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- Title
Intradural lumbosacral malignant extrarenal rhabdoid tumor: a case report.
- Authors
Garling, Richard Justin; Singh, Rasanjeet; Harris, Carolyn; Haridas, Abilash
- Abstract
Background: Rhabdoid tumors are highly malignant tumors predominantly affecting the pediatric population. When these tumors occur outside of the kidneys, they are referred to as malignant extrarenal rhabdoid tumors (MERT), a rare highly aggressive subtype. Less commonly, these tumors involve the neuro-axis. Objective: Here we present a case of a 15-year-old girl with intradural MERT of the lumbosacral spine who presented with back pain, sudden worsening of lower extremity strength, and complete loss of bowel and bladder control. Results: The patient's tumor showed loss of INI-1 and negative staining for cytokeratin AE1AE3, CD99, and SOX10. Conclusions: To our knowledge, there are no previous case reports of MERT with intradural lumbosacral spinal involvement.
- Subjects
KIDNEY tumors; TUMORS in children; BACKACHE; KERATIN; LUMBAR vertebrae; TUMORS
- Publication
Child's Nervous System, 2018, Vol 34, Issue 1, p165
- ISSN
0256-7040
- Publication type
Article
- DOI
10.1007/s00381-017-3571-2