skin lesions along Blaschko's lines and associated with ocular, dental, nails, hair, skeletal, central nervous system and cardiovascular anomalies. We report a 5-year-old boy with cutaneous hyperpigmentation along Blaschko's lines, atrophic streaks, strabismus and mental retardation. He showed the characteristic abnormal dentition seen in IP as partial hypodontia, peg-shaped anterior teeth and un-erupted teeth. The expression of IP in boys is exceptional as the disease is lethal in males.
- Subjects
DENTITION; HYPODONTIA; TOOTH eruption; TEETH abnormalities
- Publication
Journal of Dentistry of Tehran University of Medical Sciences, 2012, Vol 9, Issue 3, p267
- ISSN
1735-2150
- Publication type
Case Study