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- Title
Nasosinusal glomangiopericytoma: a case report of a rare clinical condition.
- Authors
Coêlho Neto, João; de Souza Costa, Rafael Neves; Miranda Lessa, Marcus; Cincurá Barreto, Carolina; Lucena Silveira, Débora; Burgos Camacho, Angie Paola; Barbosa Saraiva, Lucas Afonso
- Abstract
Introduction: Glomangiopericytoma is a rare type of sinonasal tumor arising from the pericytes surrounding capillaries that represents less than 0.5% of neoplasms in the nasal cavity and paranasal sinuses. It is referred as a low-grade neoplasm with borderline malignancy and a tendency of local recurrence. Objectives: To present a case report of a patient with glomangiopericytoma, an unusual pathology and little-known by health professionals, aiming to better assistance to these patients. Resumed report: A 58-year old female presented with constant right unilateral nasal obstruction for 5 years, ipsilateral yellowish rhinorrhea, epistaxis and facial pain. Endoscopic nasal examination showed a pink lesion, with an irregular surface, which extended from the sphenoethmoidal recess to the floor of the nasal cavity. Computed tomography showed a nodular lesion with an insufflative aspect, irregular limits, with contrast uptake, involving the corresponding middle turbinate, extending cranially to the ethmoid cells, at the level of the cribriform plate and caudally to the palate and posteriorly to the choana. Magnectic ressonance showed expansive formation with isosignal in all sequences and homogeneous enhancement by contrast, restricting diffusion. Incisional biopsy resulted in spindle cell proliferation. Immunohistochemistry favored glomangiopericytoma of the nasosinusal type. Endoscopic nasal surgery was indicated and anatomopathological results confirmed nasosinusal glomangiopericytoma. Conclusion: Despite being borderline and low-malignant potentially, glomangiopericytoma can extend to one or more of the sinuses and, in advanced stage, it can also spread to the skull base region. That's why must be known by otorhinolaryngologists so that early diagnosis, management and treatment can be promoted.
- Subjects
MEDICAL personnel; NASAL cavity; CRIBRIFORM plate; PARANASAL sinuses; SKULL base; DESMOID tumors; PHYLLODES tumors
- Publication
International Archives of Otorhinolaryngology, 2022, Vol 26, p67
- ISSN
1809-9777
- Publication type
Case Study