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- Title
Takayasu's Arteritis Concurrent with Marfan Syndrome.
- Authors
Han Joo Baek; Ki Chul Shin; Yun Jong Lee; Seong Wook Kang; Eun Bong Lee; Yeong Wook Song
- Abstract
Marfan syndrome (MS) is a dominantly inherited connective tissue disorder characterized by arachnodactyly, tall stature, the presence of aortic aneurysm, and lens dislocation. Takayasu's arteritis (TA) is a chronic vasculitis that primarily affects the aorta and its branches. The authors report the first case of TA in a patient with MS. The simultaneous presence of TA and MS could be a coincidence, however; the pathogenesis of TA might be linked with autoimmunity induced by abnormal extracellular matrix protein derived from the genetic mutations in MS.
- Subjects
MARFAN syndrome; CONNECTIVE tissues; AORTIC aneurysms; AUTOANTIBODIES; GENETIC disorders; ARTERIAL diseases
- Publication
Angiology, 2000, Vol 51, Issue 5, p435
- ISSN
0003-3197
- Publication type
Article
- DOI
10.1177/000331970005100512