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- Title
idiopatik Pulmoner Hemosideroz.
- Authors
Bakan, Nur Dilek; Kanmaz, Dilek; özkan, Gülcihan; Tekeşin, Muhammet; Bayram, Mehmet; Çilingir, Mesiha; Gür, Aygün; Çamsarı, Güngör
- Abstract
Idiopathic pulmonary hemosiderosis (IPH) is a rare cause of alveolar hemorrhage, characterized by recurrent episodes of alveolar hemorrhage, hemoptysis and secondary iron-deficiency anemia which occurs primarily in childhood. The pathogenesis is not known. A diagnosis of IPH can be made only when other causes of diffuse alveolar hemorrhage have been reliably excluded. A 15 year-old boy with recurrent cough, bloody sputum, dyspnea and chronic fatigue was hospitalized. Chest radiograph demonstrated bilateral alveolar infiltrates. HRCT revealed areas of ground glass opacities. Transbronchial lung biopsies showed alveolar hemosiderosis and the bronchoalveolar lavage fluid was rich in hemosiderin-laden macrophages. Serologic markers; ANA, anti-ds-DNA, RF, c-ANCA, p-ANCA, and anti-BM were negative. No evidence of other organ involvement was found. The patient was diagnosed as IPH and corticosteroid therapy was started.
- Subjects
IRON metabolism disorders; PIGMENTATION disorders; HEMOCHROMATOSIS; HEMOSIDEROSIS; PULMONARY alveoli; HEMORRHAGE; BLOOD; ARTERIAL injuries; HEMARTHROSIS; THERAPEUTICS
- Publication
Turkish Thoracic Journal / Turk Toraks Dergisi, 2008, Vol 9, Issue 3, p124
- ISSN
2149-2530
- Publication type
Article