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- Title
Surgery for cystic lymphangioma in Gorlin–Goltz syndrome.
- Authors
Kayser, C.; Kayser, G.; Baier, P.; Hopt, U. T.; Eggstein, S.
- Abstract
We present a case of three major lymphomesenteric cysts in a female patient with known basal cell nevus syndrome (BCNS or Gorlin–Goltz syndrome). Although those cysts have been reported to appear in this syndrome, the exact prevalence is not known. In this case, the patient suffered from severe and recurrent abdominal pain due to bowel obstruction. By causing severe symptoms, cystic lymphangiomas are an important complication of the BCNS despite of their seldom occurrence. Surgeons confronted with intraabdominal masses in a patient with BCNS should always be aware of this manifestation of the disorder and plan interdisciplinary operations.
- Subjects
CYSTS (Pathology); BASAL cell nevus syndrome; ANGIOMAS; BOWEL obstructions; MESENTERY tumors
- Publication
Langenbeck's Archives of Surgery, 2007, Vol 392, Issue 2, p203
- ISSN
1435-2443
- Publication type
Article
- DOI
10.1007/s00423-006-0126-5