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- Title
Anaesthetic management of a child with panthothenate kinase-associated neurodegeneration.
- Authors
Sinha, Renu; Biyani, Ghansham; Bhattacharjee, Sulagna
- Abstract
Panthothenate kinase.associated neurodegeneration (PKAN) (Hallervorden.Spatz disease) is a rare autosomal recessive chromosomal disorder characterised by progressive neuroaxonal dystrophy. The characteristic features include involuntary movements, rigidity, mental retardation, seizures, emaciation. The anaesthetic concerns include difficult airway, aspiration pneumonia, dehydration, and post.operative respiratory, and renal insufficiency. We report successful anaesthetic management of a 9.year.old intellectually disabled male child with PKAN, scheduled for ophthalmic surgery under general anaesthesia.
- Subjects
ANESTHETICS; NEURODEGENERATION; DYSTROPHY; MUSCLE rigidity; INTELLECTUAL disabilities; LEANNESS; OPHTHALMIC surgery; PATIENTS
- Publication
Indian Journal of Anaesthesia, 2015, Vol 59, Issue 1, p43
- ISSN
0019-5049
- Publication type
Case Study
- DOI
10.4103/0019-5049.149449