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- Title
Elimination of medically intractable epileptic drop attacks following endoscopic total corpus callosotomy in Rett syndrome.
- Authors
Ueda, Keisuke; Sood, Sandeep; Asano, Eishi; Kumar, Ajay; Luat, Aimee
- Abstract
Introduction: Rett syndrome is a neurodevelopmental genetic disorder, characterized by developmental delay, hand stereotypies, abnormal gait, and acquired microcephaly. Epilepsy is very common in Rett syndrome and can be medically intractable. It remains uncertain if a patient with epileptic drop attacks associated with this genetic disease can benefit from corpus callosotomy. Case report: We report an 8-year-old girl with Rett syndrome and medically intractable epileptic drop attacks who underwent endoscopic total corpus callosotomy without any complications that led to the successful elimination of her seizures. Conclusion: Total corpus callosotomy is a feasible treatment option for medically intractable epileptic drop attacks in Rett syndrome and should not be considered as a contraindication in this condition. This is the first reported case of corpus callosotomy in Rett syndrome.
- Subjects
CHILDHOOD epilepsy; RETT syndrome; CORPUS callosum abnormalities; ENDOSCOPIC surgery; THERAPEUTICS
- Publication
Child's Nervous System, 2017, Vol 33, Issue 11, p1883
- ISSN
0256-7040
- Publication type
Article
- DOI
10.1007/s00381-017-3567-y